Interstitial Lung Disease

Question 1

What are the types of ILD?

Answer 1

1. Idiopathic Interstital pneumonias
   > Idiopathic Interstital Fibrosis
2. Granulomatous ILD
   Sarcoidosis
   Hypersensitivity pneumonitis
3. ILD of known association
   Connective tissue disorders
   Drugs
   Occupational exposures
4. Miscallaneous
   Pulmonary Langherans cell histocytosis

Question 2

What is the most common ILD in older people?

Answer 2

Idiopathic pulmonary fibrosis

Question 3

What is the most common ILD In younger people?

Answer 3

pulmonary sarcoidosis in younger adults.

Question 4

How is the pathophysiology of IPF different to that of other ILD?

Answer 4

It’s primary a process of fibrosis, whereas the other subtypes, inflammation occurs prior to development of fibrosis (AFP interstitital lung disease in 2015)

Question 5

Management of IPF?

Answer 5

pulmonary rehabilitation

drugs for symptom control, such as drugs for gastro-oesophageal reflux, opioids for dyspnoea and short courses of corticosteroids for acute exacerbations

long-term oxygen therapy for patients with resting hypoxaemia; although oxygen may not improve symptoms.

Early lung transplant

Anti fibrotic agents – have shown to reduce the decline in LFT over 12 months