Cerebral Palsy Flashcards

1
Q

Cerebral Palsy

Definition

A

A group of permanent disorders of the development of movement & posture causing activity limitations that are attritbuted to non-progressive distrubances that occurred in the developing fetal or infant

The motor disorders of cerebral palsy are also accompanied by disturbances of sensation, perception, cognition, communication, and behaviour by epilepsy & by secondary MSK problems
- Can all occur b/c brain injury - depends on type & where in the brain

LESION = non-progressive BUT impairments progress & become more apparent

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2
Q

CP: Etiology & RF

(8)

A

Multifactorial d/t static lesion in the developing brain - also linked w/ PVL (Periventicular Leukomalacia) = form of white matter disorder

RF
1. Prematurity - INC risk d/t difficulty w/ ventilation - inadequate O2 & CO2 gas exchange
2. Atypical Intraurterine Growth (low/high birth weight)
3. Infection (in utero & post-natal)
4. Infarction - INC risk of stroke in utero (neonatal period) w/ mothers who are: obese, older, fmaily Hx of thembo/metabolic disease
5. Developmental defect (ie. lissencephaly - smooth brain - lacks folds & microcephaly (small brain))
6. Multiple Gestation - more babies in womb = INC risk for at least one or all
7. Placental Pathology - malfunction or inflammation fo placenta
8. Trauma (pernatal, perinatal - during birth, early post-natal - could be d/t shaken baby syndrome)

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3
Q

What is the most prevalent type of CP?

A

Spatic type CP

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4
Q

Types of Classifications

(2) + 2

A

Classification by Impairment
Anatomic Distribution - “where”
- Hemiplegia
- Diplegia
- Quadriplegia
Type of Impairment
- Spastic
- Dyskinetic
- Mixed

Classification by Function
- Gross Motor Function Classifciation System (GMFCS)

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5
Q

Classification by Impairment

(4)

A

Hemiplegia
- One side of the body is affected (similar to stroke)

Diplegia
- The legs are more affected than the arms

Quadriplegia
- Arms, legs, and trunk are affected

Asymmetrical diplegia
- The legs are more affected than the arms & one side of the body is more affected than the other

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6
Q

Type of Impairment: Spastic

Describe (5)

A

Spastic - specific type of HYPERtonia
- Velocity-dependent resistance to passive elongation
- Damage to cortex or white matter to & from sensorimotor cortex
- Most common type of CP
- DIPLEGIA most common distribution of spastic CP
** Scisooring gait - Adductor spasticity kicks in & they start crossing their legs over
** Toe walking - PF b/c of spasticity

POSTURAL INSTABILITY

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7
Q

Type of Impairment: Dyskinetic:
Ataxic

Describe (2) & Part Affected

A

Ataxic
- Movement disorder characterized by intention tremor, lack of mm control, and poor coordination of voluntary movements
- Most children with ataxis CP can walk without gait aid, but may have difficulty with balance

CEREBELLUM is affected

1 of 3 sub-categories of DYSKINETIC

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8
Q

Type of Impairment: Dyskinetic:
Athetosis

Describe (4) & Part Affected

A

Athetosis
- Movement disorder characterized by slow, continuous, involuntary writhing (contusion of body parts // continuous twisting & squirming mvmts) movments
- Commonly affects the distal extremities & mouth)
- Difficult to maintain a stable posture
Legs are also ER (valgus) & twisting which makes balancing difficult > torso rocks around in an attempt to compensate
- Significant limitations in gross motor function

2/3 sub-categories of DYSKINETIC

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9
Q

Type of Impairment: Dyskinetic:
Dystonic

Describe (2+3) & Part Affected

A

Dystonic

Dystonia (INVOLUNTARY mm contractions):
- A movement disorder that is characterized by involuntary sustained or intermittent mm contractions leading to repetitive mvmts, abnormal fixed postures, and disordered tone

Dystonic Posturing:
Co-contraction (involuntary) of muscles causing sustained abnormal posture

  • Dystonic movements are typically patterned & may included twisting or tremulous movement (tremor)
  • Often triggered by voluntary movement
  • Significant limitations in gross motor function & fatigue due to high metabolic demand

*THALAMUS is damaged - relay center &/or BASAL GANGLIA (putament or caudate nucleus)

3/3 sub-cateogires of DYSKINETIC

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10
Q

Type of Impairment: Mixed

Describe

A

Mixed
- Combination of dyskinetic & spastic
- Diffuse brain injury to motor cortex & the basal ganglia

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11
Q

Classification by Function:
Gross Motor Function Classification System (GMFCS)

A

More objective measure - can be used to communicate the severtiy of the disease (clinically & for research)

Focused on what the child CAN do in regard to self-mobility

  • 5-level (I-V) classification system that described gross motor functin (regardless of the type of CP - applied to all types)
  • 5 Age Groups:
    1. 0-2
    2. 2-4
    3. 4-6
    4. 6-12-12-18
  • Scale is considered stable after the age of 2
  • Child is classified by the method of mobility
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12
Q

Gross Motor Function Classification System (GMFCS) - General Headings for each level

A

Level I - Walks without limitations
Level II - Walks with limitations
Level III - Walks Using a Hand-Held Mobility Device
Level IV - Self-mobility w/ Limitations; May Use Powered Mobility
Level V - Transported in a Manual W/C

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13
Q

Gross Motor Function Classification System (GMFCS):
Level I

(3)

A
  • Walks w/o restrictions
  • Limitations in more advanced gross motor skills (runing, jumping)
  • DO NOT need a mobility aid
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14
Q

Gross Motor Function Classification System (GMFCS):
Level II

(2)

A
  • Walks w/o devices
  • Limitations in walking outdoors & in the community (inclines, crowds, uneven surfaces)
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15
Q

Gross Motor Function Classification System (GMFCS):
Level III

(2)

A
  • Walks with mobility devices
  • Limitations in walking outdoors and in the community
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16
Q

Gross Motor Function Classification System (GMFCS):
Level IV

(2+1)

A
  • Self mobility with limitations
    Walks very short distances w/ use of aid
  • Children are transported OR use power mobility outdoors & in the community
17
Q

Gross Motor Function Classification System (GMFCS):
Level V

(3)

A
  • Self-mobility is severely limited even with the use of supporting technology
  • NO means of independent mobility
  • Completely dependent
18
Q

Associated Impairments

(6)

A
  1. Cognitive impairments
  2. Sensory impairments
  3. Behavioural problems
  4. Speech & language
  5. Perceptual dysfunction
  6. Problems with motor planning (apraxia)
    All housed in the cerebral cortex

DEPENDs on where the brain damaged occurred
Most of these will be seen in SPASTIC CP - b/c insult occurred in the Sensiomotor cortex (cerebral cortex)

Cognition will not be seen w/ THALAMUS insult - not connected

19
Q

What is the most common distribution of Spastic CP?

A

Diplegia

20
Q

CP: Assessmet

2 Types

A

Motor Function
1. GMFM-88 > Gross Motor Function Measure
2. GMFM-66 - subset of 88 provides a more concise way of completing test
- Less time to complete & provides more detailed info of the lvl of difficulty of each item = more info to help create goals for the child
** GOLD STANDARD measure of motor function for children w/ CP

Spasticity:
- Modified Ashworth Scale
- Modified Tardieu Scale

21
Q

GMFM-88 & GMFM-66

Decription & Details

A

Observational instrument to measure change in gross motor function of children w/ CP
- Valid from 5 months-16 years old
- Appropriate for children whose motor skills are below or equal to a 5-year old w/o any motor disability

5 Dimensions:
1. Lying & rolling
2. Crawling & kneeling
3. Sitting
4. Standing
5. Walking, running, jumping

Higher score is better

GMFM-88 is also validated for Down Syndrome
TUG is also reliable w/ CP children

22
Q

AFOs commonly used with CP

(3)

A

Solid AFO
- Blocks all ankle mvmt at both talocrural & subtalar - locked in position (M-L instability)
- A rocker bottom shoe is often used in conjunction w/ a solid AFO to assist in gait
- Limits knee extension moment (DEC knee hyperextension)

Used:
- Post-Sx/ botox to protect mm
- Excessive DF
- Correctable equinus (foot can be passively moved)

Not Used:
- Crouch gait
- Fixed foot deformity

Hinged AFO
- Allows for a controlled amount of DF while still limiting PF
- Facilitates progression to foot-flat position in early stance
- Limits movement at subtalar
- Limits knee extension moment (DEC knee hyperextension)
Good for true equinus w/ a flexible foot b/c it takes them out of knee hyperextension

Used:
- Same as solid AFO: drop foot or subtalar joint OA

Not Used:
- Crouched gait
- Fixed equinus/ deformity
- Not appropriate if they just had a BOTOX injection or lengthening procedure

Ground-Reaction AFO (GRAFO)
- Blocks movement at talocrural joint & limits movement at subtalar joint
- Provides knee extension movement (INC knee extension)
ANTERIOR shell < blocks tibia from translating forward = prevents excessive knee flexion

Used:
- Good for gaits that have excess knee FLEX - want to take them out of knee flex. Ex. crouch gait, weak quads (poor eccentric control), overlengthened gastroc mm

Not used:
- FIXED hip or knee FLEX - will be painful

23
Q

Medical Intervention

(8)

A

Bony Alignment (osteotomy & fusion)
- De-rotation osteotomy
- Fusion

Botox Injection
- Reduces spasticity (lasts ~3 months)
- Neuromuscular block of Ach / Trade-off = DEC mm strength

Intramuscular Baclofen
- Reduces spasticity

Selective Dorsal Rhizotomy
- Reduces spasticity
- Cutting dorsal root at SC

Serial Casting
- INC ROM

Soft Tissue Lengthening (mm & tendon) & Tendon Transfer
- INC ROM

Percutaneous mm/tendon release
- INC ROM

Reconstruction
- Hip reconstruction - if involved

24
Q

Interventions - Address the Impairments

(9)

A
  1. Bone development/ deformity
    Hip dysplagia (highly correlated w/ GMFCS Level V), scoliosis (structural or functional - looks like a LLD), & torsions (tibia)
  2. Balance
  3. Coordination
  4. Motor Planning
  5. Range of Motion
    Flexibility - prolonged positions in W/C
    Contractures - can lead to functional limitations (stretching, serial casting, etc)
  6. Strength
  7. Tone
  8. Spasticity
  9. Address participation limitations
    - Transfers, gait, stairs
    - Sports
    - Play

Help become more independent
Teach them how to do these tasks - more involved in participation/ sports
Challenge them to perform functional activities & become better at them & also try to accomodate os they can be included