Congenital Heart Diseases

Question 0

Schmitar syndrome

Answer 0

Snowman appearance
Hypo plastic lung
Pulm vein drain into ivc

Question 1

All asd should be closed

Answer 1

If the RV begin to dilate

Question 2

Fontan

Answer 2

For tricuspid atresia

Watch for anemia

Question 3

Coarctation

Answer 3

Collaterals or gradient more than 20 mm need surgery

Question 4

Tetralogy

Answer 4

May develop low pressure severe PR pt may not have a pulmonic valve mat have severe PR which may interfere with fontan

Question 5

Deferential cyanosis

Answer 5

PDA

Question 6

Down

Answer 6

Trisomy 21

Asd primum, vsd, TOF

Question 7

Turner

XO

Answer 7

Coarctation.

Question 8

Turner

XO

Answer 8

Bicuspid valve

Ascending aneurysm in 50%

Question 9

Marfan

Answer 9

Aortic root use ARB, statin

Greater than 6 ___30% risk of rupture

Question 10

Noonan

Answer 10

Web neck

Peripheral pulm stenosis

Question 11

Root bicuspid

Answer 11

Surgery>5.5
Family history,expansion >5.0..

Dietz/ loeys bifid uvula surgery for 4.5 Aldo look for cerebral aneurysm

Question 12

Eisenmenger

Answer 12

Ps may be protective 
Bleeding 
Air thromboembolic
CHF 
Arrhythmia 
Hyper uricemia
Watch for anemia and ferritin

Question 13

Sudden death

Answer 13

HOCM
Commotio cordid
Anomalous coronary

Question 14

Infective endocarditis

Answer 14

Prosthetic valves
Previous IE
Cyanotic heart disease

Question 15

Fontan

Answer 15

Tricuspid atresia ivc to PA .
It duesnt work well with afib, thrombi,
Protein losing enteropathy

Question 16

Glen and bidirectional Glenn

Answer 16

Bypassing ivc SVC to PA

Question 17

Asd

Answer 17

Fishhook appearance on the r wave on the EKG
Chambers enlarge RA RV and pa
PDA RV and RA are spared

Question 18

Sinus node dysfunction

Answer 18

SVC obstruction
SA node dysfunction
Afib

Question 19

AV septal defect

Answer 19

EKG
First degree AV block
RBBB lafb
CHB

Question 20

Asd closure

Answer 20

RV enlargement
Paradoxical emboli
Orthodeoxia
Pa pressure less than2/3 systemic

Question 21

Vsd

Answer 21

Louder the murmur with thrill less serious it is

Vsd only peri membranous cN be fixed with closure device

Question 22

Vsd closure

Answer 22

Shunt less rhAn 1.5 and pap less than 2/3 systemic

If there is LV dysfunction

Question 23

PDA

Answer 23

If you can hear the murmur fix it

Question 24

Tof

Answer 24

Bla lock taussig, Potts , waterson all create shunts . Watch for low pressure PR there may not be a valve Qrs greater than 180 is bad Lad from RCA in 3-7% of TOF patients CTA is the best for diagnosisp

Question 25

Pulm valve

Answer 25

Only murmur on the right side which decrease on inspiration

Question 26

L transposition

Answer 26

CHB | Ppm difficult to put because if the baffle

Question 27

Transposition D

Answer 27

Arterial switch pa and aorta

Question 28

Congenital coronary stenosis

Answer 28

Rubella Homocysteinuria Supra valvular stenosis

Question 29

High RA pressure

Answer 29

Poor prognostic sign in TR

Question 30

Lower the compliance

Answer 30

Higher the V wave