Muscular Alterations Flashcards
What is muscular dystrophy?
inherited disease of the muscles, causing muscle atrophy and weakness
What is the most serious and most common of the dystrophies ____________, an X linked recessive disease affecting primarily males.
Duchenne muscular dystrophy
Duchenne muscular dystrophy appears in what age group?
early childhood ( 3 to five years)
Duchenne muscular dystrophy rapidly progresses, causing respiratory or cardiac complications and death, usually by ____ years of age.
25
What are some signs and symptoms of muscular dystrophy?
- waddling gait, lordosis
- increasing clumsiness, muscular weakness
- Gowers sign: difficulty rising to standing position; Has to “walk” up legs using hands
- pseudohypertrophy of muscles (especially noted in calves) due to fat deposits
- muscular degeneration, especially the thighs, and fatty infiltrates (detected by muscle biopsy); cardiac muscle also involved
- delayed cognitive development
- elevated CPK and SGOT/AST
what are some late signs and symptoms of muscular dystrophy?
- scoliosis
- respiratory difficulty
- cardiac difficulties
- eventually wheelchair dependency, confinement to bed
what are some nursing interventions that need to be provided to patients who have muscular dystrophy?
- provide supportive care
- provide exercises (active and passive)
- prevent exposure to respiratory infection
- encourage a balanced diet to avoid obesity
- support families grieving process
- support participation in the muscular dystrophy Association
who are some people in the health care team that the nurse coordinate with if the patient has muscular dystrophy?
- physical therapy
- occupational therapy
- nutritionist
- neurologist
- orthopedist
- geneticists
What is a traumatic injury to a bone called?
fracture
what are the three classifications of a fracture?
- complete
- incomplete
- comminuted
what is a complete fracture?
bone fragments are completely separate
what is an incomplete fracture?
bone fragments remain attached (green sticks, bins, buckles)
what are comminuted fractures?
- bone fragments from the fractured shaft break free and go in the surrounding tissue
- this type of fracture is rare in children
Fractures that occur in the __________ plate may affect growth of the limb.
epiphyseal (growth plate)
Fractures in ______ children are common because of falls during play and are involved in motor vehicle accidents.
older (school age and adolescence)
Spiral fractures (caused by twisting) and fractures in _______ may be related to child abuse.
Infants
what are the general conditions, signs and symptoms, that will be seen with fractures?
- visible bone fragments
- pain
- swelling
- contusions
- child guarding or protecting the extremity
what are the five P’s that may indicate the presence of ischemia with a fracture?
- pain
- pallor
- pulselessness
- paresthesia
- paralysis
- poikilothermia
what are some nursing interventions that need to be done for a fracture?
- obtain based on data and frequently perform narrow vascular assessments
- report abnormal assessment promptly
- maintain traction if prescribed
- maintain child in proper body alignment
- monitor for problems of immobility
- provide age-appropriate play and toys
- prepare child for cast application; use age-appropriate terms when explaining procedure
- provide routine cast care following application; petal cast edges
- teach home cast care to family
What are some signs and symptoms that need to be assessed when checking vascular changes?
- check pulses distal to injury to assess circulation
- color: check injured extremity for pink, brisk, capillary refill
- movement and sensation: check injured extremity for nerve impairment; compare for symmetry with uninjured extremity
- temperature: check extremity for warmth
- swelling: check for an increase in swelling, elevate extremity to prevent swelling
- pain: monitor for severe pain that is not relieved by analgesics
why should abnormal assessments of a fracture be reported immediately?
compartment syndrome may occur; It results in permanent damage the nerves and vasculature of the injured extremity due to compression
What should be noted if traction is prescribed?
- bed position
- type of traction
- weight
- pulleys
- pins
- pin sites
- adhesive strips
- ACE wraps
- splints
- casts
What are two types of skin traction that are used for a fracture?
- buck extension traction
- Russell traction
What is buck extension traction?
lower extremity, legs extended, no hip flexion
what is Russell traction?
2 lines pull on the lower extremity, one perpendicular, one longitudinal
What is skeletal traction and an example?
- pin or wire applies pull directly to the distal bone fragment
- Halo traction
What are some examples of home cast care to teach a family?
- teach neurovascular assessment of casted extremity
- teach child not to get cast wet
- teach child not to place anything under cast
- teach child to keep small objects, toys, and food out of cast
- teach family to modify diapering and toileting to prevent cast soilage (double diapering)
- teach that in the presence of a hip spica, family may use a Bradford frame under a small child to help with toileting; they must not use abduction bar to turn child
- Teach to seek follow up care with health care provider
what is developmental dysplasia of the hip?
abnormal development of the femoral head in the acetabulum
what are the treatment options for developmental dysplasia of the hip?
- conservative treatment consists of splinting
- surgical intervention is necessary if splinting is not successful
what are some signs and symptoms of developmental dysplasia of the hip in an infant?
- positive Ortolani sign (“clicking” with abduction)
- unequal folds of skin on buttocks and thigh
- limited abduction of affected hip
- unequal leg lengths
what are some signs and symptoms of developmental dysphasia other the hip in older children?
- limp on affected side
- Trendelenburg sign (when the child stands, bearing weight on the affected hip, the pelvis tilts downward on the normal sod instead of upward with the normal stability – this is a positive Trendelenburg sign)
What are some nursing interventions to provide for a patient who has developmental dysplasia of the hip?
- perform newborn assessment at birth
- apply abduction device or splint (Pavlick harness); therapy involves positioning leg in flexed abducted position
- teach parents home care
- provide nursing care for a child requiring surgical correction
what are some home teaching points that need to be given to parents who have a child with developmental dysplasia of the hip?
- teach application and removal of device (worn 24 hours a day)
- teach skin care and bathing (physician may allow parents to remove device for bathing)
- teach diapering
- teach that follow-up care involves frequent adjustments because of growth
What are some post-operative cares that needs to be provided for a patient who has had surgical correction for developmental dysplasia of the hip?
- assess vital signs
- check cast for drainage and bleeding
- perform narrow vascular assessment of extremities
- perform respiratory hygiene
- administer narcotic analgesic around the Clock
- teach family cast care when child goes home