cyanotic heard disease

Question 1

tricuspid atresia

Answer 1

Left axis deviation, small R waves in V1-V3, if ASD peaked p waves
hypoplastic RV, underdev of pulm value and/or artery
decreased pulm markings on cxr
ASD or VSD needed for survival

Question 2

complete atrioventricular canal defect

Answer 2

downs
cxr: increased pulmonary markings, cardiomegaly from excessive pulm blood flow
bientricular volume overload

Question 3

ebsteins anomaly

Answer 3

malformed tricuspid displaced into RV
severe triC regurg, RA enlargement
tall P waves and R axis deviation
extreme cardiomegaly
maternal lithium use

Question 4

tetralogy of fallot

Answer 4

boot shaped heart
pulmonary stenosis, VSD, overriding aorta, RV hypertrophy
cxr: paucity of vascular markings
RV axis deviation

Question 5

total anomalous pulmonary venous return

Answer 5

pulmonary venins return to RA
RA and RV enlargement
cxr: increased pulm markings

Question 6

truncus arteriosis

Answer 6

degeorge
normal ECG
cxr: cardiomegaly, increased pulm markings

Question 7

transposition of great arteries

Answer 7

pda needed for circulation