Diagnostic criteria

Question 1

Chronic exertional compartment syndrome

Answer 1

5 min exercise to tolerable pain

1) pre > 15
2) 1 min post > 30
3) 5 min post > 20

Question 2

Chronic regional pain syndrome

Answer 2

1) Pain
2) sudomotor
3) vasomotor
4) motor

Question 3

Polyarteritis nodosa

Answer 3

1) Wt loss > 4kg
2) BUN > 40 mg/dl; Cr > 1.5 mg/dl
3) DPB > 90 mmHg
4) angiographic evidence
5) histologic evidence
6) livedo reticularis
7) polyneuropathy/mononeuropathy
8) leg pain
9) groin pain/testicular pain
10) hepatitis B

Question 4

Giant cell arteritis

Answer 4

1) Age > 50
2) new headache
3) temporal artery abnormality pain, thrombosis
4) ESR > 50 mm/h
5) biopsy positive

Question 5

Takayasu arteritis

Answer 5

1) Age < 40
2) BP difference > 10 mmHg
3) diminished pulse
4) claudication
5) bruit
6) angiographic evidence

Question 6

Marfan’s

Answer 6

1) Ao Z >/= 2 + Fbn1
2) Ao Z >/= 2 + ectopia lentis
3) Ao Z >/= 2 + score >/= 7
4) Fbn1 + ectopia lentis
5) FHx + score >/= 7
6) FHx + ectopia lentis
7) FHx + Ao >/= 2

Question 7

Ghent score

Answer 7

1) thumb wrist (3)
2) pectus carinatum (2); excavatum (1)
3) protusio acetabulum (2)
4) hind foot deformity (2); flat only (1)
5) dural ectasia (2)
6) pneumothorax (2)
7) long torso
8) striae
9) mitral valve
10) myopia
11) decreased elbow extension
12) scoliosis
13) facial score 3/5: enopthalmos, mallar hypoplasia, dolichocephaly, downslanting eyes, retrognathia

Question 8

Vascular Ehler Danlos

Answer 8

MAJOR

1) translucent skin
2) uterine rupture
3) intestinal rupture
4) arterial rupture
5) easy bruising
6) facial features

MINOR

1) pneumothorax
2) carotid cavernous fistula
3) hypermobile
4) varicosity
5) tendon rupture
6) family history
7) acrogeria
8) club foot

Question 9

Cogan’s syndrome

Answer 9

1) vestibulo-auditory symptoms
2) systemic vasculitis
3) interstitial keratitis

Question 10

Behcet’s

Answer 10

1) genital aphthosis
2) ocular lesions
3) oral aphthosis
4) skin lesions
5) vascular lesions
6) pathergy test

Question 11

Neurofibromatosis-1

Answer 11

two of

1) Cafe au lait > 5mm x 6
2) Neurofibroma x 2
3) Freckling of arm pit or groin
4) Lisch nodules x 2
5) bony lesion, pseudoarthrosis
6) FHx

Question 12

Buerger’s

Answer 12

1) Age < 45
2) Smoking
3) Distal ischemia
4) Angiographic finding
5) exclusion of others