Heme/Onc Flashcards

1
Q

Christmas disease refers to:

A

Hemophilia B

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
2
Q

Hemophilia B is a deficit of:

A

Factor IX

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
3
Q

Hemophilia A is a deficit of:

A

Factor VIII

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
4
Q

Pt with hemophilia B has traumatic bleeding, what is the dose of factor IX replacement?

A

100 IU/Kg

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
5
Q

Lab findings in Wilson Disease:

A
  • Low ceruloplasmin
  • Low serum copper
  • Increased urine copper
  • Elevated aminotransferases
  • Thrombocytopenia
  • Coagulopathy (impaired liver function)
  • Coombs-negative hemolytic anemia
How well did you know this?
1
Not at all
2
3
4
5
Perfectly
6
Q

Treatment for Wilson disease:

A

Penicillamine

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
7
Q

Fever, thrombocytopenia, kidney injury, neuro findings, anemia = ?

A

Thrombotic thrombocytopenic purpura

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
8
Q

Treatment for thrombotic thrombocytopenic purpura?

A

Plasma exchange

How well did you know this?
1
Not at all
2
3
4
5
Perfectly