14. Patient demonstration Flashcards
1
Q
Describe cystic fibrosis
A
Multi system disease
Autosomal recessive
Diagnosis usually in childhood
Median survival ~40 years
2
Q
Where is the mutation causing cystic fibrosis?
A
Mutation in CFTR gene
3
Q
List 3 respiratory management strategies for CF
A
Antibiotics
Airway clearance
Lung transplant
4
Q
Who needs a lung transplant?
A
Those with progressive chronic end stage respiratory disease
5
Q
List 3 features of a transplantable patient
A
No renal, heart or liver disease
No osteoporosis
BMI >17 or <30
6
Q
List 3 transplantable conditions
A
COPD
Cystic fibrosis
Interstitial lung disease
7
Q
What are the 4 post-transplant consequences?
A
Infection (immunosuppressed)
Rejection (cellular/ antibody mediated)
Lifestyle adaptations (diet, medication)
Frequent appointments and admissions
