Test #2 Flashcards
congenital heart disease
-Anatomical: abnormal cardiac function
-Present at birth
Clinical course results in
-Heart failure
-Hypoxemia
acquired heart disorder
Disease process or abnormalities that occur after birth
Infection
Autoimmune responses
Environmental factors
Familial tendencies
Risk factors for congenital heart disease
Maternal diabetes or lupus
Medications during pregnancy (eg dilantin)
Substance use during pregnancy
Infections during pregnancy (rubella)
Low birth weight from intrauterine growth restriction
High birth weight babies
ECG
- Measure the electrical activity of the heart
- heart rate and rhythm
- abnormal rhythms or conduction, ischemic changes
- Bedside cardiac monitoring with ECG is common in peds
echo
ultra high-frequency sound waves to produce an image of the heart’s structure
MRI
Visualizes the structures
cardiac Cath nursing care
Pre
-Sedation
-NPO 4-6 hours before
Post
-Vital signs
- *pulse below cath site (equal and symmetrical)
- May be a bit weaker for the first few hours after
- Q15 min
- Hypotension → hemorrhage
- Bleeding, hematoma formation
- Fluid intake
- Blood glucose levels
- More for infants (give dextrose if low)
- The child’s usual diet can be resumed as soon as tolerated, beginning with sips of clear liquids and advancing as the condition allows
- The child should be encouraged to void to clear the contrast material from the blood
congenital heart disease
-Incidence: 12 per 1000 live births
-CHD is a major cause of death in the first year of life (after prematurity).
-Critical congenital heart disease (CCHD) is more severe and usually requires intervention early in life
-Pulse oximetry screening recommended review
-Done 24 hours after birth
-Test pulse ox from right hand
- >5% difference indicates problem
-The most common anomaly is ventricular septal defect (VSD).
-Often associated with other anomalies/chromosome abnormalities (trisomy 21, 13, 18).
Acyanotic hemodynamics
increased pulmonary blood flow
obstruction from the ventricles
Cyanotic hemodynamics
-decreased pulmonary blood flow
-mixed blood flow
increased pulmonary blood flow
-Atrial septal defect
-Ventricular septal defect
-patent ductus arteriosus
-antrioventrcilar canal defect
Abnormal connection between two sides of heart
Blood flows from higher pressure left side → lower pressure right side
Increased blood volume on right side of heart → Increases pulmonary blood flow
Decreased systemic blood flow
Obstruction from ventricles
-coarctation of aorta
-aortic stenosis
-pulmonic stenosis
Anatomic narrowing of blood vessel exiting the heart
Decreased pulmonary blood flow
-Tetralogy of Fallot
-Tricuspid Atresia
Blood has difficulty exiting right side of heart via pulmonary artery
Pressure on right side increases, greater than left-sided pressure
Desaturated blood shunts to the left side of heart and in systemic circulation
Mixed Blood Flow
-Transposition of great arteries
-total anomalous pulmonary venous return
-Truncus arteriosus
-Hypoplastic left heart syndrome
fully saturated systemic blood flow mixes with the desaturated pulmonary blood flow, causing a relative desaturation of the systemic blood flow.
Pulmonary congestion occurs because the differences in pulmonary artery pressure and aortic pressure favour pulmonary blood flow.
Cardiac output decreases because of a volume load on the ventricle.
Clinical Consequences of Congenital Heart Disease
Hypoxemia
Polycythemia and clubbing
Hypercyanotic spells (tet spells/blue spells) –> Give 100% O2, morphine, IV fluid replacement, knee to chin position
signs of digoxin toxicity
Nausea, vomiting, anorexia, bradycardia, dysrhythmias
chest xray
provides information on the heart size and pulmonary blood flow patterns, providing a baseline for future comparisons.
What is the leading cause of death after heart transplantation?
rejection
Vesicoureteral reflex
-Retrograde flow of urine from bladder to upper urinary tract (kidneys)
-Primary reflux related to anatomical abnormalities
-Secondary reflux related to acquired condition (eg. high bladder pressure, persistent PVRs or voiding dysfunction)
-Reflux increases chance for febrile UTI
-Reflux with infection is the most common cause for pyelonephritis
-Prevention with antibiotic prophylaxis
-Occasionally requires surgery
-Managed with daily low dose antibiotic until toilet independence
nursing care for post op gender assignment surgery
-Tub baths often discouraged for 1 week after surgery
-Keep surgical site clean, monitor infection
-Some older children’s activities, such as pushing, lifting, playing with straddle toys or in sandboxes, swimming, and engaging in rough activities, may be restricted after some types of surgical repairs.
-Activities of infants and toddlers are not limited.
dialysis
-The process of separating colloid and crystalline substances through a semipermeable membrane
-blood filtrate is circulated outside the body by hydrostatic pressure exerted across a semipermeable membrane with simultaneous infusion of a replacement solution.
-generally reserved for use in AKI, severe fluid overload, inborn errors of metabolism, or after bone marrow transplant.
peritoneal dialysis
-The preferred method of dialysis for children
-Abdominal cavity acts as semipermeable membrane for filtration
-Warmed solution enters peritoneal cavity by gravity, remains for period of time before removal
-The fluid and accumulated toxic wastes are then drained from the peritoneal cavity and a new cycle of fresh dialysis solution is reinstilled.
-Can be managed at home in some cases
-Performing this form of dialysis in the home can be empowering for families, especially adolescents.
hemodialysis
-Requires surgical creation of a vascular access and special dialysis equipment
-Vascular access may be one of three types: fistulas, grafts, or external vascular access devices.
-Best suited for children who can be brought to facility three times/week for 4 to 6 hours
-Achieves rapid correction of fluid and electrolyte abnormalities
-can cause adverse effects in association with this rapid change, such as muscle cramping, headaches, nausea and vomiting, and hypotension
-Disadvantages
-School absence
-Strict fluid and dietary restrictions
Kidney Transplant
-Preferred treatment for children with ESRD
-From living related donor
-From cadaver donor
-Primary goal is long-term survival of grafted tissue
-Role of immunosuppressant therapy
-Prednisone, tacrolimus, cyclosporine, mycophenolate
-Taken indefinitely
-Rejection of the transplanted kidney is the most common cause of transplant failure.
-Rejection is treated aggressively with immunosuppressant medications and can often be reversed
signs of increased ICP in infants
Tense, bulging fontanel
Separated cranial sutures
Macewen sign (cracked-pot sound on percussion)
Irritability and restlessness
Drowsiness, increased sleeping
High-pitched cry
Increased fronto-occipital circumference
Distended scalp veins
Poor feeding
Crying when disturbed
Setting-sun sign