Blue Baby and CHD Flashcards

1
Q

Hypoplastic Left Heart Syndrome S/S

A

as PDA closes… Hypoxia, acidosis, CV collapse

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
2
Q

Tx order for hypoxic, acidotic 2-10d old baby

A

O2, intubate, Dextrose, PGE, Gentamicin/Ampicillin

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
3
Q

Intraembryonic blood vessels noted at day

A

20

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
4
Q

the median heart tube is completely day

A

Days 21 – 23

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
5
Q

heart starts beating on day

A

22

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
6
Q

fetal circulation begins on day

A

Days 27-29

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
7
Q

ductus venosus shunts blood from

A

umbilical vein -> Inferior Vena Cava allowing oxygenated blood to bypasses the liver

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
8
Q

foramen ovale shunts blood from

A

Right atrium -> Left atrium allowing blood to bypass the lungs

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
9
Q

Ductus arteriosis shunts blood from

A

Pulmonary artery -> Aorta allowing blood to bypass the lungs

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
10
Q

First treatment for a BLUE baby?

A

Oxygen

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
11
Q

Gestational Diabetes increases the risk for

A

Congenital heart defects by 2X

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
12
Q

Umbilical vein PaO2 is 30-35 mmHg.

Fetus 70-80% saturated at this PaO2, why?

A

fetal Hgb functions to deliver O2 at a low O2 concentration

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
13
Q

Fetal Hgb transitions at

A

~6months

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
14
Q

Upon first breath, pulmonary pressure

A

Decreases, blood shifts from left to right

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
15
Q

Upon first breath, systemic pressure

A

Increases, blood shifts from left to right

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
16
Q

Foramen Ovale closes

A

functionally upon first breath, closed by 3 months

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
17
Q

Ductus Arteriosus closes

A

2-3 days post birth, unless CHD is present

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
18
Q

What may cause the Ductus Arteriosus to remain open past 2-3days

A

low O2 tension (hypoxia), PGE

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
19
Q

In the fetus, the normal direction of the shunted blood is

A

Right side -> Left (bypass fetal lung)

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
20
Q

What function does the PDA provide after birth in a baby w/ cyanotic CHD?

A

Provide a source of pulmonary blood flow

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
21
Q

In the neonate, the normal direction of the shunted blood is

A

reverses, Left -> Right

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
22
Q

Pulmonary resistance should drop by _______ in infants

A

6 weeks

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
23
Q

What type of CHD’s present later (closer to 6 weeks)?

A

LEFT-TO-RIGHT shunts (ASD, VSD, PDA)

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
24
Q

What S/S would you find in an infant with Persistent Pulmonary HTN?

A

Difficulty transitioning, differential pulse Ox sat > 10% (O2 sat in UE is normal, LE is low)

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
25
Q

If you have a hole in the heart, what effects shunt flow?

A

Pressure

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
26
Q

Main cause of CHD

A

No specific cause/Multifactorial

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
27
Q

Maternal Gestational diabetes is associated with what CHD?

A

Transposition of vessels, VSD, Coarctation

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
28
Q

Lupus is associated with what what CHD?

A

Complete heart block

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
29
Q

Maternal Rubella infection w/in 1st 7 weeks is associated with what CHD?

A

PDA, septal defects, pulmonary a. stenosis

30
Q

FAS (Maternal EtOH use) is associated with what CHD?

A

50% chance of CHD

ToF; L-to-R shunt

31
Q

Down Syndrome is associated with what CHD?

A

AV canal, VSD

ASD, AV septal defect

32
Q

Turner Syndrome is associated with what CHD?

A

Coarctation of the aorta

bicuspid aortic valve

33
Q

Trisomy 13 or 18 is associated with what CHD?

A

VSD, PDA

34
Q

Differential cyanosis CHD causes

A

PDA with R>L shunt

CoA with PDA after constriction

35
Q

Differential pulses

A

CoA

36
Q

Single S2 on heart auscultation

A

one semilunar valve (truncus)

37
Q

Fixed split S2 on heart auscultation

A

ASD

38
Q

Continuous murmur is associated with what CHD?

A

PDA

39
Q

Holosystolic murmur is associated with what CHD?

A

VSD

40
Q

What type of CHDs would present as cyanotic w/in hours/days of birth

A

R->L (deoxygenated blood into circulation)

41
Q

L->R shunt CHDs typically present?

A

Later, pulmonary pressure must drop enough (~6wks) to allow blood flow from L to R

42
Q

PDA/VSD present as

A

Infant w/ heart failure, murmur, and poor growth; Left heart enlargement; P & F to lungs

43
Q

ASD presents as

A

Child w/ murmur or exercise intolerance

Right heart enlargement; F to lungs

44
Q

Eisenmenger Syndrome

A

Long standing L->R shunt causing irreversible pulmonary vascular disease

45
Q

R-to-L shunt w/ increased BF:

A

Truncus arteriosus, TAPVR, TGA

46
Q

R-to-L shunt w/ decreased BF:

A

ToF, Tricuspid atresia, Ebstein’s anomaly

47
Q

CXR w/ very dark lung fields

A

decreased PBF: ToF, Tricuspid atresia, Ebstein’s

48
Q

CXR w/ increased vasculature marking & light lung fields

A

increased PBF: truncus arterioles, TAPVR, TGA

49
Q

CXR of ToF

A

boot-shaped

50
Q

ToF Sx are dependent on

A

degree of pulmonary stenosis

51
Q

Signs of ToF

A

PROV: pulmonary stenosis, RVH, Overriding aorta, VSD

52
Q

TGA physiology & findings

A

2 parallel circuits, w/ at least 2 shunts (R->L & L->R)

53
Q

Shunts in TGA

A

ASD, PFO

VSD, PDA

54
Q

TGA presents when

A

early, w/in hours typically

55
Q

TGA CXR finding

A

“egg on a string” narrow mediastinum

56
Q

Male:Female 3:1 in what CHD

A

TGA

57
Q

In TAPVR, the most common site for pulmonary veins to drains is?

A

SVC > RA = IVC

58
Q

Male:Female 4:1 in what CHD

A

TAPVR

59
Q

TAPVR typically have what shunts

A

100% ASD R->L shunt

60
Q

TAPVR CXR finding

A

Cardiomegaly “snowman Sign”

61
Q

TAPVR w/ pulmonary venous obstruction

A

cyanotic early (w/in 6hr) bc very little oxygenated blood is entering circulation

62
Q

Would PGE help resolve a TAPVR w/ pulmonary venous obstruction

A

NO, this increases pulmonary blood flow

63
Q

Tricuspid atresia involves what shunt

A

VSD

64
Q

Tricuspid atresia presents

A

Early

65
Q

Ebstein’s Anomaly CXR

A

balloon-shaped heart (enlarged RA + ARV)

66
Q

Shunt with Ebstein’s Anomaly

A

ASD, may have slight improvement over next few days as pulmonary resistance drops

67
Q

Severe HLHS or CoA are

A

ductal dependent (PDA)

68
Q

Norwood procedure for HLHS

A

(DAY 5) creates aorta from RV, closes PDA & opens shunt from aorta to pulmonary a.

69
Q

Bidirectional Glenn for HLHS

A

(5MO) get rid of BT shunt, SVC hooks to pulmonary a

70
Q

Fontan Circuit for HLHS

A

IVC connected to pulmonary a (deoxygenated blood bypasses heart & directly enters lungs)