GLYCOGEN METABOLISM (REPORT)

Question 1

is an absolute requirement for human life.

needs to be sustain within the body.

preferred energy source for the brain

Answer 1

BLOOD GLUCOSE

Question 2

is a branched-chain polysaccharide made exclusively from α-D-glucose.

Answer 2

Glycogen

Question 3

attached to uridine diphosphate (UDP) is the source of all the glucosyl residues that are added to the growing glycogen molecule.

Answer 3

α-D-Glucose

Question 4

the second product of the reaction, is hydrolyzed to two inorganic phosphates (Pi) by pyrophosphatase.

Answer 4

Pyrophosphate (PPi)

Question 5

In the absence of a glycogen fragment, a protein called ___ can serve as an acceptor of glucose residues from UDPglucose.

Answer 5

glycogenin

Question 6

Glucose 1-phosphate is converted in the cytosol to glucose 6-phosphate by ____

Answer 6

phosphoglucomutase.

Question 7

Type 0a

Glycogen synthase-2

Liver

Answer 7

Lewis’ Disease

Question 8

Type 0b

Muscle Glycogen synthase

Skeletal & Cardiac Muscle

Answer 8

Lewis’ Disease

Question 9

Type Ia
Glucose 6-phosphatase
Liver

Answer 9

Von Gierke Disease

Question 10

Type Ib
Glucose 6-phosphatase transporter
Liver

Answer 10

Von Gierke Disease

Question 11

Type IIa
Lysosomal acid maltase
Skeletal & Cardiac Muscle

Answer 11

Pompe Disease