case 4 part 2 Flashcards

1
Q

what causes pneumothorax in cystic fibrosis patient

A

structural impairments and altered airflow dynamics

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
2
Q

what is a haemoptysis

A

coughing up blood from the bronchial tubes

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
3
Q

what is HFCWO

A

high frequency chest wall oscillations
used when a person is no longer able to effectively clear mucus airway clearance would prevent infection and inflammation - inflammation lead to haemoptysis

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
4
Q

types of medications for cystic fibrosis

A

amoxicillin and clavulacin
digestive tract enzymes- help to produce protein and fat from food

vitmins
reflux medications
inhaled or nebulised medications- break down mucus
oral antibiotics for respiratory illness

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
5
Q

how many types of cystic fibrosis mutations are there

A

5

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
6
Q

clinical presentation of cystic fibrosis

A

wheezing
recurring chest infections
difficulty putting on weight
yellowing of the skin
dioreah ,constimation , lack of break down of mucus
bowel obstruction in new born babies - meconium liens

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
7
Q

what would you hear for occultation on patient with cystic fibrosis

A

crackles and wheezing

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
8
Q

medication commonly used to treat cystic fibrosis

A

kaftrio- treat the underlying causes by heling the lungs work effectively

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
9
Q

diagnosis of cystic fibrosis

A

based on symptoms
genetics
screen tests

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
10
Q

screening test for cystic fibrosis

A

prenatal screning
new born screaning
sweat test

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
11
Q

what is a sweat test

A

diagnosis and screen for cystic fibrosis
test for levels of chloride in the sweat

60 or greater- diagnosis of cystic fibrosis- chloride helps to break down mucus
30-59 unclear diagnosis
less than 30- cystic fibrosis unlikely

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
12
Q

effect of having inadequate surface airway liquid height

A

insufficient levels of the fluid can impair cilia function
individuals with cystic fibrosis have an insufficient sol layer- which causes it to have a sufficient surfactant height
cilia are unable to sweep away thick mucus so it forms a thick mucus plaque where bacteria proliferate leading to chronic infections

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
13
Q

what causes a low sol layer in cystic fibrosis

A

decrease secretion of chloride and water by epithelial cells – resulted in dehydrated mucus

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
14
Q

what is the result of impaired homeostatic regulations in cystic fibrosis

A

leads to dehydrated and acidic ASL

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
15
Q

results of abnormal CFTR protein

A

creates an adverse acidic enviornment
- damages the antimicrobial function and changes the mucus properties and mucus clearance

How well did you know this?
1
Not at all
2
3
4
5
Perfectly