Module 5: Paediatrics Flashcards
most common cause of acute respiratory obstruction in young children
croup
steeple sign think
is what
croup
loss of normal lateral convexities of the subglotic trachea
H Influenza causes
epiglottitits
thumb sign is what
swelling of epiglottis
epiglottitis asphyxiation is cause by what
aryepiglotic folds
exudative infection of the trachea can cause
exudative tracheatitis
exudative tracheatitis bug is
Staph A
exudative tracheatitis buzzword sign
linear soft tissue filling defect within the airway
what is the next step is there is pseudothickening from neck not being truly lateral
in retropharyngeal cellulitiis and abscess
repeat with extended neck
Retropharyngeal abscess vs suppurative node?
Retropharyngeal abscess is midline
supparative node is medial to the carotid
subglottic hemangioma
can cause what
subglottic obstruction.
Like croup but will b e one sided
subglottic haemangiomas are associated with
cutaenous haemangiomas (50%0
PHACES syndrome (7%)
what is the PHACEs syndrom e
Posterior fossa
Haemgiomas
Arterial anomalies
Coarctation of aorta, cardiac defects
Eye abnormalities
Subglottic haemangiomas
measurements of concern on lateral xr
for retropharyngeal absess
C2 >6mm
>22mm at C6
Should adenoids encroach on the airway
no
Exudative tracheitis sign on lateral radiograph
linear filling defect
meconium aspiraiton more common in what delivery time baby
term or post-mature babies
meconium aspiraiton appearance of lungs
ropy
hyperinflated
20-40% have pnuemothoraxx
TTN affects which ne wborn (dleivery style)
c-section
diabetic mother
maternal sedation
TTN findings start at what time
6 horus
TTN is normally done by what time frame
3 days
SDD (surfatant deficiency) which babies
pre term
Chest radiograph appearance of SDD
low lung volums and bilateral granular opacities
NOT pleural effusion as with B haemolytic pnuemonia
surfactant replacement therapy risks
pulmonary haemorrhage
PDA
Neonatal pneumoina
look like what on radiograph
patchy
asymmetric hilar densitiies
hyper inflation
Beta haemolytic strep pneumonia
neonate
dirty birth canal
low lung volums
GRANULAR opacities
pleural effusions
Persistent pulmonary HTN
caused by
primary
secondary to hypoxia (infection, aspiraiton)
pulmonary interstitial emphysema
linear lucencies
PIE vs bronchopulmonary dysplasia
age
PIE less than 2 weeks
Chronic lung disease - who get this?
small, pre term kid.
after 2 weeks get hazy lungs.
band like opacities is a buzzword
Pulmonary hypoplasia causes
Primary or secondary
secondary
- decreased hemithoracic volume ( decreased vascular supply, decreased fluid
decreased hemithoracic volume what can cause this,
(CONGENTIAL DIAPHRAGMATIC hernia
types of bronchopulmonary sequestration
intralobar
extralobar
bronchopulmonary sequestration distinction is based on
pleural covering
sequestration blood supply
intralobar drains to pulmonary veins
extra drain to systemic veins
neonatal lung volumes on radiograph
if low
surfactant deficiency
heta haemolyticpneumonia (pleural effusion)
neonatal lung volumes on radiograph
if high
meconium aspiration
transient tachypnoea
neonatal pneumonia
more common?
sequestration type?
intralobar
how do people with intralobar sequestration present
pneumonia in their late teens / adult
intralobar is commonly which segment
left lower lobe posterior segments
no pleural cover for sequestration ascribed to
intralobar
Extralobar sequestration present in
infancy
what are the associations to extralobar sequstration
Congenital Cystic Adenomatoid malformation (CCAM)
Congenital diaphragmatic hernia
vertebral anomalies
congenital heart disease
pulmonary hypoplasia
why does extralobar sequestration rarely get infected?
has its ow pleural covering
bronchogenic cysts - do they connect to the airway?
if they have gas in them?
no
if gas in them consider infection
CCAM / CPAM different types
1 - 3
cystic
solid
3 is middle ground
if theres systemic arterial feeding a CCAM?
not a CCAM but a sequestration
congital lobar emphysema has preference for which lobe?
left upper lobe
how to treat congenital lobar emphysema
lobectomy
congenital Bochdalek hernia is found where?
back left of the diaphragm
associations of Congenital Diaphragmatic Hernia
malrotated
congenital heart disease
mortality of the congenital diaphragmatic hernia
is associated to the hypoplasia
what is round pneumonia
less than 8 years old
looks like a mass
Common bug for round pneumonia
S Pneumoniae
What is Swyer James
unilateral lucent lung
post viral lung infection in childhood post infectious obliterative bronchiolitis
the size of the affected lobe is smaller! Of note for a lucent lung
what causes papillomatosis ?
perinatal HPV
sickle cell kids get what in bones
infarcts
H shaped vertebra
cystic fibrosis vs primary ciliary dyskinesia
sodium pump broken therefore thick secretions in CF. Men are missing vas deferens.
PCD - cilia motile doesn’t work. Therefore lower lobe predominant. Men sperm not motile
PCK and Kartaganers relationship
50% will have Kartageneres (situs inversus)
Thmic rebound on PET
can be bright
and large
Germ cell tumour in anterior mediastinal masses - three types
Teratoma - calc and fat
Seminoma - bulky lobulated
NSGCT - necrotic
Middle mediastinal masses
Lymphadenopathy (TB or lymphoma)
Duplication cysts (bronchogenic or enteric)
Bronchogenic - water attenuation.
Enteric- water attenuation close the oesophagus.
Posterior mediasintal mass
Neuoblastoma
Ewing sarcoma
Neuroenteric cyst
Extramedllary hematopoiesis
posterio med mass - neuroblastoma
found in age -
less than 2
Askin (PNET) is now considered to be
past of the Ewing sarcoma .
Neuroenteric cyst - associated with
vertebral anomalised
What is extramedullar hematopoiesis
myloproliferative disorder patients, manifests with big liver and spleen.
mediastinal mass by age
?lymphoma
if over 10
if under think thymus
how to distinguish between a pleuropulmonary blastoma and an askin tumour
PPB doesn’t invade the ribs
Course of the umbilical venous cathter
umbilical vein
left portal vein
ductus venosus
hepatic vein
IVC
mbilica lartery cathter should sit
T8-10
or
L3 - L5
Esophageal atresia subtypes
number
ax
common type
air in stomach means
5
VACTERAL
N - blind oesophagus, oesophagus to trachea
H type
VACTERAL is WHAT
most common affected
Vertebral anomalies
Anal
Cardiac
TE fistula
Renal
Limb
heart and kidneys
Vascular ring that goes between the oesophagus and the trachea
Pulmonary sling
most common symptomatic ring
doulbe aortic arch
neonatal obstruction - high causes
Midgut volvulus or malrotation
duodenal atresia
duodenal web
annular pancreas
jejuna atresia
neonatal obstruction - low causes
Hirschsprung
meconium plug syndrome
ileal atresia
meconium ileus
anal atresai / colonc atresia
radiograph
triple bubble dx
jejunal atresia - caused by vascular insult during development
doulbe bubble with gas
distal gas excludes atresia.
ddx - duodenal web, stenosis or volvulus midgut
radiograph
multiple diffuse dilated loops
differential and management plan
low obstruction
enema contrast
then upper GI if that is normal
malrotation puts which ligament on the right
Trietz
malrotation blood vessel orientation
SMA to the right of the SMV
Corkscrew duodenum is diagnositc of
midgut volulus
pyloric stenosis age range
2 - 12 weeks
pyloric stenosis length criteria
4mm and 14mm
single wall and legnth
two types of gastric volvulus
organoaxial
mesenteroaxial
duodenal web is posiootined
distal to ampulla vater (bilious vomitting )
duodenal web is ax with what
downs and malrotation
annular pancreases causes waht in adults vs kids
adults pancreatitis
kids - duodenal obstruction
differentials for long microcolon
meconium ileus (CF patients)
Distal ileal atresia (fetus gets a vascular insult to cause this)
large bowel contrast enemea
caliber change
ddx
small left colon syndrome or Hirschsprungs
what is small left colon syndrome
transient functional colonic obstruction
relieved by contrast enems
who gets small left colonic syndrome
infants of diabetic mothers
(NOT ax to CF)
what is Hirschsprungs
failure of ganglion cells to migrate and innervate the distal colon
appearance of hirschsprungs
rectum is smaller than sigmoid or sawtooth pattern (spasm)
what is total colonic aganglionosis
super rare version of Hirschprungs
affects the Terminal ileus
mimic microcolon.
What is meconium periotonitis ?
calcified mass in mid abdo
sterile periotneal reaction to an intra utero bowel perforaiton
Imperforate anus / ectopic anus
associated to
tethered cord
- need US to review for this
VACTERL
Tender abdomen in an oler child
AIM diagnosis
Appendicitis or adhesion
inguinal hernia or Itussusception
Midgut volvulus / meckels
Appendicitis size
> 6mm
intusseption target sign size
how does it affect the tratment
> 2.5cm - likely to be ileocolic and so air enema
<2.5 small bowel small bowe, not getting an air enema
Meckels diverticulum rule of 2s
Persistent omphalomesenteric duct
2% of population
2 hetertopic mucosa (gastric and pancreatic)
2 ft from IC valve
2 inhes long and 2cm in diameter
present symtpoms pre-2yo
Which nuclear medicine scan in meckels
pertechnetate
WHAT IS an enteric duplication cyst
failure to canalize.
Can communicate with GI lumen.
common in ileal region.
can cause IN UTERO obstruction and perforation
distal intestinal obstruction syndrome
affects which patient group
CF
aren’t compliant with their pancreatic enzymes
NEC
who gets
prem
low birth weighty
cardiac
perinatal asphyxia
Hirschsprung
what does NEC look like?
Pneumatosis
Focal dilated bowel (especially in right lower wquadrant)
featureless small bowel (oedema)
unchanging bowel gas pattern
what is Gastroschisis
extra-abdominal evisceration of neonatal bowel through paraumbilical defect
Gastroschisis
membrane
sided
ax anomalies
AFP level
OUtcome
complications post repair
NO membrane
right sided
ax anomalies are RARE
Maternal serum AFP will be elevated.
Outcome is usually good
bad reflux
What is omphalocele
congenital midline defect with herniation of gut at the base of the umbilical cord
omphalocele
membrane
ax anomalies
outcomes
DOES have a membrane
ax tto Trisomy 18 and others
Outcomes not good
umbilical cord cysts
What is physiological gut herniation
normal around 6- 8 weeks.
does not cintain any liver
what to see on mesenteric adenitis
cluster of right lower quadrant lymph nodes