FINAL! - Test 3 Tiff Flashcards
nursing care management for a child with congenital adrenal hyperplasia
- of major importance is recognition of ambiguous genitalia and diagnostic confirmation in newborns
- cortisol and aldosterone replacement are the treatments
- during stressful situations cortisol disagree must be tripled to accommodate the body’s increased need for glucocorticoids. failure to meet this requirement will precipitate an acute crisis. overdose appears as cushingoid signs
- sudden termination sof ht drug because of inadequate supplies, places the child in danger of an acute adrenal crisis. teach parents to always have a spare supply of medication.
- undesirable side effects of cortisone include gastric irrigation, increased excitably and sleeplessness, weight gain, occasionally behavioral changes.
- infants are especially prone to dehydration and salt-losing crises, parent need to be aware of signs of dehydration.
Management of Hirschsprung disease?
- Diagnosis made through identification of aganglionic sections of colon with rectal biopsy.
- Treatment consists of temporary colostomy with later endo-rectal pull through surgery
fluid maintenance calculation
100 ml for each of the first 10kg = up to 1000 ml
50ml for each kg 11-20 = up to 500 ml
20 ml for each additional kg
Primary causes of Diabetes Insipidus are
__________ or __________ and secondary causes can be __________, ________, & ___________.
familial or idiopathic
Tumors, infections and Vascular anomalies
Vision loss in child (not a question, just an informative card :) )
Nurses have a major role in minimizing the effects of temporary loss of vision. They need to talk to the child about everything that is occurring, emphasizing aspects of procedures that are felt or heard. They should always identify themselves as soon as they enter the room and before they approach the child.
Encourage the parents to room with their child and participate in the care. Familiar objects, such as a teddy bear or doll, should be brought from home to help lessen the strangeness of the hospital. As soon as the child is able to be out of bed, orient the child to the immediate surroundings. If the child is able to see on admission, this opportunity is taken to point out significant aspects of the room. Encourage the child to practice ambulating with the eyes closed to
If a metabolic crisis is not treated, a child with CPT1A arctic variant can develop:
low blood sugar (hypoglycemia) high levels of ammonia in the blood breathing problems seizures coma, sometimes leading to death
Signs and symptoms of Hirschsprung Disease?
- Neonate: delayed passage of meconium, poor feeding, bilious emesis and abdominal distension
- Infant: infrequent stools failure to thrive, distended abdomen, diarrhea and vomiting
- Child: encopresis, constipation, foul smelling stools, difficulty toilet training, visible peristalsis and palpable fecal masses
Nephrotic Syndrome (Nephrosis)
Massive proteinuria, hypoalbuminemia, hyperlipidemia and edema
normal:
ph?
pCO2?
HCO3?
ph: 7.35 - 7.45
pCO2: 35 - 45mmHg
HCO3: 22 - 26 mEq/L
lab values for a child with appendicitis
- The WBC count becomes elevated
- Elevated C-reactive protein (CRP)
Nursing objectives for a child with visual impairment
The nursing care objectives in either situation are to (1) reassure the child and family throughout every phase of treatment, (2) orient the child to the surroundings, (3) provide a safe environment, and (4) encourage independence.
Nursing goals for an infant with a myelomeningocele
*
- Infection prevention
- Avoid using latex as infants w/ myelomeningocele have a high risk of developing latex allergy
- Daily head circumference measurements ( high risk for hydrocephalus)
- Cover with sterile gauze or tegaderm
hypotonic dehydration
Greater loss of Na+ than water causing hypotonic serum
Fluid shifts from intravascular to interstitial space causing signs of severe dehydration
May cause shock
Serum Na+ <130
Causes: vomiting, diarrhea, inappropriate fluid administration
Ketoacidosis Treatment
- Administration of Bicarb - reduce acidosis and protect heart muscle
- Kusmal breaths to breathe off C02
- Hydration - (dehydrated b/c they are over saturated with sugar)
- Insulin (after hydration)
Parent teaching for an infant in a Pavlik Harness
*
- Harness should not be removed until provider says its ok
- 23hrs a day and then off for an hour to bath
- Parents should not adjust harness
- Parents should assess child’s skin at least 2-3 times daily for red areafs or skin irritation in skin folds under the straps
- Gently massage healthy skin under the straps once a day to stimulate circulation
- Always place diaper under straps
- Encourage parents to hold the infant with harness and continue care and nurturing activities
treatment of dehydration
- Restoration and maintenance of intravascular volume and systemic perfusion
- Initial therapy focuses of treating or preventing shock
- Mild dehyration may be treated with oral fluid replacement
- For moderate to severe shock must have vascular access - Replacement of fluid and electrolytes
-Fluid replacement with isotonic fluids
=NS or LR usually first choice
=May require colloids if intravascular dehydration not responsive to fluid bolus - Provision of maintenance fluid
- Supportive care
-Monitor respirations
=May be inadequate if child is tachypneic or acidotic
-Monitor electrolytes, glucose, urine output
- Weight
-Vital signs
- If the child’s condition is deteriorating early vital sign changes will be heart rate and respirations.
-Blood pressure is usually the last vital sign to change as child’s condition worsens.
-Also assess: color, perfusion, activity, responsiveness, feeding behavior
What causes hypothyroidism?
Thyroid-stimulating hormone(TSH) deficiency
What is Greenstick fracture:
*
- bone bends causing an incomplete fracture
- kids are more prone bc there bones are soft
post op care of an infant with imperforate anus:
- monitor the skin for signs of infection
- the preferred position is side-lying prone position with the hope elevated
- keep the anal surgical incision clean and dry
- maintain IV fluids unti gi motility returens
- provide care for colostomy if present
- a new colostomy stoma may be red and edematous, but should decrease with time
- instruct parents ot performa anal dilation is prescribed to achieve and maintain bowel patency
lab changes in a child with frequent emesis
- low potassium
- metabolic alkalosis
What is precocious puberty?
Development of secondary sexual characteristics before age 8 in girls and age 9 in boys. Precocious puberty is a normal variant in 80-90% of girls and 50% of boys.
The principal disorder of posterior pituitary hypofunction is _____________ which is an under secretion of antidiuretic hormone (ADH), or vasopressin (Pitressin), and producing a state of uncontrolled diuresis
diabetes insipidus
Therapeutic management of a child with muscular dystrophy
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- No effective treatment has been established
- Primary goal is to maintain function in unaffected muscles as long as possible
- Keep the child as active as possible
- Range of motion, bracing, performance of activities of daily living, surgical release of contractures as needed
- Genetic counseling for the family
Causes of hypoglycemia is diabetic kids
- Increased activity
- Decreased nutrition
- GI sickness
- Infection
Nurse assesses a child with suspected cerebral palsy
*
- Child doesn’t smile
- Weak head control
- Persistent Moro Reflex (startle reflex)
- Gags or chokes while eating
- Kids not meeting developmental milestones
palliative care:
- palliative care for children is the active total care of the child’s body, mind, and spirit and involves giving support to the family.
- it begins when illness is diagnosed and continues regardless of whether or not a child receives treatment directed at the disease.
- health providers must evaluate and alleviate the child’s physical, psychological, and social distress
- effective palliative care requires a broad multidisciplinary approach that includes the family and makes use of available community resources; it can be successfully implemented even if resources are limited.
- it can be provided in tertiary care facilities, in community health center, and even in children’s homes
arctic variant CPT1A nursing considerations
for babies and young children, caregivers must monitor and intervene when food has been lacking for long periods. Hirschfeld, a pediatrician, and other health providers have been spreading information for years about how to prevent complications like seizures — caregivers should make sure the babies and children take in breast milk, formula or other glucose-containing liquids, by intravenous means if necessary, according to the advice.