06 Anomalies of Development

Question 1

There is a wide range of normal for this tooth characteristic

Answer 1

color

Question 2

What are you evaluating when you are looking for potential develoment anomolies

Answer 2

Texture and Structure
Weakness is Structure, excess wear, abrasion
Abnormal radiographic appearance

Question 3

This is an abortive attempt by a single tooth bud to divide

Answer 3

Gemination

Question 4

Union of normally discrete teeth

Answer 4

Fusion

Question 5

Fusion of two teeth along the root surfac

Answer 5

concrescence

Question 6

Complete cleavage of a tooth bud resulting in the formation of a supernumerary tooth

Answer 6

twinning

Question 7

What is the clinical risk presented by taurodontism

Answer 7

Increased risk of pulp exposure

Question 8

The pulp is easily exposed in these tooth anomolies

Answer 8

Dens in dente

Dens invaginatus

Question 9

What is another name for Dens evaginatus

Answer 9

Talon cusp

Question 10

This condition is autosomal dominant with incomplete penetrance and variable expression

Answer 10

hypodontia

Question 11

Top 4 most likely missing teeth

Answer 11

Mn 2nd Premolar
Mx Lateral
Mx 2nd Premolar
Mn Lateral

Question 12

This syndrome is

Autosomal Recessive
Polydactyly
Short Stature
Cardiac anomalies

Answer 12

Ellis Van Creveld Syndrome

Chondroectodermal dyplasia

Question 13

This syndrome is Autosomal dominant
Missing maxillary incisors
Degeneration of the anterior chamber of the eye

Answer 13

Rieger Syndrome

Question 14

This syndrome is X-Linked
Cleft lip/palate
Digital anomalies
Long Nose

Answer 14

Oro-Facial-Digital Syndrome (OFD-1)

Question 15

This syndrome is
Autosomal Recessive
Broad nasal tip
Cleft lip/palate
Long nasal philtrum

Answer 15

OFD-II/ Mohr Syndrome

Question 16

What do you need to see to define an abnormality as an ectodermal dysplasias syndrome

Answer 16

Must meet at least one of:

Involvement of two or more ectodermal tissues

Genetic diagnoses

First degree affected relative

Question 17

This syndrome is x linked recessive

Multiple missing teeth
conical/peg teeth
lack of development of the alveolar process

Answer 17

Hypohidrotic Ectodermal Dysplasia

Question 18

This syndrome is Autosomal Dominant

Multiple Odontomas
Intestinal polyps
High malignancy rate

Answer 18

Gardner’s Syndrome

Question 19

This syndrome is Autosomal dominant

Extra teeth
Hypoplastic clavicles
Acorn shaped skull

Answer 19

Cleidocranial Dysplasia

Question 20

This extra tooth syndrome has extra teeth in the area of bony sutures due to splintering of the developing tooth bud

Answer 20

Cleft lip and palate

Question 21

This occurs in 1:14000 births

Defect is limited to tooth enamel

Dentin and Cementum are normal

Answer 21

Amelogenesis imperfecta

Question 22

Normal thickness
Soft
Pitted surface
Moth eaten radiographic appearance

Answer 22

Hypocalcified AI

Question 23

Soft enamel of normal thickness
Fractures and flakes aways
Enamel and Dentin are indistinguishable on x-ray

Answer 23

Hypomature AI

Question 24

Teeth have normal enamel with an amber hue

Bulbous crown with short, conical roots

Primary and Permanent dentitions involved

Answer 24

Dentinogensis Imperfecta