Bicuspid Aortic Valve

Question 1

MC congenital heart abnormality

Answer 1

bicuspid aortic valve dz

Question 2

murmur heard w/ bicuspid aortic valve dz

Answer 2

• systolic ejection CLICK at LLSB

- AS or AR

Question 3

other cardiovascular and systemic abnormalities a/w bicuspid aortic valve dz

Answer 3

• aortic coarctation
• aneurysm of sinuses of Valsalva
• PDA
• aortic aneurysm and dissection

Question 4

first-line tx for stenotic bicuspid aortic valve

Answer 4

SAME AS FOR TRICUSPID AORTIC VALVES:

aortic valve replacement

Question 5

tx for regurgitant bicuspid aortic valve

Answer 5

aortic valve replacement if regurgitation is clinically significant

Question 6

when is regurgitation clinically significant in bicuspid aortic valve?

Answer 6

• symptomatic HF, or

- asymptomatic LVEF < 50%

Question 7

when to repair aortic root or replace ascending aorta in bicuspid aortic valve?

Answer 7

aortic root diameter > 5 cm

Question 8

how often to get echos in Asymptomatic pts w/ SEVERE AS or AR?

Answer 8

SAME AS FOR TRICUSPID AORTIC VALVES

yearly

Question 9

how often to get echos in Asymptomatic pts w/ MILD AS or AR?

Answer 9

SAME AS FOR TRICUSPID AORTIC VALVES

every 3-5 years

Question 10

when should the ascending aortic diameter be assessed and how often?

Answer 10

• yearly if 4 cm or more

- every 2 years if < 4 cm