Peds & CV Flashcards
The Cyanotic defects
Pulmonary flow with acyanotic vs cyanotic lesions
acyanotic (L→R) increased pulmonary blood flow
acyanotic (R→L) = decreased pulmonary blood flow
most common congenital defect in children
VSD
Tetralogy of Fallot
- RV outflow obstruction [pulmonary stenosis]
- right ventricular hypertrophy
- overriding aorta
- VSD
Complex Shunts
mixing of pulmonary and systemic blood flow with cyanosis
- Transposition of the great arteries
- Truncus arteriosus
- Total anomalous pulmonary venous connection (TAPVR)
- Double outlet right ventricle
- Hypoplastic left heart syndrome
Only true neonatal surgical emergency
Total anomalous pulmonary venous connection (TAPVR)
Total anomalous pulmonary venous connection (TAPVR
All 4 pulmonary veins drain into RA
Transposition of the great arteries
Deoxygenated blood circ through systemic
Oxygenated blood circ through pulmonary
Hypoplastic left heart syndrome
- Left ventricle is small or absent
- Mitral and aortic valves are small or absent
- Ascending aorta is small
- Often an atrial septal defect (ASD)
Diaphragmatic hernia
most cases develop like this…
a portion of the posterior diaphragm fails to close on the left = triangular defect, foramen of Bochdalek
How do Hernias through the Foramen of Bochdalek affect respiratory status and anesthesia care?
those occurring early in fetal life usually cause respiratory failure immediately after birth d/t pulmonary hypoplasia
avoid BMV – immediate ETT
foramen of Bochdalek
vs.
Tracheoesophageal fistula
airway considerations
foramen of Bochdalek- do not mask; ETT right away
TEF- Avoid masking and ETT (may worsen gastric distention & further compromise respirations)
TEF:
Atresia v. Fistula
clinical signs
- Atresia: Drooling and occasional aspiration
- Fistula: Choking with feeding; possible breathing problems
TEF
Where is the fistula usually located?
one to two tracheal rings above the carina
TEF is usually a/w this condition
VACTERL
VACTERL
vertebral, anorectal, cardiac, tracheal, esophageal, renal, and/or limb defects
What confirms a TEF?
OG tube cannot be advanced more than ~7cm
Pyloric Stenosis
hypertrophy and hyperplasia of the muscularis layer of the pylorus (sphincter muscle) = gastric outlet obstruction
Pyloric Stenosis
and Acid/Base Balance
- hypoK, hypoCl metabolic alkalosis
- severe cases may progress to a metabolic acidosis
- kidneys pH compensate by excreting bicarb
- kidneys also excrete H and K, while retaining Na to maintain euvolemia and charge neutrality
Gastroschisis results from….
occlusion of the omphalomesenteric artery during gestation
T/F:
Gastroschisis is commonly a/w VACTERL syndrome.
False
Gastroschisis is usually not a/w other congential issues
Gastroschisis
how is the bowel affected?
- herniated viscera and intestines are periumbilical, usually on the right
- exposed to amniotic fluid in utero and to air after delivery
- inflammation
- edema, and dilated
- foreshortened
- functionally abnormal bowel
Infant vs Adult
Epiglottis
infant: narrow, omega shaped, and angled away from tracheal axis
adult: flat, broad, axis is parallel to the trachea