Abdominal Flashcards
Ascariasis
- Round wrom 15-30cm long
- Jejunum>ileum.
- Imaging:
- longitudinal filling defects.The worm guts full with barium and can be seen.
- Worms can cluster and call SBO
- Cancause biliary obstruction and strictures.
*
Carney Triad
- Pulmonary chondromas
- Gastric leiomyosarcoma (GIST)
- Extra-adrenal paraganglioma
Caroli Disease
- Rare AR disease presents in children and young adults
- Cystic dilatation of the segmental bile ducts
- Presentation:
- frequent cholangitis and jaundice
- Complications:
- Liver cirrhosis
- Intraductal stones
- Cholagitis
- Cholangiocarcinoma.
- Assoc w PKD and medullary sponge kidney
Cowden Syndrome
- Inheritance: AD Ch 10 Age: 20s
- Features:
- rectosignoid polyps
- fibrocystic breast disease
- dysplastic cerebellar gangliocytoma (Lhermitte-Duclos )
- Facial skin lesions = trichemmomas
Cronkhite-Canada syndrome
- 60s M>W
- Multiple harmatomous polyps in stomach> colon>small bowel.
- Assoc w alopecia and nail atrophy.
Epithelioid haemangioendothelioma
- Middle aged females
- Assoc w OCP and vinyl chloride
- Peripherally located with internal calcification.
- Causes capsular retraction and compensatory hypertropohy of normal liver.
- Invasion into port and hepatic veins.
Familial Adenomatous polyposis
Inheritance: AD Ch 5 Age: 30-40 Features: -colonic carpets -stomach harmatomas -duodenal adenomas -periampullary carcinoma -desmoid tumours
Fibrolamellar HCC
- Lobulated heterogenous mass with a cenral scar in an otherwise normal liver. (Age = 20-40)
- Fibrous scar is usually hypointense on T2 (= differentiatior from FNH.)
- Heterogenous inhancement with non-enhancing scar (best seen on delayed imaging.
Gardner syndrome
- Inheritance: AD Ch 5
- Age: 15-30
- Features: - colonic polyps -skull osteotomas -poor dentition
Gaucher disease
- Lysosomal storage disease.
- Deficiency in glucocerebrosidase or beta-glucosidase activity.
- Accumulation of a glycolipid (glucocerebroside) within the lysosomes of macrophages, particularity in the bone marrow, spleen and liver.
Imaging:
Liver: hepatomegaly
Spleen: massive splenomegaly & focal infarcts.
MSK: Erlenmyer flask deformity, osteopaenia, multiple lytic bone lesions, aseptic necrosis of the femoral head.
Klatskin tumour
Old people.
Hilar cholangiocarcinoma.
Non-communicating right and left dilated intrahepatic ducts with normal calibre extrahepatic ducts.
Liver adenoma
- More common in females.
- Composed of hepatocytes but not bile ducts.
- Assoc with oral contraceptive pill and glycogen storage disease.
- Can resolve if stopping OCP.
- Complications:
- haemorrhage, infarction and malignant degeneration.
Imaging:
- CT - peripherally hypodense, isoattenuation to normal liver.
- MRI - signal fall out on of phase gradient echo. Reticolendothelial contrast uptake but not hepatobiliary.
- Cold on Tc99 sulfur colloid.
Liver angiosarcoma.
RARE! (aka Kupffer cell sarcoma)
Mor common in men.
RF:
- Thorotrast
- Vinyl choloride
- Arsenic
- Haemochromatosis
- Neurofibromatosis.
Imaging:
- CT: hypodense masses pre and post contrast. (high density may be from haemorrage)
- MR: heterogenous mass wth slow filling post gad.
- PET: FDG avid.
Liver mets
Colon > Stomach > Pancreas > Breast > Lung.
Ménétrier disease
- Rare idiopathic hypertrophic gastropathy.
- Presentation:
- Achlorhydria, hypoproteinaemia and oedema comprise the classic triad secondary to protein losing enteropathy.
- Imaging:
- Fluro/CT = thickened rugal folds.