Myelodysplasia

Question 1

Myelodysplasia

Answer 1

Defective development of any part of the spinal cord

Associated with encephalocele, hydrocephalus, and Arnold Chiari Type II malformation

Question 2

Myelomeningocele

Answer 2

Opening in spine and sac

Question 3

Myelodysplasia high level lesion (T12-L2)

Answer 3

Hip flexion, hip abduction, hip external rotation, knee flexion, and ankle plantar flexion contractures. Lumbar lordosis

Question 4

Myelodysplasia mid-to-low level lesion (L3-L5)

Answer 4

Hip flexion, knee flexion, calcaneal valgus, pronated feet, genu valgus, lumbar lordosis, crouched gait

Question 5

Myelodysplasia low level lesion (sacral)

Answer 5

Calcaneal valgus and varus, mild hip and knee flexion contracture, mild crouched gait, lumbar lordosis

Question 6

Signs of shunt dysfunction

Answer 6

Changes in speech, headache, decreased activity level, upward dolls’ eye sign, irritability, decreased grip strength

Question 7

Dandy Walker syndrome

Answer 7

Congenital brain malformation involving the cerebellum and the fluid around it. Cerebellar vermis is not formed

Question 8

Myelodysplasia sensory deficits

Answer 8

Vibratory, light touch/pin-prick, and kinesthesia

Question 9

Myelodysplasia cognitive deficits

Answer 9

“Cocktail party” personality

Question 10

MOMS

Answer 10

Prenatal surgery benefits outweigh risks