Pediatric GI Flashcards
kids who get NEC
preterm, term infants with CHD, immunosuppression, umbilical venous catheter
XR findings
EARLY: bowel thickening, fixed distension on serial exams
LATE: pneumatosis, portal venous gas, pneumoperitoneum
NEC common location
iluem, RLQ right colon
Football sign
pneumoperitoneum, air outlining falciform ligament
Delayed complication of NEC
stricture
progressive projectile nonbilious emesis in firstborn males
HPS; 3x less common in females
Common age for HPS
2-12 weeks old
Caterpillar sign
undulating contour of gastric wall peristalsing against pylorus on XR
US criteria for HPS
wall thickness > 4 mm (echogenic mucosa to serosa) and channel lenght >16; 3.14; no feeds passing through pylorus
treatment for HPS
pyloroplasty, electrolyte replacement
Ddx for HPS
pylorospasm
Appendicitis findings
> 6 mm swolleng incompressible blind-ending tubular structure in RLQ; possible echogenic appendiclolith
Neonatal bilious emesis
midgut volvulus; nonobstructive gastroenteritis
age of presentation for malrotation
75% within first month of life; 90% symptomatic within one year
normal embryologic development of bowel rotation
270 counterclockwise around SMA; retroperitoneal course of duodenum; occurs 5-11th weeks
most important anatomy to show on upper GI
C sweep of duodenum and duodenojejunal junction; left of the left sided pedicle of the duodenal bulb (L1)
double bubble sign
duodenal obstruction; stomach and duodenal gas bubbles
corkscrew appearance of bowel
twisted bowel seen in midgut volvulus
Sublte findings associated with midgut volvulus
DJJ inferior to duodenal bulb, left of pedicle; cecum midline or in LLQ; inversion of SMA/SMV; whirlpool sign of mesenteric vessels
treatment of malrotation with volvulus
Ladd procedure; volvulus reduction, resection of necrotic bowel, lysis of Laddbands
most common location for intussusception
ileocolic location
typical presentation of intussusception
colicky abdominal pain; current jelly stol, palpable RLQ mass
types of intussusception
idiopathic from lymphoid tissue after viral infection; pathologic lead point (intestinal polyp, Mckel, lymphoma)
target or pseudokidney sign
intussuception
Differential for intussusception
intussusception, colitis, intramural hematoma, HSP/trauma
treatment for intussusception
air vs contrast enema; air up to 120 mmHg; successful flush of air into small bowel; up to 3 attempts up to 3 minutes each.
Contraindications to pneumatic reduction
free air, peritoneal signs, septic shock
Esophageal atresia is associated with?
TEF
VACTERL stands for
Vertebral, anal atresia, cardiac, TEF, renal anomalieis, limb (radial ray) anomalies
Most common type of TEF
Type A; NG tube terminating in mid esophagus with air filled bowel from distal TEF
Fetal suspicion for TEF
polyhydramnios and lack of visualization of stomach
TEF associations
VACTERL, bronchus suis, tracheomalacia
obstruction of distal stomach
gastric atresia
cause for nonbilious vomiting that dos not get progressively worse
gastric atresia; HPS gets progressively worse; nonobstructive antral web
Single bubble sign
gastric atresia
Imaging of choice with bowel obstruction
XR, upper GI for proximal obstruction, lower GI/contrast enema for distal obstruction
Windsock deformity
Duodenal web, symptomatic when child begins to eat solid food
Double bubble sign
duodenal atresia, may also suggest midgut, annular pancreas, duodenal stenosis/web
Associations with duodenal atresia
Down syndrome, VACTERL, shunt vascularity cardiac lesions, malrotation, annular pancreas
Triple bubble sign
proximal jejunal atresia
Causes for jejunal atresia
in utero vascular insult
type of contrast for contrast enema
isotonic or hypertonic water soluble contrast (400 mOsm)
Definition of microcolon
abnormally small caliber (<1 cm)
Types of microcolon
meconium ileus, ileoal/colonic atresia, colonic Hirshprung, megacystic microcolon hypoperistalsis syndrome
Complications of meconium ileus
bowel obstruction, perforation, peritonitis, abdominal and scrotal calcs
earliest manifestation of CF
meconium ileus
imaging findings of meconium ileus
XR: distal obstruction with soap bubble lucencies in the RLQ
Contrast enema: microcolun with multiple round filling defects in the distended ileum; smallest of all microcolons
Treatment of meconium ileus
gastrograffin enema, surgery if resistant
Ileal/colonic atresia imaging appearance
abrupt cutoff at the site of atresia; no filling defects
Small left colon syndrome or functional immaturity of the colon (FIC), meconium plug syndrome
most common diagnosis in failure to pass meconium; temporary functional immaturity of colonic ganglion cells; abnormal colon motlitiy
Infants who get small left colon
preterm neonates, neonates with moms with preeclampsia who received magnesium, diabetic
Imaging appearance of small left colon
small left colon, discrete transition at splenic flexure; filling defects = meconium plugs
Ddx small left colon
Hirschsprung with transitin at splenic flexure (does not hve a distensible rectum or resolve after enema)
aganglionoisis of distal bowel; distended distal bowel
Hirschsprung
consideration in neonates with bowel obstruction/colitis
Neonates with Hirschsprung may develop a form of eneterocolitis –> toxic megacolon; frank colitis in newborn is HD until proven otherwise
Associations with Hirschsprung
Down syndrome, less than duodenal atresia
Hirshsprung enema findings; rectosigmoid ratio
cone shaped transition zone; rectum normally has larger diameter than sigmoid; if the sigmoid is bigger than rectum, consider Hirshsprung
Megacystic microcolon intestinal hypoperistalsis syndrome
loss of bowel/bladder smooth muscle; fatal
Causes of childhood bowel obstruction
AAIIMM: appy, adhesions, internal/inguinal hernia, intussusception, Meckel, malrotation
Patent processus vaginalis complication
indirect inguinal hernia
Landmark for imperforate anus
puborectalis sling; high vs low; gender dependent
Association with high male anorectal malformation
posterior urethral valve/bladder fistula
Association with high female anorectal malformation
vaginal fistula
Treatment for high imperforate anus
colostomy, then definitive repair
association with low anorectal malformation
perineal fistula; treat with perineal anoplasty
Diagnosis of imperforate anus
infracoccygeal ultrasound
Conjugated/direct hyperbilirubinemia causes
biliary atresia, Alagille syndrome, bile acid synthetic defecs, metabolic disease, alpha 1 antitrypsin deficiency, infectious etioloties
Indirect/unconjugated hyperbilirubinemia
found in bloodstream; hemolytic jaundice; hepatitis
Imaging test of choice in conjugated hyperbilirubinemia
Tc 99m HIDA hepatobiliary scintigraphy; premedicate 5 days before with phenobarbital to stimulate hepatocytes
obliterative cholangiopathy of the intrahepatic and extraheatic bile ducts; obstructive jaundice
Biliary atresia
Triangle cord sign
The triangular cord sign is a triangular or tubular echogenic cord of fibrous tissue seen in the porta hepatis at ultrasonography and is relatively specific for the diagnosis of biliary atresia
Is gallbladder present with biliary atresai
suggestive of BA; gallbladder seen in 20% cases
NM findings of neonatal hepatitis
hepatobiliary scintigraphy: poor hepatic excretion, delayed hepatic clearance, variable bowel excretion
Types of primary pediatric liver tumors
epithelial/hepatocyte or mesencymal; liver mets
Cystic liver masses Mesencymal hamartoma
multicystic hamartomous lesion; developmental anomaly of the bile ducts, portal vein, and extramedullary hematopoeisis
Treatment for mesencymal hamartoma
surgical resection
presentation of mesenchymal hamartoma
enlarging abdominal mass; most diagnosed by ae2; no elevation of tumor markers
Choledocal cysts
saccular or fusiform dilation of bile ducts
gallbladder hydrops association
infection, inflammatory process (Kawasaki)
Classification of pediatric vascular malformations and neoplasms
High flow (AVM, AVF) or low flow lesions (venous malformation and lymphatic malformations)
High flow vascular neoplasm in pediatrics
Infantile hemangioma/hemangioendothelioma
Association with infantile hemangioma
Kasabach-Merit syndrome: vascular neoplasm, hemolytic anemia, consumptive coagulopathy
Types of infantile hemangiomas
focal, multifocal, diffuse; 60% occur in head and neck
Imaging findings of hemangioma
highly vascular, T2 hyperintense, T1 hypointense enhance peripherally with delayed fill-in; may have variable calcification, central necrosis, hemorrhage
Management of infantile hemangioma
most involute (if GLUT1 positive) although propranolol or surgery may be necessary if it causes CHF
Hepatoblastoma
malignant embryonal neoplasm; 3rd most common abdominal malignancy (after neuroblastoma and Wilms)
Association with hepatoblastoma
Beckweith Wiedemann (Q6 mo screening US), familiar adenomatous polyposis syndrome (FAPS), fetal alcohol syndrome
Tumor markers with hepatoblastoma
elevated AFP
Imaiging findings of hepatoblastoma
XR: RUQ calcification
CT: heterogenous solid enhancing mass; portain vein/hepatic vein invasion
HCC in kids
cirrhosis; alpha 1 antitrypsin deficiency, glycgen storage disease, tyrosinemia, biliar atresia, chronic viral hepatitis; elevated AFP
Malignant mesenchymoma
undifferentiateed embryonal sarcoma in kids 6-10 yo; AFP is negative
negative AFP with hepatic tumors
malignant mesenchymoma; hepatoblastoma, HCC positive
Common pediatric tumors that met to liver
Wilms, neuroblastoma
Remnant omphalomesenteric duct
Meckel diverticulum
Complications with Meckel
lead point for intussusception; GI bleeding (ectopic gastric mucosa)
omphalomesenteric duct connections
connect yolk sac via umbilicus
Complications of omphalomesenteric duct anomalies
umbilicoileal fistula, meckel diverticulum
Where is Meckel located
antimesenteric aspect of distal ileum; 2 feet from ileocecal valve
NM scan for Meckel
Tc99m pertecnetate scan; only positive of it contains ectopic gastric mucosa
Meconium spectrum
aspiration, ileus, plug, ileus-equivalent syndrome, peritonitis
Types of abdominal calcifications in peds
meconium peritonitis, pediatric neoplasm (neuroblastoma, teratoma, hepatoblastoma), adrenal hemorrhage, RUQ calcifications (gallstones, hepatoblastoma, hepatic TORCH infections)