Protein metabolism Flashcards
what does rennin in infant do
turns casein to paracasein to allow milk to stay in stomach for digestion`
the only AA that undergoees oxidation deamination
glutamate
most amino acids undergo transamination except
threonine, lysine , proline, hydroxyproline
the active form of thyroxine
tri-idotyrosine and tetra-idotyrosine
breakdown of dopamine
HVA
breakdown of norepinephrine
VMA
breakdown of dopamine
metarephrin
SULPHUR CONTAINING AMINO ACIDS
i) Include Methionine (M), serine(s), threoserine (T) & cysteine (c)
ii) Non-essential amino acids
iii) Found at the carboxy-terminal of polypeptide chain
why is creatine used in GER test?
GER ( glomeular filtration rate ) cause it’s 24hr secreted in urine
the three amino acids needed for making creatine ?
RGM ( arginine, glycine, methionine )
the three amino acids needed for making glutathione ?
ECG ( glutamate, cysteine, glycine )
maple syrup urine disease cause by
deficiency in alpha keto acid dehydrogenase
What is the difference between carbamoyl phosphate synthetase 1 and 2
CPS I is exclusively intramitochondrial, and its deficiency is responsible for the disease. CPS I. CPS II is exclusively cytosolic and is an important enzyme in de novo synthesis of pyrimidine nucleotides
treatment in hyperammonia `
arginine and benzoate
what supplements to give a patient with maple syrup urine disease
vitamin B1 (thiamine)