Cystic Disorders of the Bile Duct Flashcards
Where are cystic disorders of the bile duct most common?
East Asia (incidence 1 in 13,000
What are Type I choledochal cysts?
cystic, fusiform, saccular extrahepatic biliary dilation
What are Type II choledochal cysts?
extrahepatic biliary diverticulum (supraduodenal)
What are Type III choledochal cysts?
dilation of extrahepatic intraduodenal biliary tree (choledochocele)
What are Type IV choledochal cysts?
A) intra and extra-hepatic saccular/cystic dilations, B) multiple extrahepatic cysts
What are Type V choledochal cysts?
Caroli disease, intrahepatic biliary cust
What is the classic triad of symptoms described for children with choledochal cysts and what percentage present with this triad?
abdominal pain, jaundice, palpable abdominal mass; 10-15%
What is the reported incidence of hepatopancreaticobiliary cancers in patients with choledochal cysts?
2.5-26%
Which choledochal cyst types have the highest risk of malignancy?
Types I, IV, and V
What are contraindications to operative management of choledochal cysts?
severe portal hypertension, uncorrected coagulopathy, and end-stage liver failure
What is the surgical treatment of choice for type I choledochal cyst?
45-60cm Roux-en-Y end to side hepaticojejunostomy
What is the treatment for Type II choledochal cysts?
simple cyst excision
What are treatment options for patients with Type III choledochal cysts?
Endoscopic sphincterotomy; complete excision via lateral duodenotomy, excision of the cyst, sphincteroplasty between bile duct mucosa and duodenal mucosa; pancreaticoduodenectomy if malignancy is suspected
What is the surgical treatment of choice for Type IVA choledochal cysts?
Unilateral cystic disease-hepatic lobectomy +hepaticojejunostomy; bilobar disease-complete extrahepatic excision, biliary enteric bypass, drainage of intra-hepatic biliary tree with bilateral silastic stents
What is the surgical treatment of choice for Type IVB choledochal cysts?
complete extrahepatic ductal excision with Roux-en-Y hepaticojejunostomy