NBHSEIP Flashcards
Aim of NBHSEIP
Identify children w/ permanent HL for better language, educational & psychological outcomes
1-3-6
Screen by 1month
Diagnose by 3months
Intervene by 6months
Target permanent congenital hearing loss (PCHL)
- Established by ABR testing any HL >35dB eHL@500Hz
HL >30dB eHL@1-4kHz in either ear - This includes ANSD or retrocochlear lesion related impairment
- This includes CHL associated with structural anomalies but NOT TTS attributable to non-structural ME conditions
- Eligible for amplification
Children requiring monitoring of hearing
- Mild HL of 25-30 dB due to higher risk for progressive HL& TTS from CHL
Types of assessments
- ABR based
- OAE based
- Behaviour based
Behaviour Based assessments
- VRA
- CPA
- PTA
*choice is at the discretion of audiologist
Hearing Surveillance
AKA Targeted FU
Referral from paediatricians, nurses, midwives to screeners who will refer them to audiology
- Requiring OAE testing at 18months
- Requiring audiological care on a case by case basis but needs triage by audiologist due to low incidence
- Risk factors with specific pathways for audiological testing
Risk factors w/ specific pathways for audiological testing
- Down Syndrome
- Cleft Palates
- Cytomegalovirus
- Meningitis
Risk factors requiring triage
- Atresia
- Jaundice levels at or above transfusion is recommended
- Head or brain trauma
Risk factors requiring OAE testing @18months
- Continuous ventilation>5days: IPPV ECMO nitric oxide excludes CPAP
- Severe asphyxia (lack of oxygen supply)
- Brain haemorrhage
- Ototoxic meds
- Other syndromes associated with HL including but not limited to Pierre Robin, Sticklers, Goldenhar, CHARGE, Waardenburg, Pendred
- Toxoplasmosis
- Rubella
Cleft Palates
- Likely to develop OME
- Even if passed NBS —> FU at 7-9 months
- Management : BCHA needs to be determined based on timing of repair surgery & degree of loss
- Conventional not appropriate due to the nature of fluctuating HL in cleft
- Discussion w/ family
Discussion with family
- Good communication strategies
- Ways to enhance the listening developments
- How to recognise signs that hearing may have changed
- what to do if concerned about hearing
- Give brochures about hearing milestones and HL
Down Syndromes
- Mild HL can severely impact development of speech & Lang
- ME dysfunction leading to frequent OME
- Grommets not easy due to small sized ear
- Usually consider BCHA (at a younger age) than BTE due to fluctuating nature of CHL and small ear canal size
CMV
- Either normal or abnormal from screening
- Normal CMV have 4.3% risk of late onset SNHL
- Abnormal have risk of progression of HL
- If normal —> OAE at 5months then yearly till 5yo
- If abnormal —>ABR at 2~6wk and continue monitoring & intervention
Amplification goals
- Access to speech signal that’s consistently audible
- Avoid distortion
- Ensure flexibility electro acoustically for changes related to ear growth or acoustics of the child’s ear. (Sufficient headroom)
Amplification components
- A completed audiological result for both ears
- Acoustic characteristics of the baby’s ear canal in RECD
- Ear impression
- Assessment of non-electro acoustic of the baby
- Electro acoustic analysis of prescribed HA (ANSI test)
- DSL v5 target ear canal SPL for the amplified LTASS
- DSLv5 target ear canal SPL for defining the max saturation
- Response of the HA
- DSL v5 target ear canal SPLs for soft & loud speech
- Verification of whether HA are meeting the targets electro-acoustically
- Simulated REAR &RESR
- Education & counselling sessions with the family about first HA fitting &FUs
- Evaluation of the outcome of the intervention (LittlEARS PEACH)
- Appropriate FU
ABR based assessment
- Otoscopy
- Should be in both ears regardless of the referral
- Tone burst ABR including 500, 2k & 1 &4kHz if alerted
- High intensity click
- HF tympanometry + ART starting @80dB for BBN
- DPOAE amplitude & noise floor measurements @ 1.5, 2, 3, & 4kHz
Transducer for ABR and reason
Inserts unless contraindicated (structural abnormality in which case supra-aural are optional) to avoid AC masking
Indications for high intensity click ABR
All cases except when baby
1. Passes tone burst ABR & starting to wake up
Possible consequence for not doing click ABR because baby passed tone burst
Missing ANSD
ABR-based assessment: If the baby passes DPOAE protocols
Not essential to perform immittance testing
ABR completed + No DPOAE or immittance + baby wakes up & unable to finish testing
DC if no concern
High intensity click starting levels
80dBHL if tone burst normal
95dBHL (or the max. Intensity) if tone burst elevated (no identifiable waveform)
BC ABR
Placement- superoposterior to the canal opening