Cystic Fibrosis

Question 1

What is cystic fibrosis

Answer 1

It is a genetic disorder that affects the lungs, pancreas, liver, intestine and reproductive organs- viscous sputum, chest infection and malabsorption

Question 2

What is the treatment of cystic fibrosis

Answer 2

Prevent lung infection and maintain lung function

Mucolytic: dornase Alfa
-aids clearance of mucus or sputum from the lungs

Long term antibacterial considered to suppress chronic staph. Aureus

Nutrition and exocrine pancreatic insufficiency: pancreatin. Replace pancreatic enzymes

Monitor patients for liver disease, diabetes and bone density