Other renal tumors

Question 1

Clear cell sarcoma is more prevalent amongst which age group?

Answer 1

2 months - 14 years, average 36 months

Question 2

metastasis sites of clear cell sarcoma

Answer 2

lung
Bone
brain (less frequent)
soft tissues

If CCS suspected (tumor infiltrates kidney, no claw sign), proceed to pet/bone scan, consider brain ct/mri

Question 3

Name 1 histological findings of rhabdoid tumor of the kidkey

Answer 3

Large prominent “owl eye” nucleoli

Question 4

Name 1 syndrome associated with renal cell carcinoma

Answer 4

Von hippel-lindau

VHL is associated with Pheochromocytoma.

Question 5

What is the age distribution of renal cell carcinoma?

Answer 5

> 15 yo

Question 6

What is the classical presentation of renal cell carcinoma?

Answer 6

Hematuria

Question 7

What is the average age at diagnosis for rhabdoid tumors?

Answer 7

11 months (0-4 yo)

Question 8

What should be included in the metastatic workup of rhabdoid tumor?

Answer 8

Brain ct/MRI

10-15 % of CNS mets.

Question 9

Suspected diagnosis based on calcified mass in kidney and hematuria in an infant?

Answer 9

ossyfying renal tumor of infancy

<1 yo. benign. nephron sparing surgery.

Question 10

Suspected renal tumor in neonate?

Answer 10

congenital mesoblastic nephroma

excellent outcome
typically < 2 months old.

Question 11

Neoadjuvant chemotherapy is given for a suspected unresectable WT in a 4 yo. At 6 weeks, tumor has reduced 20 % in size. Name 2 other renal tumors which should be considered.

Answer 11

Rhabdoid tumor

clear cell sarcoma

Question 12

Name 2 renal tumors which can occur in teenages

Answer 12

Clear cell sarcoma

renal cell carcinoma