Soft Tissue Sarcomas

Question 1

Most common soft tissue sarcoma is

Usually located

Answer 1

Rhabdomyosarcoma

Head/neck
Orbit
Genitourinary
Extremities

Question 2

Rhabdomyosarcoma

Light microscope appearance

Histological subtypes

Answer 2

Small round blue cell

Embryonal (60%, intermediate prognosis)

Botryoid (GU & nasopharynx)

Alveolar ( trunk & extremism;poorest prognosis)

Question 3

Presentations rhabdomyosarcoma

Answer 3

Mass +/- pain
Nasal congestion, mouth breathing, epistaxis, difficulty swallowing & chewing
CN palsy
Swelling, trsmus
Mass after trauma
Ptosis, periorbital oedema, change in VA
Unremitting croupy cough, stridor
Middle ear pain, deafness, chronic discharge
Sarcoma botryoides ( grape like mass at vaginal orofice)
Testicular mass