Cardiomyopathies Flashcards

1
Q

On a routine echo, you notice that your patient has a dilated LV, rounded heart, decreased endocardial systolic motion, a large LA, and RV dysfunction. What is your diagnosis? What is the underlying etiology?

A
Dilated Cardiomyopathy
Idiopathic (50%)
Myocarditis
Ischemia 
Chemo agents
How well did you know this?
1
Not at all
2
3
4
5
Perfectly
2
Q

A new pt presents to your office. During he history you learn that her father had a hypertrophic Cardiomyopathy. What does this mean for your pt?

A

Monitor her for hypertrophic Cardiomyopathy via an Echo

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
3
Q

A pt presents with a mid-systolic harsh murmur that worsens with valsalva. An echo shows RVH and LVH. What diagnosis do you suspect? What treatment should you recommend?

A

Hypertrophic Cardiomyopathy
B-blockers (1st line)
Dihydro CCBs (2nd line)
Avoid stress

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
4
Q

A pt present with a mid-systolic murmur that worsens with valsalva. He has arrhythmias and diastolic dysfunction. You suspect hypertrophic Cardiomyopathy which is confirmed with an Echo. What risk are you most worried about?

A

Increased risk of sudden cardiac death

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
5
Q

A pt presents with arrhythmias and diastolic dysfunction. Echo shows signs of hypertrophic Cardiomyopathy. What is the most likely etiology of this disease?

A

Genetic (60-70%) - sarcomere protein mutation
Acquired - HTN, aortic stenosis
LVH, concentric/Apical hypertrophy, normal/reduced LV volume

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
6
Q

What is the pathology behind restrictive Cardiomyopathy?

A

Non- dilated, non-hypertrophic ventricles
Impaired ventricular filling
Biatrial enlargement
RV failure

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
7
Q

What are the 4 types of restrictive Cardiomyopathy?

A

Infiltrative
Non-infiltrative
Storage Dz
Edomyocardial Dz

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
8
Q

How do you treat amyloid restrictive Cardiomyopathy?

A

Transplant, chemo, stem cell transplant

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
9
Q

How do you treat sarcoid restrictive cardiomyopathy?

A

Steroids

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
10
Q

How do you treat endomyocardial restrictive Cardiomyopathy?

A

Warfarin

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
11
Q

How do you treat Fabry’s restrictive Cardiomyopathy?

A

a-galactosidase replacement

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
12
Q

Which type of cardiomyopathy is associated non-dilated, non-hypertrophic ventricles, impaired filling, and biatrial enlargement?

A

Restrictive

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
13
Q

Which cardiomyopathy is genetically linked and characterized by RV free wall fibrosis, regional/global akinesis/dyskinesis, and ventricular arrhythmias?

A

Arrhythmogenic cardiomyopathy

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
14
Q

A pt presents with benign arrhythmias. He has been feeling fine but yesterday after his marathon training his heart felt funny so he came in today to get it checked out. Echo shows symmetric LVH of 15mm and increased LV cavity size and mass. What is the most likely diagnosis?

A

Athlete’s Heart

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
15
Q

What type of cardiomyopathy is associated with endocardial fibroelastosis and LV noncompaction?

A

Unclassified cardiomyopathy

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
16
Q

A 65yo female pt presents with symptoms of MI. Echo shows apical ballooning of the LV during systole. What cardiomyopathy could this be?

A

Takotsubo (Stress-Induced) Cardiomyopathy

17
Q

A 35 yo African American woman presents with her 6 mo old son to the ER. Last month she was treated for heart failure and today her BP is 160/95 despite being on lisinopril and esmolol. What cardiomyopathy could this be? What is her prognosis?

A
Peripartum cardiomyopathy
Prognosis is poor
Transplant (4-7%)
Mortality (6-23%)
Recover (~54%)
18
Q

A pt presents with Wet Beriberi. Echo shows LV dilation, increased Lv mass, and diastolic/systolic failure. What cardiomyopathy does the pt most likely have? What is the treatment?

A

Alcoholic cardiomyopathy

Stop drinking!

19
Q

Which cardiomyopathy can be caused by coxsackie virus, the flu, adenovirus, Chagas, or Lyme?

A

Infectious Cardiomyopathy

20
Q

What can cause toxic cardiomyopathy?

A

EtOH, cocaine, chemo drugs, trace element overload

21
Q

What can cause miscellaneous cardiomyopathy?

A

Tahcycardia, SLE, end-stage renal Dz, celiac’s Dz, autoimmune disorders, endocrine disorders