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Peds UWORLD > Peds > Flashcards

Peds Flashcards

1
Q

Coombs neg hemolytic anemia, jaundice, splenomegaly
Labs showing spherocytosis, hyperbilirubinemai, reticulocytosis, family hx anemia - DIAGNX?
Confirmed by?

A

Hereditary spherocytosis

Acidified glycerol lysis test

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2
Q

Calcified suprasellar tumor with bitemproal hamianopsia and pituitary hormonal defic (eg DIABETES INSIPIDUS, GROWTH HORMONE DEFIC)?

A

Craniopharyngioma

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3
Q

DiGeorge chromosome?

A

22q11.2 del (defective dev of phayngeal pounches)

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4
Q

DiGeorge clinical pres C.A.T.C.H.?

A 
Conotruncal cardiac defects
Abnormal facies
Thymic aplasia/hypoplasia
Cleft palate
Hypocalcemia
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5
Q

Ataxia and dysarthria onset in teen years, with scoliosis and feet deformities, with concentric hypertrophic cardiomyopathy - diagnx?
Most common causes of death?

A

Friedrich’s ataxia

Cardiomyopathy and resp complications

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6
Q

Fluid to correct hypovolemic hypernatremia?

A

NS (or LR)

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7
Q

Recurrent sinopulmonary and GI infections, plus often atopic or autoimmune dz. If severe, anaphylaxis during blood transfusion (most common primary immune defic) - what is it?
Why anaphylaxis?

A

Selective IgA defic

Anaphylaxis due to anti-IgA Ab

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8
Q

Most common cause of hip pain in kids 3-10?

Treat with?

A

Transient synovitis

Ibuprofen and rest

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9
Q

Exudative chest/pleural effusion due to disruption of thoracic duct (milky white fluid with elveated triglycerides) - diagnx?

A

Chylothorax

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10
Q

Pediatric hypertension in UE and hypoperfusion in LE (low O2 sat) - think?
Pathology?

A

Coarctation of aorta

Due to thickening of tunica media of aortic arch near ductus arteriosus

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11
Q

Contraindications (3) for DTaP vaxx?

A

immediate analphylaxis, unstable neurologic disorders, encephalopathy within a week of vaccine

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12
Q

Tumor in precocious puberty, increasing estrogen?

A

Granulosa cell

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13
Q

hematuria, famhx renal failure and sensoneurinal deafness - think?

A

alport’s syndrome

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14
Q

Cyanotic spells with a harsh crescendo-decrescendo murmur LUSB- Likely diagnx? Spells due to?
Murmur due to?

A

Tetralogy of Fallot
Obstruction of RVOT during exertion
Murmur due to turbulence at stenotic pulmonary artery

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15
Q

Primary amennorrhea workup:

A

First measure FSH if no breast development

  • If FSH decreased then pituitary MRI
  • If FSH increased then karyotype
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16
Q

Waterhouse Friedrich from meningococcal meningitis - telltale sign? Due to?

A

Sudden vasomotor collapse with skin rash

Due to adrenal hemorrhage

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17
Q

PNA, cutaneous abscesses and suppurative adenitis form catalase positive organisms - think?
What are the catalase positive organisms?
Dianostic test for this?

A

CGD
Staph aureus, serratia, burkholderia, aspergillus
Neutrophil testing with dihydrohodamine 123, or Nitroblue tetrazolium

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18
Q

PNA, cutaneous abscesses and suppurative adenitis from catalase positive organisms - think?
What are the catalase positive organisms?
Diagnostic test for this?

A

CGD
Staph aureus, serratia, burkholderia, aspergillus
Neutrophil testing with dihydrohodamine 123, or Nitroblue tetrazolium

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19
Q

Adolescent male with bone pain not related to physical activity, often proximal femur, responds to NSAIDs - diagnx and treat?

A 
Osteoid osteoma (bone forming tumor)
Benign, treat with NSAIDs
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20
Q

What differentiates Fe defic anemia from thalassemia?

A

RDW (increased in Fe defic)

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21
Q

Cyanotic tet spells helped by what position?

Why?

A

Knee-chest

Increases systemic vac resistance thus increases pulmonary blood flow and improves hypoxemia

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22
Q

Hip pain after viral infx that goes on 1-4 weeks?

Longer than that?

A

Transient synovitis

Legg Calve perthes DZ (osteonecrosis of femoral head)

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23
Q

Mild papular/nodular skin lesion with ipsilateral LAD with gradual onset?
Bug responsible?
Treat?

A

Cat scratch disease (if cat exposure)
Bartonella henselae
Azithromycin

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24
Q

Infant with cyanosis at rest and feeding but relived by crying - think?
First assessment, then?

A

Choanal atresia
Try to pass a catheter into the nose to oropharynx
Then CT scan to show narrowing at pterygoid plate in posterior nasal cavity

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25
Q

Normocytic anemia, vit defic?

A

B2 riboflavin

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26
Q

Increased gastric residual volume, vomiting, abd distension in preterm neonate?
Xray findings?

A

Necrotizing eneterocolitis

Intramural air and portal venous air

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27
Q

Clubfoot treatment?

A

Stretching and manipulation of foot, serial casts

If that fails then surgery (between 3-6 months old)

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28
Q

HUS triad along with diarrhea?
Organisms?
Treatment?

A

hemolytic anemia, thrombocytopenia, acute renal failure
Shiga toxin from sigella or E coli O157:H7
supportive treatment

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29
Q

Lyme dz in kids - antibiotic?

A

Amoxicillin (NOT doxy as contraindicated <8 yo)

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30
Q

Neonatal bilious vomting - managment?

A

Xray then if stable: contrast enema to determine meconium ileus vs Hirschspring dz

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31
Q

Meconium ileus (pathognomonic for CF) - treat?

A

Gastografin enema to break up the meconium. If unsuccessful then surgery

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32
Q

fever, lethargy and signs of heart failure with viral prodrome?
treat?

A

myocarditis

supportive, diuretics, inotropes

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33
Q

most common brain tumor in kids?

2nd most common posterior fossa tumor?

A

pilocytic astrocytoma

medulloblastoma

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34
Q

sore throat with exudative, fever and all the rest, looks like strep but the polymorphous, maculopapular rash after amoxilllin or ampicillin - diagnx?

A

EBV (mono)

Make sure with a monospot test

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35
Q

Neonate with macrosomia, macroglossia, umbilical hernia/omphalocele, hypoglycemia - think?
Check for?

A

Beckwith-Wiedemann
Abd/renal US and serum alpha fetaprotein to check for tumors such as Wilms tumor or hepatoblastoma as kids are very susceptible

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36
Q

Pathogen for PNA in KIDS with CF as opposed to adults?

A

Kids - staph aureus, Adults - Pseudomonas

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37
Q

Risk factors for surfactant defic?

A

Prematurity

Maternal DM

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38
Q

Orchiepexy for crytorchidism lowers risk of (3)?

A

lowers risk of testicular malignancy, improves fertility, removes risk of testicular torsion

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39
Q

Osteomyelitis bug in infants and kids?

A

Staph aureus

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40
Q

Scaly erythematous lesions on face, chest, extensor surfaces, poss flexural involvement?
Treat?

A 
Atopic dermatitis (eczema)
Rx: topical emollients
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41
Q

Setting fires with no motive?

Setting fires with a pattern of violation societal rules? Then >18?

A

Pyromania
Conduct disorder
Antisocial PD

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42
Q

Hemophilic arthropathy - what deposited in joint causing synovitis?
Prophylactic tx?

A 
hemosiderin
Factor concerntrates (VIII, IX)
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43
Q

Edwards syndrome features (6)?

A

IUGR, microcephaly, prominent occiput, micrognathia, closed fists with overlapping digits, rocker bottom feet

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44
Q

harsh, holosystolic murmur over LLSB - defect?

A

VSD

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45
Q

Intracranial calcifications and ventriculomegaly, manifesting as macrocephaly as well as nonspecific sign of congenital infx - Bug?
Tx?
Vectors?

A

toxoplasmosis
Pyrimethamine, sulfadiazine, folate
Raw or undercooked meat, unwashed fruit/veg, cat feces

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46
Q

Threshhold for polycythemia of neonate?
Risk factors?
Present?

A

HCT >65%
Delayed cord clamping, maternal HTN, maternal DM
resp distress, hypoglycemia, neuro sx

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47
Q

Painless hematochezia in young toddler (2 y/o)?

Diagnose with?

A

Meckel’s diverticulum

Tech-99 scan

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48
Q

Most common causes of viral meningitis?

A

echoviruses or coxsackieviruses (non-polio enterovirus)

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49
Q

Severe infx, FTT, chronic dairrhea - think?

TX?

A

SCID (absence of T-cells and dysfucntional B-cells)

Treat with stem cell transplant

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50
Q

Neonate with catracts, PDA, sensorineural hearing loss?

A

Congential rubella

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51
Q

Fever, exudative pharyngitis, circumoral pallor, SANDPAPER RASH, strawberry tongue?
Caused by?
Treat?

A

Scarlet fever
GAS extotoxin
PCN V

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52
Q

Hepetiform rash on top of atopic deramtitis?

A

HSV causing eczema herpeticum

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53
Q

Hereditary Spherocytosis is a defect of the ….

A

RBC membrane

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54
Q

1 VUR complication?

A

Renal scarring

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55
Q

Elevated lead fingerstick - next step?

A

Check venous lead levels, only chelate if >45
DMSA: 45-69
>70 or acute encephalopathy: EDTA & British anti-Lewsite

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56
Q

Toddler with firm, smooth, unilateral abd mass and HEMATURIA, no pain, suspect?`

A

Wilms tumor

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57
Q

gray vesicles on the tonsillar pillars (with or without hand and foot involvement?

A

herpangina due to coxsackie, an enterovirus

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58
Q

Bacterial meningitis in >1 month bugs?

A

Strep pneum and meningococcus

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59
Q 
Maneuver effects on preload/afterload:
Valsalva?
Sustained hand grip?
Passive leg raise?
Squatting?
A

Valsalva: -preload
Hand grip: +afterload
Leg raise: +preload
Squat: +preload and +afterload

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60
Q

HOCM murmur increases with what maneuver?

Why?

A

Valsalva

decr preload so der LV cavity size so incr LVOT and incr murmur intensity

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61
Q

Major protein source human milk vs formula?

A

Whey vs casein

whey more easily absorbed

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62
Q

Nephrotic syndrome in adult/adolescent with Hep Infx?

A

Membranous nephropathy

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63
Q

fever, hives, arthralgia, lymphadenopathy 1-2 weeks after B-lactams or sulfa (bactrim)?
Tx?

A

Serum sickness like reaction

Resolves with withdrawal of agent

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64
Q

Congenital rubella triad?

A

Hearing loss, cataracts, PDA

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65
Q

Bronchiolitis complications in neonates?

A

Apnea, resp failure

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66
Q

Most common cause of sepsis in SCD?

A

Strep pneumo

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67
Q

Bedwetting pharmacotherapy - 1st and 2nd line?

Try after what?

A

1st line desmopressin, 2nd line TCAs

Try pharm after behavioral mods and alarm therapy

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68
Q

Most common cause of pediatric stroke?

A

SCD

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69
Q

Mecomium ileus vs Hirschsprung obstructions?

A

MI: ileum with narrow colon
HD: aganglionic rectum and proximal dilated colon

70
Q

2 tourette’s combordities?

A

ADHD, OCD

71
Q

Ringworm tx?

A

Clotrimazole or terbinafine

72
Q

F/u for UTI in <2 yo girl?

A

Renal and bladder U/S, if abnormal then voiding cystourethrogram

73
Q

Precocious puberty with high LH and FSH - central or peripheral?
Treat?

A

Central (check an MRI too!)

GnRH tx

74
Q

A. P. G. A. R. stands for?

Cutoff for intervention?

A

Appearance/color, pulse, grimace/reaction, activity/muscle tone, respiratory effort
<7 (often pulse ox and positive pressure ventilation, HR <60 then chest compressions)

75
Q

Bugs and tx: Conjunctivitis <24 hours?
2-5 days?
5-14 days?

A

Chemical, eye lube
Gonococcal, IM 3rd gen cep single dose
Chlamydia, PO macrolide (erythro) (milder swelling than gono)

76
Q

New onset hearing loss, with chronic ear drainage despite ABX (also granulation tissue and skin debris poss) - diagnx?

A

Cholesteatoma

77
Q

How to treat subluxation of radial head (nursemaid’s)?

A

Hyperpronation (or next best supination with elbow flexion) - no XRay required

78
Q

Most common risk factor for intussusception?

A

viral illness (gastro) and resultant hypertrophy of Peyer patches

79
Q

Sudden drop of HgB with low retic count in SCD and no hepatosplenomegaly?
Most common trigger?

A

Aplastic crisis

Parvovirus B19

80
Q

Recurrent sinopulmonary and GI infx - consider?

A

Bruton’s

81
Q

Foreign body aspiration - next step?

A

Bronchoscopy NOT CXR

82
Q

Tx for adolescents with heavy vaginal bleeding (HD stable)?

A

high-dose OCPs (stabilizes endometrium and stop acute bleeding)

83
Q

Sternocleidomastoid muscle mass (in neck), head tilt, chin deviation - diagnx?

A

Torticollis - postural neck deformity

84
Q

Situs inversus, recurrent sinusitis, bronchiectasis- diagnx?

A

Kartagener syndrome (subroup of primary ciliary dyskinesia)

85
Q

Neonate with rhinorrhea and bullous or desquaming rash? (along with nonspecific congential signs: jaundice, hepatosplenomegaly and blueberry muffin rash)

A

Congenital syphilis

86
Q

Diastolic rumble at apex WITH pansystolic murmur at LLSB suggests?
WITHOUT?

A

VSD

mitral stenosis

87
Q

Hand and foot swelling with potential for SCD - pathology?

A

Vaso-occlusion

88
Q

Vaso-occlusion vs osteomyelitis vs necrosis in SCD?

A

Acute in >1 site = occlusion
Acute in only 1 site with fever, and positive blood culture = osteomyelitis
Chronic pain with no fever or warmth/erythema = avascular necrosis

89
Q

Ingestion: abd pain, hematemesis, metabolic acidosis AND you can see the tablets on Xray?
Tx?

A

Iron poisoning

Chelate with deferoxamine if moderate to severely ill

90
Q

Acute unilateral lymphadenitis - bugs?

Nodes most affected?

A

staph aureus and strep pyogenes

sub-mandibular

91
Q

Tourette’s pharmacotherapy?

A

a2-agonists (eg guanafacine)
1st gen antipsychotics (haldol, pimozide)
@nd gen antipsychotics eg risperidone

92
Q

Down syndrome pt with UMN signs?

A

Atlantoaxial instability

93
Q

3 associations with celiac?

A

T1DM, Iron defic anemia and dermatitis herpetiform

94
Q

How old can you see the thymic silhouette in right middle/upper lung?

A

<3 years old

95
Q

Neonate with feeding intolerance, bloody stool, distension - suspect?
Other risk factors?
Xray finding?

A

Necrotizing enterocolitis
Prematuritiy, hypotension, congenital heart dz
Pneumatosis intestinalis

96
Q

Absent red reflex - suspect what until proven otherwsie? Next step?

A

Retinoblastoma

Refer to optho

97
Q

Infant who is normal at birth but develops apathy, weakness, hypotonia, large tongue, sluggish movement, bloating, umbilical hernia - suspect?
Screened for at birth along with 2 others?

A

Hypothyroidism

Phenylketonuria and galactosemia

98
Q

UTIs with normal VCUG and renal US - consider?

A

Urinary stasis caused by constipation

99
Q

HUS triad?

A

microangiopathic hemolytic anemia (so DECR haptoglobin), thrombocytopenia, AKI

100
Q

Delayed growth spurt, delayed puberty and delayed bone age =

A

Constitutional growth delay

101
Q

Measles prodrome?
The rash starts where?
What precuations?

A

Cough, coryza, conjunctivitis
Maculopapular rash that spreads cepahlocaudal
Airborne (N95 mask)

102
Q

Orbital cellulits with vision changes and pain on EOM - most common predisposing factor?

A

Bacterial sinusitis

103
Q

JA - cutoff for poly or oligoarticular?

Lab findings?

A

5 or more poly, less than 5 oligo
High ESR, CRP, and ferritin,
High platelets, and high gammglobulins
With Anemia

104
Q

Double bubble = duodenal atresia, but “triple bubble” is?

Risk factors?

A

Jejunal atresia

Prenatal exposure to cocaine and other vasoconstrictors

105
Q

micro-Thrombocytopenia, eczema and recurrent infection - syndrome?
Inheritance pattern?
Gene mutated (WAS) responsible for?
Treat with?

A

Wiskott-Aldrich
X-linked Recessive
Cytoskeleton regulation
Hematopoetic stem cell transplant

106
Q

Infant with a hydrocele (it transilluminates) - management?

A

Watch and wait. Should disappear by 12 months of ago, if not, remove with surgery due to hernia risk

107
Q

Chronic BIPHASIC stridor as opposed to inspriatory?

A

Biphasic: vascular ring (improves with neck exptension)
Inspiratory: laryngomalacia (worse when supine, improves when prone)

108
Q

AOM vs Otitis media with effusion

A

Both have effusion but only AOM has acute eardrum inflammation

109
Q

Impetigo treatment?

A

Topical muciprocin

110
Q

SGA - weight percentile cutoff?

Possible complications?

A

<10th

hypoxia, hypoglycemia, hypothermia, hypocalcemia and polycythemia

111
Q

Scaly erythematous patch on scalp that can progress to alopecia (also inflammation, LAD, scarring) - suspect?
Diagnose with what?
Treat?

A

Tinea capitis (a dermatophyte infx)
KOH exam of hair shaft
PO terbanifine, griseofulvin (or itra/fluconazole)

112
Q

Overweight adolescent with a limp?

Treat?

A

SCFE

Urgent surgical fixation (to prevent avascular necrosis)

113
Q

Scaly, oily rash on scalp, eyelids, nasolabial folds, postauricular area AND umbilicus - diagnx?
Treat?

A

Seborrheic dermatitis

Often spontaneous remission, also emollients and nonmedicated shampoo

114
Q

DKA - serum potassium is normal or elevated. Total body K stores are ??? and why?

A

LOW due to osmotic diuresis (high blood glucose)

115
Q 
Febrile paroxysms (cyclic fever) - suspect?
Diagnose with?
A

Malaria

Thick and thin blood smears (Giemsa stained parasites)

116
Q

Single, round, blue inclusions on Wright stain in RBCs - what are they and what do they suggest?

A

Howell Jolly bodies
suggest physical absence of spleen or functional hyposplenism
might have splenectomy for hereditary spherocytosis

117
Q

Nonpitting edema in hands and feet in Turner’s?

A

lymphedema due to dygenesis of lymphatic system leading obstruction

118
Q

Premies: vaccine by chronological or gestaional age?

Exception?

A

Chronological

Except Hep B, must be >2kg (4lb6oz) for first dose

119
Q

Pertussis treatment?

Who gets prophylactic tx?

A

Macrolides

All close contacts regardless of age, immunization status, symptoms

120
Q

SCD splenic sequestration crisis - 3 labs?

A

normocytic anemia, incr reticulocyte count, thrombocytopenia

121
Q

Low grade fever, maculopapular rash with rapid cepahlocaudal spread, posterior auricular and suboccipital LAD with possible joint pains - think?

A

Rubella!

122
Q

Refeeding syndrom presents with?
Electrolytes affected?
Hormone causing it?

A

arrythmias and cardiopulmonary failure
K, Phos, Mg (cellular uptake so drop in serum)
insulin

123
Q

Ewing’s sarcoma mets sites?

Common pt demographic?

A

Lungs and lymph nodes

White males, 1st-2nd decade

124
Q

RDS presents immediately after birth with increased WOB - xray finding?
Tx?

A

fine reticular granulairty of lungs

CPAP

125
Q

Delayed umbilical cord separation, reurrent skin and mucosal bacterial infx (no purulence), severe PERIODONTAL disease. High Leukocytosis with neutrophilia?

A

Leukocyte adhesion defic

126
Q

Rapidly progressing, acute liver failure, encephalopathy, vomiting after aspirin? Micro or macrovesicular steatosis?

A

Reye’s syndrome, MICRO!

127
Q

Trachoma due to what bug?
Diagnostic sign?
Tx?

A

Chlamydia trachomatis
Tarsal conjunctivae inflammation
Oral azithro

128
Q

Limitation of upward gaze, billateral eyelid retraction, pupils react to accomodation but not light - suspected tumor?
Name of above syndorme of sx?
Then addition of headache and vomiting?

A

Pineal gland tumor
Parinaud syndrome
Obstructive hydrocephalus

129
Q

Macrocytic anemia with congenital anomalies (eg. short stature, webbed neck, cleft lip, triphalangeal thumbs) - think? (PRESENTS in first 3 MONTHS of LIFE)

A

DBS (Diamond-Blackfan anemia)

A pure red aplasia

130
Q

Decreased activity, hoarse cry and jaundice AND hypothyroidism in neonate (although most are asymptomatic)- suspect?
Due to?

A 
Congenital hypothyroidism
Thyroid dysgenesis (most common cause)
131
Q

Marfan’s gene?

A

Fibrillin 1

132
Q

Shock emergency when IV access is too hard - do what?

A

Intraosseus cannulation

133
Q

Resp distress due to congenital diaphragmatic hernia in newborn - what to do?

A 
Endotracheal intubation (NOT bag and mask)
Then place gastric tube to decompress stomach and bowel
134
Q

Palpable purpura on LE, abd pain, arthrlaigais, renal involvement, hematuria, possible scrotal sweeling (BUT NORMAL PLT COUNT) - suspect?
Pathophys?
GI complication?

A

Henoch Schonlein purpura
IgA mediated vasculitis
ileo-ileal intussusception

135
Q

SCID (adenosine deaminase defic) effect on lympocyte count?

A

SEVERE lymphopenia

136
Q

Squatting improves cyanosis in tet of fallot - why?

A

Increases blood flow across RVOT

137
Q

Most common side effect of sickle cell trait?

A

Painless hematuria

138
Q

Pancytopenia with blood counts dropping 4-12 years ld, plus congenital anomialies (hyperpigmentations, eyes, renal, hypogonadism, short staure, limbs)?

A

Fanconi’s anemia

139
Q

Pancytopenia followng drugs, toxins (radiation) or viral infection?
MCV?
On bone marrow biopsy (diagnostic)?

A

Aplastic anemia (acquired)
Normocytic or macrocytic
Hypocellularity with fatty infiltrate

140
Q

Adolesecent male athlete with knee pain - think?

Which is?

A

Osgood Schlatters
Traction apophysisits of tibila tubercle
On XR - soft tissue swelling, lifting or fragmentation of tubercle

141
Q

1 complication of AOM?

A

mastoiditis

142
Q

Asymmetric corneal light reflections, deviation on cover test - think?
Treat how to avoid what?
When is reassurnace OK?

A

Strabismus
Occlusion (patching) or penalization (blurring) of the NORMAL eye to avoid AMBLYOPIA (if doe snot work then surgery)
<4mo old, older needs to treat

143
Q

New onset stabismus with white eye reflex - suspect?

A

Retinoblastoma

144
Q

Cyanotic infant with LEFT AXIS DEVIATION (and decreased pulmonary markings) - suspect?

A

Triscupid valve atresia

145
Q

<10 years old, Abdominal pain, jaundice, palpable mass (single, multiple, intra or extrahepatic) - suspect?
Diagnose?
Treat?

A

Biliary cyst = choledochal cyst
US or ERCP
Surgical excision

146
Q

ALL age group? Also boys and tri21
Anemia and thrombocytopenia but what about WBCs?
Diagnosis?

A

2-5 years
Half have WBC <10, 20% have WBC >50
>25% lympoblasts on bone marrow biopsy

147
Q

Pyloric stenois diagnostic?

A

Abd US

148
Q

Trenelenburg sign due to wekaness of which 2 muslcles?

Innervated by what nerve?

A

gluteus minimus and medius

sup gluteal nerve

149
Q

Abx for a deep cat bite?

Bug??

A

Amoxi/clav

Pasteurella multocida

150
Q

Hereditary spherocytosis is a lack of what in RBC membrane?

How ling PCN prophylaxis post splenectomy?

A

spectrin

3-5 years

151
Q

Diarrhea, dementia, dermatitis (and death) is called what?
Caused by deficiency of what?
Which is vitamin Bwhat?

A

pellagra
Niacin (think corn diets)
B3

152
Q

Deliberate scald injury signs (4)?

A

Sharp demarcation
Uniform depth
Spared flexor surfaces
No splash marks

153
Q

Isolated thrombocytopenia and megakaryocytes with purpura and petechiae post viral infx - suspect?
Age most likley?
Treat?

A

ITP (immune thrombocytopenia)
2-5
Observe and should get better after 6 mo, unless bleeding then IVIG or steroids (but adults aget these <30 PLT count)

154
Q

SCID treatment?

A

Stem cell transplant

155
Q

Enzyme defic in CGD?

A

NADPH oxidase

156
Q

Friedrich’s ataxia 3 systems affected?

A

neuro, skeletal, cardiac

157
Q

Most common cyanotic heart porblem in neonates?

Associated murmur?

A

Transpostiion of great vessels

Single loud S2

158
Q

Limp: boys 4-10, girl 5-7 with antalgic gait?

A

Legg Claves (osteonecrosis)

159
Q

Test for CGD?

A

Test neutrophils with dihydrohodamine 123 or nitroblue tetrazolium

160
Q

Hypoglycemia at 3-4 months, hepatomegaly, Doll-like face - associated with?

A

G6PD defic

161
Q

Hypothyroid like sx BUT with macrosomia and rapid growth?

Do what?

A

Beckwith Wiedermann

Abd US to assess for Wilms tumor

162
Q

What does valsalva do to preload?

A

reduces!

163
Q

baby head edema crosses suture line then? does not?

A

caput if crosses, cephalohematoma if does not

164
Q

dubin johnson vs rotor difference (direct-conj bilirubinemia)?

A

dubin black liver

165
Q

where does indirect bilirubin deposit in brain?

A

basal ganglia, brainstem nuclei

166
Q

light isomerizes bilirubin NOT conjugates - T or F?

A

T

167
Q

theophylline used for?

A

central apnea!

168
Q

most common heart defect in down syndrome?

A

endocardial cushion defect (between ASD and VSD)

169
Q

Goat’s milk formula - think?

A

FOlate defic

170
Q

Clotting factors still OK with bad liver?

A

VW and 8

Peds UWORLD (1 decks)

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