Rheuma

Question 1

Presents with fever at least 5 days with four of the ff

Conjunctivitis (nonpurulent, limbal sparing)
Rash (truncal, polymorphous)
Adenopathy (>1.5cm, unilateral)
Strawberry tongue/change in mucosa of oropharynx( or red cracked or swollen lips)
Hand changes (periph ext changes including edema/erythema and periungal desquamation)

Answer 1

Kawasaki disease aka Mucocutaneous lymph node syndrome

Question 2

Severe vasculitis affecting <5 y/o more commonly affecting medium-sized arteries with predilection to coronary arteries

Answer 2

Kawasaki disease

Question 3

Most common pediatric inflammatory myopathy presenting as systemic vasculopathy with characteristic cutaneous findings, and focal area of myositis resulting in progressive proximal muscle weakness

Answer 3

Juvenile dermatomyositis

Question 4

Classic rash (heliotrope of eyelids, gottron papules plus 3 of ff
Weakness (symmetric, proximal)
Muscle enzyme elevation
EMG changes (myopathy, denervation)
Muscle biopsy (necrosis, inflammation)

Answer 4

Juvenile dermatomyositis