Restrictive Flashcards
Restrictive Disease
- An inspiratory impairment
- May ultimately reduce all lung volumes, not just inspiratory volumes
- difficulty getting air in
Restrictive disease Causes
- Decreased compliance of lung or chest wall
- Reduced inspiratory effort (i.e. pain, weakness, etc.)
***dec expansion= dec air in
Restrictive disease Signs and symptoms
- Tachypnea, dyspnea, decreased breath sounds (primarly lower lobe), dry (nonproductive) cough, and emaciated appearance
Restrictive disease Interface with cardiac system
- Left sided heart failure → pulmonary symptoms
- Pulmonary symptoms → right sided heart failure
- Chronic alveolar hypoxemia → pulmonary vasoconstriction → pulmonary hypertension
- Manifested as cor pulmonale
***Rt ventricle working harder!
Common Restrictive pathologies
- Fibrotic diseases,
- sarcoidosis,
- acute respiratory distress syndrome (ARDS),
- pleural effusion,
- pulmonary edema,
- pneumonia,
- tuberculosis,
- sequelae secondary to musculoskeletal and neuromuscular conditions
Restrictive Disease-CXR
- CXR
- Radiopacities (appear white)
- Regions with retained secretions or flud (mucus in chest)
- Atelectatic segments (areas will collapse down)
- Radiopacities (appear white)
Restrictive disease PFTs
- Reduced lung volumes
- Reduced FVC
- Normal to increased (ratio > 80%)
- FEV1 / FVC ratio
Why might inspiratory crackles occur in a restrictive pathology in the absence of secretions?
- When actelectic segments open back up from being filled with air
Fibrotic Diseases
- Focal lung lesions representing progression of an inflammatory process to tissue fibrosis
- Destruction of alveolar capillary beds
- Irregular shape and size of alveolar spaces
- Decreased lung compliance (harder to inspire air)
Common Fibrotic pathologies
- Idiopathic pulmonary fibrosis (IPF): most common
- Asbestosis, silicosis, and interstitial lung disease
Fibrosis Causes (not for IPF)
- Cigarette smoking, viral infection, environmental pollutants, chronic aspiration, and genetic predisposition
Fibrosis Diagnostic findings
- CXR consistent with reticulonodular pattern (honeycombing)
- CT scan consistent with “ground glass” findings
- PFTs consistent with restrictive pathology
- ABGs consistent with decreased PaO2 with unchanged CO2 (difficulty getting in enough oxygen)
Fibrotic Diseases: Hallmark Signs and Symptoms
- Diminished breath sounds with potential for crackles
- DOE
- Progresses to SOB at rest
- Dry, non‐productive cough
- Weight loss (need to work harder to breath so more energy expenditure)
Fibrotic disease PT
- PHYSICAL THERAPY
- Breathing exercises
- Focus on inspiration
- Activity / exercise
- Breathing exercises
***aerobic activity (60-80%), interval training, UE/Le resistance training, long duration more favorable outcomes
Given a diagnosis of fibrotic disease, what assessments must be performed to guide the selection of the most optimal physical therapy intervention(s)?
- lung ascutation (how much can be inspired)
- expansion of chest wall (will be decreased with less inhaled)
- posture
- endurance testing
Sarcoidosis
- Uniform, epithelioid, fibrotic granulomas within multiple organs
- Most common locations: lung and lymph nodes
- Pulmonary insufficiency results in death in 5‐7% of patients
Sarcoidosis Diagnostic findings
- CXR consistent with diffuse infiltrates in bilateral lung fields
- Honeycomb appearance as disease progresses
- PFTs consistent with restrictive pathology
- ABGs consistent with hypoxia as disease state progresses
- Bloodwork consistent with leukopenia, anemia, and increased erythrocyte sedimentation rate