Final Study Guide Flashcards
Causes of JIA?
Genetic predisposition with external trigger
Systemic JIA
4-17%
Male=female
**Fever! 1-2x/day (at least 2 weeks)
Rash
Systemic signs
Polyarticular JIA
2-28%
>= 5 joints
-large and small joints
- symmetrical
- swollen +warm
- female > male (rarely red)
Two types RF + and RF -
RF+
Onset= 2-4 and 6-12
Nodules on
Elbows, tibial crest and fingers
RF-
Late childhood ; adolescence
Most common type of jIA
Oligoarticular
Oligoarticular JIA
27-56% most common
Less than or equal 4 joints
- female> male
- swollen + warm: not always painful
- systemic signs uncommon
Primary issues of JIA
Swelling
Pain
Weakness
Systemic
Secondary issues of JIA
Contracture Fatigue Aerobic Osteopenia Participation restriction
JIA joint issues in acute
Inflammation
effusion
Lig laxity
Instability
Joint issues in JIA in subacute +chronic
Synovial hypertrophy
Joint erosion
Loss of alignment
OI Type 1 presentation
Mild-mod bone fragility Few-several fx before puberty No bone malformation Normal height/weight Lift avg lifespan: Blue sclera, triangle face, hearing loss (20-30)
OI Type 2 presentation
Perinatal fatal Extreme fragility Long bones =crumbled Small+short Curved Deformed
OI Type 3 presentation
Autosomal dominant usually Short Progressive deformity Severe fagility 10s-100s of fx. Blue sclera (lessens with age)
OI Type 4 presentation
Mild- mod deformity Short (after birth) Dentiogenesis (teeth) Variable hearing loss Ambulation potential =excellent
OI Type 5 presentation
Autosomal dominant Hypertrophic calcification Surgical osteotomies Limited supination+pronation -$calcification of IM
OI Type 6 presentation
Autosomal recessive
- RARE
- mod -severe deformity
OI Type 7 presentation
Autosomal recessive
—issue =translation of collagen
- mod-severe fragility
- humerus+femur short
OI Type 8 presentation
Autosomal recessive
—issue =translation of colagen
-flattened long bones
- skinny ribs
- small head
- growth deficiency (teenage survivors)
What should be included in exam of OI?
- Pain: FLACC
- caregiver handling
- AROM — never PROM
- strength - via observation
Gross motor- PDMS-2, PEDI, Bayley
Sitting @10 mo in OI
Good predictor for future walking
Contraindication of OI
pROM Baby walkers Jumping seats Pull to sit Grabbing by arms/legs
PT intervention of OI infants
Education on proper handling/positioning -avoid forces to long bones -loose clothing -bathe in padded plastic bin -infant carrier for household mobility -may need car bed Aquatic therapy more than or equal 6mo
Pt positioning in OI infants
Sidelying= support with towels Prone=initiate with infant on caregivers chest Supine= arms+knees supported Change position frequently —dont restrict natural movement Prevent contractures +deformity