Lecture 6.2: Hearing Disorders Flashcards
What is Sound?
- A compressive wave that travels at 343m/sec in air
- > 1500m/sec in water
What are the 2 properties of sounds waves?
1) Frequency = Distance = Hertz (Hz)
2) Volume = Pressure = Decibels (dB)
What is the hearing range (frequency) of humans?
20-20,000 Hz
What is normal volume of conversation in humans?
60dB
At what volume doe sound get painful for humans?
120dB
What is Hearing?
Conscious appreciation of vibration perceived as sound
What is Deafness?
Hearing loss so severe that there is very little or no functional hearing
What does it mean to be Deaf (capital D)?
- Deaf (capital D) people that have been deaf for all of
their lives, or since before they started to learn to talk * Prelingually deaf
What does it mean to be deaf (lower case d)?
- Anyone that has a severe hearing problem
- Usually postlingual
- May use hearing aids/cochlear implants
What does it mean to be hard of hearing?
Mild to moderate hearing loss
External Ear Anatomy (3)
- Pinna (Auricle)
- External Auditory Meatus
- Tympanic Membrane
Middle Ear Anatomy (4)
- Tympanic Membrane
- Ossicles
- Mastoid
- Eustachian Tube
Inner Ear Anatomy: Bony Labyrinth (4)
- Cochlea
- Vestibular Apparatus
- 3 Semicircular Canals
- Filled with perilymph
Inner Ear Anatomy: Membranous Labyrinth (4)
- Inside Bony Labyrinth
- Cochlear Duct
- Utricle and Saccule
- Semicircular Ducts
- Filled with Endolymph
Mechanism of Hearing
- The pinna collects and amplifies sound waves
- The EAM funnels them to the tympanic membrane
(TM) - The TM vibrates, transferring the vibrations
sequentially to the ossicles, the oval window and the
fluid of the inner ear - The middle ear amplifies the sound by ~30dB
- Thus the middle ear converts sound waves in air of
EAM to vibrations in fluid of inner ear - The inner ear converts mechanical signals (vibrations
in fluid) to electrical signals → auditory pathway→
brain
Function of the Inner Ear
1) Convert mechanical signals (vibrations in
fluid) to electrical signals → auditory pathway→
brain
2) Maintain balance
Inner Ear openings to Middle Ear (2)
- Oval window (connects vestibule to ME at stapes
footplate) - Round window (connects scala tympani with middle
ear)
Mechanism of Hearing in the Cochlea
- Vibration of stapes at oval window→ vibrations of
perilymph in scala vestibuli - Vibrations transmitted to endolymph in cochlear duct
and spiral organ of Corti on basilar membrane - Hair cells stimulated→impulses travel along CNVIII to
brain
Auditory Transduction: Hair Cells
- 4 rows of hair cells
- 1 inner hair cells row (provide most of the signal to CN
VIII) - 3 outer hair cell rows (role in modulating the response
of the inner hair cells)
What is the Primary (Lemniscal) Pathway?
Main pathway through which auditory information reaches the primary auditory cortex
What is the Non-Lemniscal Pathway?
Mediating unconscious perception eg. attention, emotional response, and auditory reflexes
Can supranuclear lesions cause hearing loss?
No
Where in the ear do lesions occur in conductive hearing loss?
Lesions in the outer or middle ear
Where in the ear do lesions occur in sensorineural hearing loss?
Lesions in the inner ear or vestibuloccochlear nerve (VIII)
What is Mixed hearing loss?
Lesions in the outer or middle ear AND Lesions in the inner ear or vestibuloccochlear nerve (VIII)
Where in the ear do lesions occur in Central hearing loss?
Lesion in the auditory pathway in the brain (rare)
Hearing loss usually involves sensitivity and acuity, what does this mean?
Sounds are harder to hear (sensitivity) and they are usually distorted (acuity)
What happens to the Tympanic Membrane in Conductive Hearing Loss?
- EAM/TM may look abnormal
- (except otosclerosis)
- May be temporary or treatable
What happens to the Tympanic Membrane in Sensorineural Hearing Loss?
- TM usually looks normal
- Often permanent
What is the Weber Test?
- Tuning fork in middle of head
- Sound should be equal in both ears if normal
Weber Test in Conductive Hearing Loss
Sound lateralises to affected side
Weber Test in Sensorineural Hearing Loss
Sound lateralises to unaffected side
What is the Rinnes Test?
- Tuning fork behind ear and in front of ear
- Compares perception of sounds transmitted by air
conduction to those transmitted by bone conduction - Patient should be able to hear the sound of the tuning
fork adjacent to their ear for approximately twice as
long as the sound they heard over their mastoid.
process
Rinnes Test in Conductive Hearing Loss
Bone conduction is better than air conduction
Rinnes Test in Sensorineural Hearing Loss
Air conduction is better than Bone conduction
What is the Speech Banana?
Represents the level/intensity and tone/frequency of sounds of speech in language
Ability to hear depends on….? (2)
- Pitch (frequency) (Hertz (Hz))
- Loudness (decibel (dB))
What is a Pure Tone Audiogram?
A graphical representation of a person’s hearing acuity at a range of frequencies and loudness levels
Pure Tone Audiogram: Normal Hearing
Pure Tone Audiogram: Conductive Hearing Loss
Pure Tone Audiogram: Sensorineural Hearing Loss
Pure Tone Audiogram: Mixed Hearing Loss
- BC > AC
- BC >20dB hearing loss
Mild High-Frequency Loss
Moderate-to-Severe Bilateral Loss
What conditions can cause Conductive Hearing Loss? (5)
- Acute Otitis Media (AOM)
- Glue Ear (OME)
- TM Perforation/Retraction
- Cholesteatoma
- Otosclerosis
What conditions can cause Sensorineural Hearing Loss Bilaterally? (5)
- Congenital Defect
- Infections: measles, meningitis
- Presbyacusis
- Noise induced hearing loss
- Ototoxic Drugs (eg. gentamicin)
What conditions can cause Sensorineural Hearing Loss Unilaterally? (3)
- Congenital Defect
- Acoustic Neuroma (vestibular schwannoma)
- Menieres
What can cause Congenital Hearing Loss? (3)
- Genetic
- Intrauterine Infections (rubella, CMV)
- Prematurity
When are children tested for congenital hearing loss in the UK?
- Newborn screening hearing test
- Again at 8 months of age
How do people with hearing loss go about daily life? (2)
- Hearing Aids
- Sign Language
What is seen on an Audiogram in Noise Induced Hearing Loss?
4kHZ dip
What is seen on an Audiogram in Congenital Hearing Loss?
Cookie Bite like shape
What is seen on an Audiogram in Presbyacusis?
High frequency SNHL
What is seen on an Audiogram in Menieres?
Low frequency SNHL
What is seen on an Audiogram in Noise Induced Hearing Loss?
What is Presbyacusis?
Bilateral age-related hearing loss.
What is Acute Otitis Media?
- An infection of the middle ear
- Most commonly seen between the ages of 6 to 24
months
What is Glue Ear (OME)?
Glue ear is where the middle part of the ear canal fills up with fluid, the Eustachian tube seems to lose the ability to drain away the mucus
What is Cholesteatoma?
A type of skin cyst that is located in the middle ear and mastoid bone in the skull
What is Otosclerosis?
- Fixation of the stapes footplate to the oval window of
the cochlea - This greatly impairs movement of the stapes
- Therefore transmission of sound into the inner ear
(“ossicular coupling”) is lost
What is Menieres?
A distension of membranous labyrinth by the endolymph, equally called endolymphatic hydrops
What are the 4 symptoms of Menieres Disease?
- Vertigo Attacks
- Fluctuating Hearing Loss
- Tinnitus
- Auricular Plenitude Sensation
What is an Acoustic Neuroma (Vestibular Schwannoma)?
- Tumour of the vestibulocochlear nerve arising from
the Schwann cells of the nerve sheath - Benign and usually slow-growing
- Bilateral acoustic neuroma occurs in
neurofibromatosis-type 2 (NF2) - Investigate unilateral SNHL and/or tinnitus with MRI
Management of Acoustic Neuroma (3)
- Microsurgery
- Stereotactic Radiosurgery
- Observation
What treatments can be given for Sensorineural Hearing Loss?
- Hearing Aids
- Cochlear Implant
What key investigation should be done in Sensorineural Hearing Loss?
MRI Internal auditory meati if unilateral, to exclude
acoustic neuroma
How do Hearing Aids aid hearing?
- Improve sensitivity to sound by amplifying it
- But do not improve acuity.
- Make it louder but not clearer
How do Cochlear Implants work?
How do Cochlear Implants aid hearing?
Bypass damaged portions of the ear and directly stimulate the auditory nerve
Bone Anchored Hearing Aid (BAHA)
- Transferring sound through bone conduction, and
stimulating the cochlea of the normal hearing ear - Effectively transmitting sounds from the bad side into
the normal ear resulting in a sensation of hearing
from a deaf ear
How to prepare for communicating with people who are d/Deaf or hard of hearing? (11)
- Book an interpreter
- Talk directly to your patient, not the person
interpreting for them - Make sure you have your patient’s attention before
talking - Maintain eye contact whilst communicating
- Use normal lip movement
- Make sure the room is well lit so that the patient can
see your face clearly - Speak in plain English at a normal speed
- Use written notes or diagrams
- Use gestures and facial expressions to help explain
yourself - Point to parts of your body if necessary
- Keep checking to make sure your patient understands
you