Hypospadias Flashcards
incidence
1/300 live male births
principles of hypospadias repair
Regardless of the particular type of repair, there
are three specific components to the surgical correction of hypospadias:
• correction of the penile chordee
• reconstruction of the urethra (urethroplasty)
• skin coverage of the penis aimed at achieving a normal cosmetic appearance.
formation of urethra embryology
Influence of DHT on androgen receptors results in differentiation of genital tubercle, genital labioscrotal folds and genital swelling between 9-13 weeks gestation into male structures of glans penis, penile shaft, and scrotum respectively
features of hypospadias
- an abnormal ventral opening of the urethral meatus
- ventral curvature (chordee) of the penis
- a hooded foreskin, which is deficient ventrally.
embryology hypospadias
incomplete closure of the penile structures during embryonegensis
urethral opening displaced ventrally
corpus spongiosum is divied proximal to meatus
distal to meatus urethra is hypoplastic
Duckett classification hypospadias
glanular subcoronal distal penile mid shaft proximal penile penoscrotal scrotal perineal
Duckett classification hypospadias
glanular subcoronal distal penile mid shaft proximal penile penoscrotal scrotal perineal
Hadidi 2004 classification hypospadias
glanilar
distal - to mid shaft
then proximal
embryological time period tubularisation urethra
from week 10 to week 14
when would do work up for dsd
if hypospadis with unliateral or bilateral UDT
familial risk
7% will have one relative affected
when to do surgery for hypospadias
usually 6-18 months
aims of hypospadias surgery
correct chordee
site meatus to tip of glans
cosmetic appearance
adquate voiding and sexual function
technique operation
penile degloving orthoplasty urethroplasty glansplasty meatoplasty
distal hypospadias techniques
MAGPI
snodgrass/TIP
Mathieu
proximal hypospadias techniques
two stage repair with graft
MAGPI
glanular and selected coronal hypospadias
aim to advance meatus onto glans
TIP/snodgrass
urethral plate tubularised around a catheter
if urethral plate too narrow incise
can correct to mid shaft cases
deglove
urethral plate seperated from glans wings
midline relaxing incision through plate for tension free tubularisation
interval period two stage repair
6 months
first stage of graft repair
skin deglovement
resection chordee
transection urethral plate
graft then formed neourethral plate
second stage
new formed urethral plate tubularised to create neourethra which is then covered with dorsal dartos flap
catheter after hypospadias repair
try to leave in for a week in double nappy 6F feeding tube
complications hypospadias surgery
glans width less than 14mm
higher risk complications
more proximal location
fistula - will rarely close spont
reduced if cover with dartos layer so not in contact penile skin
meatal stenosis when blood supply neourethra is compromised
or when urethra is sutured distally can get meatal stenosis
urethral diverticular due to urethral stenosis distally
glans dehiscence
ongoing penile curvature