Juvenile Dermatomyositis

Question 1

MC inflammatory myositis in children

Answer 1

JDM

Question 2

Rheuma: Proximal muscle weakness and a characteristic rash

Answer 2

JDM

Question 3

JDM, T/F: History of infection is commonly reported

Answer 3

T, in the past 3 months

Question 4

JDM: First symptom in 50% of cases

Answer 4

Rash

Question 5

JDM, T/F: Rash appears concomitant with weakness in a vast majority

Answer 5

F, 25% of the time

Question 6

Rheuma: Shawl sign

Answer 6

JDM, erythema over chest and neck from extreme photosensitivity to UV light

Question 7

Rheuma: Heliotrope rash

Answer 7

JDM, Blue-violet discoloration of eyelids

Question 8

Rheuma: Gottron papules

Answer 8

JDM

Question 9

Bright pink or pale shiny thickened ATROPHIC plaques over the PIP and DIP and occasionally on other areas seen in JDM

Answer 9

Gottron papules

Question 10

Rheuma: Mechanic’s hand

Answer 10

JDM

Question 11

Thickened erythema and scaly rash in children over the palms and soles along the flexor tendons

Answer 11

Mechanic’s hand

Question 12

Mechanic’s hand is associated with what antibodies

Answer 12

Anti-Jo-1 antibodies

Question 13

Rheuma: Gower sign

Answer 13

JDM

Question 14

JDM, T/F: Muscle weakness is symmetric

Answer 14

T

Question 15

JDM, T/F: Characterized by head lag in a child after infancy

Answer 15

T

Question 16

Use of hands on thighs to stand from a sitting position

Answer 16

Gower’s sign

Question 17

Associated with long-standing JDM

Answer 17

1) Lipodystrophy 2) Calcinosis

Question 18

JDM: Criteria for diagnosis

Answer 18

Characteristic rash (Heliotrope or Gottron) + at least 3 of the ff: 1) Muscle weakness (symmetric, proximal) 2) Muscle enzyme elevation (CK, AST, LDH, aldolase) 3) EMG changes (myopathy, denervation) 4) Muscle biopsy (necrosis, inflammation)

Question 19

JDM that presents with classic rash but no apparent muscle weakness or inflammation

Answer 19

Amyopathic JDM

Question 20

Mainstay of therapy in JDM

Answer 20

Corticosteroids