DEVELOPMENTAL DYSPLASIA OF THE HIP Flashcards
DDH
abnormal development of the hip resulting in dysplasia and possible displacement/subluxation of the coxofemoral joint due to capsular laxity and some mechanical issues.
Development abnormality
bony structures (proximal femur and acetabulum), labrum, joint capsule and soft tissue
Crucial – an early diagnosis
Ultrasonography
Screening
Minimal treatment techniques to lower morbidity and fast recovery
ANATOMY
Normal development of the hip – depends on :
- Normal growth of the triradiate cartilage
- Bone ossification nuclei of the acetabulum (ilion, ischion and pubis)
- A spherical femoral head and congruency with the acetabulum (centered)
At birth– cartilaginous structures:
acetabulum
entire femoral head
femoral neck - partially
greater trochanter
FISIOPATHOLOGY
Presure ↑↑ on the cartilaginous FH ► ↓ blood perfusion► necrosis of the chondrocytes
Affects FH and growth cartilage
Doesn’t affect the greater trochanter (normal dimensions)
Muscular imbalance :
Deteriorates growth and morphology of the proximal femur
Contracture of the adductors
Improper function (weakening) of the abductors
ETIOLOGY
Multifactorial
- Laxity of the ligaments and capsules
- Race – caucasians – a smaller acetabulum
- In utero position (20%)
- Oligohydramnios
- Sex (80% - females)
Genetic susceptibility
History - x 10 incidence in children with DDH parents
- twins - 34% (monozygotic)
EPIDEMIOLOGY
Incidence
Most frequent pediatric orthopedic issue in newborns
dysplasia - 1:60-100
luxation (displacement) - 1:1000
Barlow – instabilitaty 1 out of 60 nb.
60% get stable during the first week and stabile 80% up to the age of 2 months (0,2% remain with residual hip dysplasia)
EPIDEMIOLOGY
localization and demographics
Localization
- Most frequent in the left hip of girls
- Bilateral in 20%
Demographics
Frequent in Native Indians, Laplanders, Balcans (Romania – unknown incidence)
Rare in africans
PROGNOSIS OF DDH
Diagnosed early and properly – very good prognosis
Treatament by closed reduction - prognostic bun
Failure of conservative treatment – open reduction – uncertain prognosis, at least good for a short term
According to R. Graf - DDH diagnosis during the first 14 days of life and a proper treatment (ultrasound) – healing up to 3 months of life
Ortolani (Le Damany,1912) sign
Out of 3 cases only one develops DDH
Hip abduction (45-60°), pushing the greater trochanter→ FH centers
Barlow’s sign
Adduction and pressure on the knee and inner thigh→ FH exits the acetabulum
CLINICAL EXAM
other signs
- Galeazzi
- Limited abduction
- Piston sign
- Lumbar Hyperlordosis
- Gluteal/inguinal fold assimetry
- Trendelenburg sign and walking (insufficiency of the pelvitrochanteric muscles)
IMAGISTICS
Hip ultrasound–Graf (most used), Harcke
Recommended – SCREENING (and clinical exam)
CLASSIFICATION AFTER GRAF
CENTERED HIP TYPE I
NORMAL
Type I: • α angle ≥ 60º, β < 77º
• stable hip
(Ortolani and Barlow negative)
High risk hip -> surveillance
Type I: • α ≥60º
• familial history positive
CENTERED HIP TYPE II – ß < 77º
Type II a : • acetabular dysplasia (0 – 3 months)
• α = 50º - 59º
medical surveillance
Type II b : • acetabular dysplasia (3 – 12 months)
• α = 50º - 59º
Pavlik harness
Type II c : • acetabular dysplasia (0 – 12 months)
• α = 43º - 49º
palster casting in human position
DECENTERED HIPS TYPE D, III & IV
Type D • α = 43º - 49º
• ß > 77º
• eversed labrum
Type III a and b • α < 43º Type IV • α < 43º • inversed labrum
adductor tenotomy
open reduction Ludloff /Smith-Petersen and
plaster casting
Other imagistic exams
- Xrays
- Artrography
- MRI
- CT/CT-3D – not useful
NATURAL EVOLUTION OF DDH
Untreated cases of DDH may ↓ Instability ↓ Degenerative changes present in teenagers ↓ Severe degenerative changes ↓ Osteoarthritis (early hip surgery)
TREATAMENT OF DDH
Conservative (according to R. Graf)
Phase
1.Reduction -Decentered hips(D,III,IV) - Manually,by extension,Pavlik
2.Retention - Unstable hips ( IIc unstable) - Human position,plaster according to f..
3.Maturation - Stable ‘‘dysplastic’’ hips ( IIc stable,IIb,IIa-) - Harness according M.Graf/Pavlik
Frejka pillow
a pillow splint used for abduction and flexion of the femurs in treatment of congenital hip dysplasia or dislocation in infants.
Pavlik harness
a support device used to immobilize a body part or hold it in position.
Pavlik harness a device used correct hip dislocations in infants with developmental dysplasia of the hip, consisting of a set of straps that hold the hips in flexion and abduction.
Surgery
- Adductor release (tenotomy)
- Open reduction
- Derotation osteotomies
- Acetabuloplasties
- Arthroplasties
Open reduction and pelvic osteotomies
Salter, Pemberton, Dega, Hopf, Steel, Ganz, Chiari, Dial, Shelf, etc.)
CONCLUSIONS
Early diagnosis, early treatment
US Screening + clinics
Healing up to 3 months of age
Untreated – LLD (limb length discrepancies), limping, hip pain and early osteoarthritis
Even if treated properly hip arthritis is not excluded (especially for late treatment)