lens Flashcards
acquired ectopia lentis causes
trauma
large eye
anterior uveal tumor
hypermature cataract
hereditary ectopia lentis causes
familial ectopia lentis ectopia lentis et pupillae marfan syndrome weill-marchesani syndrome homocystinuria
hereditary ectopia lentis RARER causes
aniridia stickler syndrome ehlers danlos hyperlysinaemia sulphite oxidase deficiency
familial ectopia lentis
AD
bilateral
symmetrical
superotemporal
ectopia lentis et pupillae
AR
bilateral ectopia of lens and pupil but in different directions
marfan syndrome ectopia lentis
AD bilateral symmetrical superotemporal Intact zonules
weill-marchesani syndrome ectopia lentis
AD or AR
bilateral
inferior
homocystinuria ectopia lentis
AR
inferonasal
disintegration of zonules
ectopia lentis complications
refractive error optical distortion glaucoma cataract endothelial damage lens induced uveitis
ectopia lentis tx
spectacles for astigmatism/ aphakic correction
surgery for cataract, glaucoma, uveitis, endothelial touch
coloboma
notching or segmental agenesis at inferior equator
absence of zonular fibres
lenticonus
conoid curvature + thinning of capsule
ant = Alports
lentiglobus
spherical curvature + thinning of capsule
microspherophakia
def
causes
spherical lens with a small diameter
familial AD Marfan weill-marchesani syndrome hyperlysinaemia congenital rubella
microspherophakia
complications
ocular associations
lenticular myopia
subluxation
dislocation into ant chamber
Peters anomaly
Familial ectopia lentis et pupillae
congenital cataract
types
nuclear lamellar sutural ant polar post polar coronary/ supranuclear blue dot
congenital cataract inheritance
AD
congenital cataract
metabolic causes
Galactosemia oil droplet galactokinase def lowe syndrome hypocalcemia hypo/hyperglycemia mannosidosis
congenital cataract
infectious causes
TORCH
toxo
rubella
CMV
HSV
congenital cataract
chromosomal abnormalities
Trisomy 21, 13, 18
turner
cri du chat
complications of cataract surgery
rupture of post capsule post loss of lens material post dislocation of IOL Suprachoroidal haem endophthalmitis acute/ delayed capsular opacification decentration of IOL Retinal detachment CMO
rupture of post capsule
problems
tx
vitreous loss
post loss of lens material
remove lens material
clear vitreous from ant chamber
long term comp of vitreous loss
updrawn pupil chronic uveitis endothelial vitreous touch retinal detachment CMO
post loss of lens material
COMP
Tx
glaucoma
chronic uveitis
retinal detachment
CMO
remove nuclear fragments by pars plana vitrectomy
post dislocation of IOL
COMP
Tx
vitreous haem
uveitis
retinal detachment
CMO
pars plana vitrectomy
remove IOL
Suprachoroidal haem
Predisposing
Tx
elderly glaucoma increased axial length systemic CV disease vitreous loss
immediately close incision
U/S
Pars plana vitrectomy 7-14 days later