Ch 14 Syndromes + Ch 15 Ventricle Lesions

Question 1

What is the goal of the several stage surgical procedures used to “correct” single ventricle defects?

Answer 1

To relieve workload of the single functional ventricle by shunting all deoxygenated return to the lungs

Question 2

What pathology is suspected from this pediatric AP4? Image shows really small LV

Answer 2

Hypoplastic left heart syndrome

Question 3

The inlet variant of HRHS consists of?

Answer 3

Tricuspid atresia

Question 4

During an echocardiogram you encounter this image when you reach the apical window. What do you suspect ? Image shows linear structure in LA

Answer 4

Cor Triatriatum Sinister

Question 5

During an echocardiogram you notice this aberrant flow while evaluating the pulmonary valve + pulmonary artery in PSAX at the level of the AoV. What pathology could you suspect. Image shows red jet flowing into PA

Answer 5

ALCAPA

Question 6

During an echo you notice this aberrant flow while zooming up on the AV in PSAX. What do you suspect? Image shows blue jet flowing into PA

Answer 6

ARCAPA

Question 7

During an echo you encounter this image when you reach the apical window. What pathology do you suspect? Image shows linear structure in RA

Answer 7

Cor Triatriatum Dexter

Question 8

What is the most severe variant of HLHS?

Answer 8

Aortic atresia with mitral atresia

Question 9

With the outlet variant of HRHS you would expect to see ___?

Answer 9

RVH due to an atretic pulmonary valve

Question 10

A patient presents to the echo lab with history of fever longer than 5 days, rash, conjunctivitis and a red tongue/lips. At PSAX level of AoV you visualize this when you zoom up on the Ao. What do you suspect? Image shows LCA aneurysm

Answer 10

Kawasaki’s disease