IEM Urine Odor Flashcards
1
Q
Sweaty feet, acrid
A
Glutaric acidemia, Isovaleric acidemia
2
Q
Swimming pool
A
Hawkinsuria
3
Q
Boiled cabbage
A
Hypermethioninemia, Tyrosinemia
4
Q
Tomcat urine
A
Multiple carboxylase deficiency
5
Q
Hops-like
A
Oasthouse urine disease
6
Q
Mousey/musty
A
PKU
7
Q
Rotting fish
A
Trimethylaminuria
8
Q
Rancid butter
A
Tyrosinemia