PAH Clinic

Question 1

Why is giving PAH therapies (dilator medications) problematic in pulmonary veno-occlusive disease (PVOD)? (Ryan)

Answer 1

1. PVOD causing narrowing in the veins and capillaries
2. When patients received PAH therapies, dilation occurs in the arteries and significant edema results and the patient feels terrible
3. In these therapy, gene therapy may be done to diagnose the disease