Random Flashcards

1
Q

what are the rule of 2’s in Meckel’s diverticulum?

A
2 feet from ileocecal valve 
2 in long
2 times more common in males
2% of population
2% develop complication over course of their lives
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2
Q

what conditions mimic acute appendicities

A
Yersinia enterocolitis 
mesenteric adenitis
constipation
crohn's 
meckel's 
ectopic pregnancy
UTI 
ovarian torsion
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3
Q

what murmur is associated with marfan ?

A

aortic root dilatation leading to diastolic decrescendo murmur (aortic insufficiency)

can also have mitral valve prolapse

can lead to aortic dissection

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4
Q

what is DiGeorge syndrome

A

facial features

  • low-set ears
  • eyes wide apart
  • palate anomalies
  • widened area below nasal bridge
  • short philtrum
  • micrognathia

cardiac lesion

  • abnormal heart sounds
  • murmur
  • right sided aortic arch
  • conotruncal anomalies

No thymic shadow seen on CXR

Hypocalcemia- parathyroid hypoplasia - (tetancy, seizures)

results from failure of the third and fourth pharyngeal pouches

**lots of viral and fungal infections b/c of lack of thymus

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5
Q

what are the common conotruncal anomalies associated with DiGeorge

A

transposition of great vessels, truncus arteriosus, right sided aortic arch

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6
Q

by age 12 months, infants should weigh how much compared to birth weight

A

3 times

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7
Q

what is the point of substituting medium chain triglycerides for long chain triglycerides in a babies diet?

A

if a baby has malabsorption and steatorrhea this will help because MCTs do not require bile acids for absorption.

preterm infants have steatorrhea b/c of poor absorption of fat due to small bile acid pool

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8
Q

what is a mongolian spot

A

hyperpigmentation found in 66% of all infants of hispanic, asian and native american ethnicity

sometimes mistaken for bruise

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9
Q

vomiting in a 10 month old, with lethargy, dehydration, full anterior fontanelle , no diarrhea, posturing

A

administer dexamethasone to decrease the intracranial pressure

most likely a brain tumor

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10
Q
resp tract infection
neonatal jaundice
recurrent bronchiolitis
nasal polyps
chronic diarrhea
features of malabsorption
meconium ileus
recurrent sinus infection
A

cystic fibrosis

obstructive airway disease
clubbing

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11
Q

what antibiotics do you use for CF treatment

A

tobramycin plus antipseudomonal (ticarcillin/piperacillin)

tobramycin pluse third gen cephalosporin (cefepime, ceftazidime)

tobramycin plus carbapenem (imipenem/cilastatin, meropenem)

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12
Q

what antibiotic is used to cover pasturella multocida

A

penicillin is the treatment of choice, but rare isolates with B-lactamase activity have been reported.

amoxicillin-clavulanate helps with resistance

if penicilin allergy use azithromycin

dog/cat bites
symptoms occur within a 24 hour period

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13
Q

if you suspect a lactase deficiency in a kid, what test should you do

A

lactose breath test

Its prevalence
in subjects of Asian (Far-Eastern) extraction is at least 85%

sucrase-isomaltase deficiency is the most common congenital disaccharidase deficiency

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14
Q

what is the lactulose breath test used for

A

useful in evaluation of suspected bacterial overgrowth, particularly pt’s who have undergone prior bowel surgery and present with symptoms that suggest a blind or stagnant intestinal loop

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15
Q

what are watery, acidic stools indicative of

A

carbohydrate malabsorption

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16
Q

“thumb sign”)

A

epiglottitis

lateral radiograph

Affected patients typically
present between the ages of 2 and 8 years with the rapid onset of fever,
sore throat, and the “four Ds” (drooling, dysphagia, dysphonia, and
dyspnea). Patients often assume a position of comfort by sitting upright,
leaning forward, and bracing themselves with their arms, known as the
tripod position.

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17
Q

steeple sign

A

AP view of croup

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18
Q

what is the treatment for acute rheumatic fever in a peds patient

A

Penicillin G or 10 days of oral penicillin even if throat culture is negative

19
Q

what are the major criteria for rhf

A
polyarthritis
carditis
subcutaneous nodules
sydenham chorea
erythema marginatum
20
Q

what are the minor manifestations for RHF

A

fever
arthralgia
prolonged PR interval on ECG
Elevated acute phase reactants (ESR, CRP)

21
Q

hyponatremia
postural hypotension
hyperkalemia
lack of response to cosyntropin stimulation test

plus

neurologic deficits -weakness, spasticity, dementia, blindness, quadraparesis

A

Adrenoleukodystrophy

x-linked disease where there is a mutation in the transportation of very long-chain fatty acids (VLCFA) into peroxisomes, thereby preventing beta-oxidation and breakdown of VLCFA
accumulation of VLCFA in neurons and adrenal cortex causes symptoms

adrenal stuff is usually detected before neuro stuff

22
Q
hypotonia
upslanting palpebral fissures
epicanthal folds
excess nuchal skin
enlarged tongue
clinodactyly of the fifth fingers
single transverse palmar crease
A

trisomy 21

23
Q
small palpebral fissures
low set ears
low birth weight
microcephaly 
rocker bottom feet
cleft lip
hypotonia
clenched hands
A

Edward syndrome (Trisomy 18)

24
Q

what are the cyanotic diseases of the newborn

A
truncus arteriosus
tricuspid atresia 
tetrology of fallot 
transposition of the great arteries
total anomalous pulmonary return and pulmonary stenosis
25
what is rx for scabies
premethrin cream
26
what anomalies are associated with diabetes during pregnancy
``` small left colon anencephaly meningomyelocele cardiac- assymetric septal hypertrophy, transposition of great vessels, VSD -sacral agenesis renal vein thrombosis renal agenesis ```
27
what heart defect is associated with turner
coarc of aorta
28
rash that spreads from the trunk to the extremities and is particularly associated with high fevers ....
roseola infantum caused by human herpes virus 6
29
Patient presents with short stature, webbed neck, shield like chest and widely spaced nippled, no secondary sex characteristics.... what will the levels of FSH, LH and Estradiol be? What will a buccal smear show?
High FSH High LH Low estradiol Buccal smear shows normal appearing epithelial cells with no barr bodies Rx: Estrogen Therapy Turner = XO
30
X-linked causes low or absent numbers of B cells leading to panhypogammagloblulinemia cellular immunity is intact pt develops infections after approximately 6 months of age when maternal ab's have decreased to low levels recurrent infections
Bruton Agammaglobulinemia
31
eczema thrombocytopenia recurrent infection
Wiskott -Aldrich Syndrome
32
positive whiff test
gardnerella or bacterial vaginitis Rx. Metronidazole
33
most common cause of neonatal meningitis
strep agalactiae - group B strep other common bugs are e coli and listeria monocytogenes
34
consumptive thrombocytopenia microangiopathic hemolytic anemia fever renal dysfunction fluctuating neuro deficitis
thrombotic thrombocytopenic purpura
35
anemia, thrombocytopenia, leukopenia and/or bone pain, hepatosplenomegaly, lymphadenopathy
ALL
36
what eye findings are seen in neurofibromatosis
lisch nodules (iris hamartomas)
37
what skin findings are seen in tuberous sclerosis
``` ash-leaf macules facial angiofibromas (adenoma sebaceum) and shagreen patches (connective tissue nevi) ``` seizures are the most common presenting symptom
38
Cerebral calcification facial nevus glaucoma in the ipsilateral eye seizures contralateral to the side of the nevus
sturge weber
39
freckling in the axillary or inguinal region
NF-1
40
``` history of neonatal jaundice recurrent bronchiolitis nasal polyps chronic diarrhea malabsorption meconium ileus ```
cystic fibrosis
41
antidote for iron poisoning
deferoxamine
42
what is the antidote for lead poisoning
EDTA + either DMSA or BAL (Dimercaprol ) with encephalopathy? EDTA + BAL
43
most common pathogen in young children with CF
staph aureus Rx. assume there is methicillin resistance and start vancomycin
44
what drugs can be used to treat pseudomonas in CF pt's
amikacin ceftazidime ciprofloxacin