1] CP Topics In Peds Flashcards
What weeks does the respiratory system begin to develop?
Weeks 4 - 7
Bronchial buds continue to evolve until all segments are formed; what weeks?
Week 7 - 16
Around what week does the diameter expand?
Week 13
By what week are all major lung structures developed
Week 16
Blood vessels and alveolar ducts have developed by what weeks?
Weeks 16 - 24
Type I and Type II pneumocytes have began to differentiate at week
Week 19
Fetal breathing at week?
Week 20
Sufficient alveolar precursors have
matured so that a baby born prematurely at thistime can usually breathe on its own
At week ?
Week 28
Alveoli develop and mature until the age of ?
8 years old
Less what type fibers in the diaphragm of an infant?
Less type 1 fibers
Age 0 - 3 months chest wall is ?
Triangular in anterior plane and circular from lateral view
The ribs are what age 0 - 3 months
Horizontal
Independent sitting happens around what months?
6 - 12 months
Chest becomes elliptical in what view at 6 - 12 months
Lateral view
Mutation of a gene on chromosome 7 that produces a protein called CFTR
Cystic fibrosis
Problems with CF
Chronic inflammation and infection in airways, digestive enzymes cant reach stomach, at risk for DIOS
Antibiotic therapies, steroids, bronchodilators, hypertonic saline and pulmozyme and new meds help manage?
CF
Autosomal recessive disease that effects the growth and function of hair-like structures called cilia
PCD
Primary ciliary dyskinesia
Life expectancy for PCD is?
Normal
What 4 parts of the body does PCD affect?
Sinus
Lungs
Ears
Reproductive system
Sinus rinses, bronchodilators, hypertonic saline, Pulmozyme.
Steroids and antibiotics similar to those used with CF
Airway Clearance
Exercise
All help to manage?
PCD
Saccharine tests for CF
Less than 60 minutes
Saccharine test for PCD
More than 60 minutes
Sweat test for CF vs PCD
Normal to elevated for CF
Normal for PCD
Lung disease for CF vs PCD
Progressive for CF
Stable for PCD
Life expectancy for CF vs PCD
Limited for CF
Normal for PCD
A serious lung condition that affects infants, primarily the premature infants
BPD
Bronchopulmonary dysplasia
commonly associated with low birth weight, prematurity, low amount of surfactant, supplemental O2 support
BPD
What is RDS
Respiratory distress syndrome; its when the infant lungs are not fully formed and it affects their ability to make surfactant
What is surfactant?
A liquid that coats the lungs that keep the lungs open to allow for spontaneous breathing when born
Outcome of BPD
Most babies show improvement over time with proper management
Medical management: Bronchodilators, steroids, and diuretics
Supplemental O2 via nasal cannula, CPAP, or mechanical ventilation
Surfactant replacement therapy
Emphasis on nutrition and caloric intake
Management of BPD
WHat does BPD stand for?
Broncopulmonary dysplasia
Survivors of BPD are at increased risk for ?
Respiratory disease and infection, asthma like disease, arterial hypertension
A birth defect formed in uterus where there is 1 or more abnormal connections b/w the esophagus and trachea
TEF