CH 27 - NEONATAL & PEDIA KIDNEYS & ADRENALS Flashcards

0
Q

THE MOST COMMON CAUSES OF HYDRONEPHROSIS ARE?

A

OBSTRUCTION, REFLUX, OR ABNML MUSCLE DVLPMT

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1
Q

THIS IS THE DILATION OF THE URINARY COLLECTING SYSTEM.

A

HYDRONEPHROSIS

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2
Q

WHAT IS THE MOST COMMON KIDNEY PATHOLOGY IN CHILDREN?

A

HYDRONEPHROSIS

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3
Q

THIS IS THE MOST COMMON TYPE OF OBSTRUCTION OF THE UPPER URINARY TRACT.

A

URETEROPELVIC JCT OBSTRUCTION

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4
Q

WHAT IS THE MOST OFTEN CAUSE OF URETEROPELVIC JCT OBSTRUCTION?

A

INTRINSIC NARROWING OR EXTRINSIC VASCULAR COMPRESSION AT LEVEL OF URETO JCT.

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5
Q

THIS IS THE SONO APPEARANCE THAT WILL SHOW PELVOCALYCEAL DILATION WITHOUT URETERAL DILATION; BEST SEEN CORONALY; THE DILATION WILL BE PROXIMAL TO OBSTRUCTION.

A

URETEROPELVIC JCT OBSTRUCTION

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6
Q

THIS IS AN OBSTRUCTED URETER THAT CAN BE AFFECTED ANYWHERE BETWEEN THE PELVIS TO THE UTV JCT.

A

URETERAL OBSTRUCTION

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7
Q

WHAT IS THE SONO APPEARANCE OF URETERAL OBSTRUCTION?

A

HYDRONEPHROSIS & HYDROURETER WITH A NARROW SEGMENT OF THE DISTAL URETER BEHIND THE BLADDER

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8
Q

THIS IS THE MOST COMMON CAUSE OF BLADDER OUTLET OBSTRUCTION IN MALE NEONATES.

A

POSTERIOR URETHRAL VALVES

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9
Q

BILATERAL HYDRONEPHROSIS IS FREQUENTLY CAUSED BY OBSTRUCTION AT THE LEVEL OF THE ____ OR ______ ______.

A

BLADDER OR BLADDER OUTLET

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10
Q

WHAT IS THE SONO APPEARANCE OF BLADDER OUTLET OBSTRUCTION?

A

THICKENED BLADDER WALLS, “KEYHOLE” APPEARANCE

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11
Q

THIS RESULTS FROM AN ECTOPIC INSERTION AND CYSTIC DILATION OF THE DISTAL URETER OF THE UPPER MOIETY OF A COMPLETELY DUPLICATED RENAL SYSTEM.

A

ECTOPIC UERTEROCELE

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12
Q

ECTOPIC UERTEROCELE IS MORE OFTEN SEEN IN ____ AND ON THE _____ SIDE.

A

FEMALES; LEFT

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13
Q

THE SONO APPEARANCE OF ECTOPIC UERTEROCELE IS?

A

FLUID FILLED MASS WITHIN THE URINARY BLADDER; LOCATED INFEROMEDIALLY TO THE URETERAL INSERTION OF THE LOWER POLE URETER.

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14
Q

THIS IS THE TRIAD OF ABDOMINAL MUSCULATURE, CRYPTORCHIDISM, AND URINARY TRACT ANOMALIES.

A

PRUNE BELLY SYNDROME AKA ABDOMINAL MUSCLE DEFICIENCY SYNDROME

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15
Q

WHAT ARE SOME OF THE URINARY TRACT ANOMALIES THAT CAN RESULT FROM PRUNE BELLY SYNDROME?

A

LG HYPOTONIC DILATED URETERS, LG BLADDER, A PATENT URACHUS

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16
Q

WHAT IS THE SONO APPEARANCE OF PRUNE BELLY?

A

DILATED URETERS AND A HUGE BLADDER & PHYSICALLY THE WRINKLED ABDOMEN

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17
Q

THIS IS THE MOST COMMON CAUSE OF RENAL CYSTIC DISEASE IN THE NEONATE.

A

MULTICYSTIC DYSPLASTIC KIDNEY

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18
Q

THIS IS THE MOST COMMON CAUSE OF ABDOMINAL MASS IN THE NEWBORN (WHEN HYDRO IS EXCLUDED).

A

MULTICYSTIC DYSPLASTIC KIDNEY

19
Q

THIS CAUSES SPORADIC DYSPLASIA DURING THE 1ST TRIMESTER.

A

MULTICYSTIC DYSPLASTIC KIDNEY

20
Q

WHAT IS THE SONO APPEARANCE OF MULTICYSTIC DYSPLASTIC KIDNEY?

A

UNILATERAL “CLUSTER OF GRAPES”

21
Q

THIS DISEASE IS ID IN THE NEONATAL PERIOD, IT IS MOST PREDOMINENT IN FEMALES, RARE.

A

AUTOSOMAL RECESSIVE PKD

22
Q

WHAT IS THE SONO APPEARANCE OF AUTOSOMAL RECESSIVE PKD?

A

BILATERALLY ENLARGED, HYPERECHOIC, MACROSCOPIC CYSTLIKE APPEARANCE.

23
Q

THIS DISEASE APPEARS DURING MIDDLE AGE WITH HYPERTENSION, HEMATURIA, AND ENLARGED KIDNEYS.

A

AUTOSOMAL DOMINANT PKD

24
WHAT IS THE SONO APPEARANCE OF AUTOSOMAL DOMINANT PKD?
BILATERAL WELL-DEFINED CYSTS OF VARYING SIZES.
25
THIS INFECTION USUALLY BEGINS IN THE BLADDER THEN MOVES UP INTO THE RENAL PELVIS. PATIENT WILL PRESENTS WITH SUDDEN FEVER, FLANK PAIN, AND TENDERNESS.
ACUTE PYELONEPHRITIS
26
WHAT IS THE SONO APPEARANCE?
MIXED ECHOGENIC PATTERN WITH ABSCESS
27
THIS RESULTS WHEN REPEATED EPISODES OF ACUTE PYLONEPHRITIS CAUSE THE KIDNEY TO BECOME SCARRED AND DECREASED IN SIZE.
CHRONIC PYELONEPHRITIS
28
WHAT IS THE SONO APPEARANCE OF CHRONIC PYELONEPHRITS?
IRREGULAR OUTLINE, INCREAED ECHOGENICITY OF PARENCHYMA
29
THIS IS MOST LIKELY TO OCCUR IN THE DEHYDRATED OR SEPTIC INFANT & OF A DIABETIC MOTHER.
RENAL VEIN THROMBOSIS
30
RENAL VEIN THROMBOSIS AFFECTS THE KIDNEYS HOW?
UNILATERAL OR BILATERAL ENLARGEMENT, HEMATURIA, PROTEINURIA, AND LOW PLATELET COUNT.
31
WHAT IS THE SONO APPEARANCE OF RENAL VEIN THROMBOSIS?
ACUTE ENLARGED HETEROGENEOUS KIDNEY, ADRENAL HEMORRHAGE, AND CALCIFICATION
32
THIS IS THE MOST COMMON BENIGN RENAL TUMOR OF THE NEONATE.
CONGENITAL MESOBLASTIC NEPHROMA | - IS BENIGN BUT INDISTINGUISHABLE FROM A WILMS TUMOR
33
HOW CAN YOU TELL THE DIFFERENCE FROM A WILMS TUMOR AND A NEPHROMA?
IT IS IN CHILDREN < 1 YEARS OLD.
34
THIS IS THE MOST COMMON MALIGNANT RENAL TUMOR IN CHILDREN > 1 YEAR WITH A PEAK BETWEEN 2-5 YRS OLD.
NEPHROBLASTOMA / WILMS TUMOR
35
DOES A NEPHROBLASTOMA HAVE A GOOD PROGNOSIS?
IF IT IS CAUGHT EARLY; SURGICAL REMOVAL & CHEMO
36
WHAT IS THE SONO APPEARANCE OF A WILMS TUMOR?
VARIABLE, CALCIFICATIONS, HOMOGENEOUS - COMPLEX TEXTURE, POORLY DEFINED, DISPLACED KIDNEY
37
THIS IS A MALIGNANT TUMOR OF THE ADRENAL MEDULLA, IT IS THE 2ND MOST COMMON ABD CHILDHOOD TUMOR (2 MONTHS - 2 YRS).
NEUROBLASTOMA
38
WHAT IS THE SONO APPEARANCE OF A NEUROBLASTOMA?
HIGHLY ECHOGENIC OR COMPLEX, POORLY DEFINED, CALCIFICATIONS, CYSTIC, DISPLACES KIDNEY, LIVER METS
39
THIS IS CAUSED BY A DIFFICULT DLVRY, LG SIZE, DIABETIC MOTHERS, STRESS/HYPOXIA AT DLVRY, SEPTICEMIA, AND SHOCK.
ADRENAL HEMORRHAGE
40
WHAT ARE THE CLINICAL SIGNS OF AN ADRENAL HEMORRHAGE?
ABDOMINAL MASS, JAUNDICE, ANEMIA
41
WHAT IS THE SONO APPEARANCE OF AN ADRENAL HEMORRHAGE?
- OVOID ENLARGEMENT OF THE GLAND, ANECHOIC TO HYPERECHOIC OR MIXTURE, INF DISPLACEMENT OF KIDNEY WITH BLUNTING OF SUPERIOR POLE. - DECREAES IN SZ WITHIN 4-6 WKS
42
WHAT SONO APPEARANCE DOES A NML NEONATE KIDNEYS HAVE?
- LG, HYPOECHOIC MEDULLARY PYRAMIDS (NOT TO BE MISTAKEN FOR DILATED CALYCES OR CYSTS) - THIN, ISOECHOIC OR HYPERECHOIC CORTEX
43
THIS IS PARENCHYMAL TRIANGULAR DEFECT AT SITE OF FETAL LOBULATION.
JUNCTIONAL PARENCHYMAL DEFECT
44
WHAT IS THE SZ NML DISTENDED BLADDER WALL OF A NEONATE & THE NML WALL WHEN EMPTY?
< 3 MM & < 5 MM