Peds/fetal GI Flashcards
- What is the first DDx for a pancreatic tumour in the 1st decade of life?
- What does it look like?
- pancreatoblastoma
- large w/calcs & liver mets.
- What part of the duodenum is narrowed w/annular pancreas?
- 2nd.
Neonatal low/distal bowel obstruction: megacystis microcolon intestinal hypoperistalsis syndrome
- Common?
- Path?
- Ix?
- Prognosis?
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Anorectal malformations: imperforate anus
- What is the role of radiology in these?
- How is this done?
- What is assoc w/a high ARM in males vs. females?
- What other 2 associations?
- What is Tx in either sex for a high lesion?
- Tx for low lesion?
- How to clinically diagnose high vs. low?
- Ix used to diagnose?
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Neonatal low/distal bowel obstruction: meconium ileus
- Path?
- Complication?
- Ix Fx-2.
- What is meconium ileus the earliest manifestation of?
- What is the relationship here?
- Classic Ix findings-2
- Tx-2
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Peds GI ED: malrotation/midgut volvulus:
- Path; what actually causes the volvulus?
- Typical presentation.
- How to rule it out?
- Can you have malrotation w/o volvulus?
- What % of infants present in 1st month? % that are symptomatic w/in 1 year?
- The 2 most important anatomy to show on every UGIS?
- Location of a normal duodenojejunal junction?
- Classic XR finding of midgut volvulus?
- Classic UGI finding?
- Ix clues to the presence of malrotation-5
- Tx?
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Pediatric lymphoproliferative disorder:
- How are kids different than adults?
- What % of peds xplant pts develop this?
- Which xplanted organs are less at risk of this?
- They’re 2-3x at greater risk.
- 15%
- Renal.
Neonatal low/distal bowel obstruction: Hirschsprung disease
- Path; what does this cause?
- Specific path?
- How often is the entire colon affected?
- 1/3 of kids develop what?
- 5% of kids w/this have what?
- Typical Ix Fx.
- How does this compare to functional immaturity of the colon, i.e., meconium plug?
- Gold standard Dx?
- Tx?
- Aganglionosis of the distal bowel that starts at the anus, causing pinching/lack of bowel relaxation.
- The vagal neural crest cells don’t migrate fully to the bum.
- Rarely, 1-3% is the whole colon affected.
- 1/3 develop enterocolitis similar to NEC.
- T21.
- Rectum will be smaller than dilated sigmoid (usually is the other way around).
- Hirsch is tapered rather than abrupt.
- Bx.
- Tx=surgical.
Fetal GI: esophageal atresia
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- What is the first DDx for pt w/pancolitis, who recently was on abx?
- Ix findings?
- What can this progress to & mortality?
- Pseudomembranous colitis.
- Marked, diffuse wall thickening w/paucity of adjacent fat inflammation.
- toxic megacolon in 5% of cases w/35% mortality.
Solid liver/biliary masses: HCC
- Similar to adults, when is this seen in kids?
- Causes of the above-5
- Tumour markers?
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Neonatal bowel obstruction: duodenal atresia, stenosis, web:
- Classic Ix sign for atresia.
- Classic Ix sign for web.
- Duodenal anomalies have associated abnormalities in what % of cases?
- Most common abnormality?
- What % of babies w/duodenal atresia have Down?
- Name 3 other associated abnormalities.
- DDx double bubble + distal bowel gas.
- double bubble
- windsock deformity
- 50%
- T21
- 30% of atresias have T21
- VACTERL, malrotation, annular pancreas (in 20% of babies w/atresia)
- DDx:
- Annular pancreas
- duodenal web
- malrotation
Fetal GI: distal bowel obstruction
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Fetal GI: general
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Childhood bowel obstruction: DDx
- DDx of the most common causes:
- DDx: AAIIMM
Solid liver/biliary masses: liver mets
- 2 most common liver mets in kids?
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Hepatobiliary neoplasia/masses: cystic: mesenchymal hamartoma
- Benign/malignant?
- Path?
- Tumour markers?
- Ix-2
- Tx?
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Childhood bowel obstruction: Crohn disease
- What % of newly diagnosed Crohn’s pts are kids?
- 30%
Neonatal cholestatic jaundice: approach
- Diff b/w unconjugated & conjugated hyperbili?
- Which one is always abnormal in the neonate?
- Generally, what causes this?
- DDx conjugated, the big ones.
- Goal of imaging in conjugated hyperbili?
- Test of choice?
- What is done to prep for this test?
- How does the test work?
- .
- .
- DDx: biliary atresia (25%), Alagille syndrome, alpha-1-antitrypsin deficiency.
Normal midgut rotation:
- How many degrees, in what rotation?
- Around what structure?
- At what GA does this occur?
- At what fetal age does the physiologic bowel herniation disappear?
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Fetal GI: meconium manifestations
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Hepatobiliary neoplasia/masses: cystic: GB hydrops
- Ix?
- Association?
- Pathologically distended GB w/no signs of infection.
- Kawasaki disease.