Orthognathic/Cleft/OSA Flashcards

1
Q

When performing a floor-of-the-mouth lowering procedure, it is necessary to:
A. perform a subperiosteal dissection
B. cover the denuded region with a soft tissue graft
C. avoid altering muscle attachments in patients diagnosed with retrolingual sleep apnea
D. detach all muscle attachments at the genial tubercle

A

Answer: C

Rationale:
Patients with suspected or diagnosed obstructive sleep apnea should not have muscle attachments altered in floor-of -mouth lowering procedures because this may worsen or create obstruction. Supraperiosteal dissections are performed and the incision margin is sutured to the periosteum at the depth of the vestibule. It is not necessary to place a soft tissue graft over
the denuded periosteum as this may be allowed to secondarily epithelialize. The genioglossus muscle attachments at the genial tubercle may be partially removed to increase the lingual sulcus, but approximately ½ oproper tongue function.

Reference:
Fonseca RJ Oral and Maxillofacial Surgery Vol. 7 p. 49WB Saunders2000

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2
Q
While under general anesthesia for a maxillo-mandibular advancement procedure, an obstructive sleep apnea patient is exhibiting significant hypotension. Pre-operatively, the patient’s baseline blood pressure was 170/90. On pre-operative physical examination, the patient had jugular venous distention and a para-sternal PMI. In this circumstance what is the most appropriate management for hypotension?
A. Intravenous fluid bolus
B. Trendelenberg positioning
C. Intravenousalpha-1blockade 
D. Intravenous vasopressor agent
A

Answer: D
Rationale:
This OSA patient has physical signs of pulmonary hypertension. The most appropriate manner to treat anesthetic induced hypotension without exacerbating right heart failure is an IV vasopressor agent (e.g. phenylephrine). Fluid bolus may exacerbate right heart failure and positioning has little effect on anesthesia induced hypotension. Alpha blockade may prevent the physiologic responses during efforts to correct the hypotension.
Reference:
Ronderos, J and Boyd, G: Anesthetic Considerations for Obstructive Sleep Apnea. Oral and Maxillofacial Clinics of North America: Vol. 7, No. 2 1995,
Hess, ML and Sibbald, WS: Applied Cardiovascular Physiology in the Critically Ill. Textbook of Critical Care, 4th Edition 2000, Chapter 89: 1001

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3
Q
In a patient who undergoes mandibular advancement, the ratio of soft tissue changes to hard tissue changes at pogonion would most likely be which of the following?
A. 1:1 
B. 1:2 
C. 2:3 
D. 1:4
A

Answer: A
Rationale:
During mandibular orthognathic surgery, the overlying soft tissues follow osseous changes closely. Generally, the soft tissues follow bony movements in a 1:1 ratio. The exception is the lower lip which relies heavily on the position of the incisor teeth and can also be affected by the position of the upper lip.
Reference:
Betts NJ, Dowd KF. Soft tissue changes associated with orthognathic surgery. Atlas Oral Maxillofac Surg Clin North Am 8: 13-38, 2000.

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4
Q
In a distraction osteogenesis procedure, the consolidation phase of treatment extends until which of the following stages of bone healing?
A. Hematoma formation and inflammation 
B. Soft callus formation
C. Hard callus formation
D. Bony maturation
A

Answer: C
Rationale:
Bony healing after a fracture or osteotomy consists of four histologically distinct stages: an inflammatory phase, soft callus formation, hard callus formation, and bony maturation/remodeling. During soft callus formation, fibrovascular structures bridge the osteotomized bone segments and there is recruitment of fibroblasts and mesenchymal stem cells within the fracture zone. It is this flexible soft callus which is lengthened via gradual traction during the subsequent distraction phase. Once the desired bony lengthening has been achieved, the distraction appliance is left in place and serves as a stabilizing device while the regenerate bone (soft callus) matures and calcifies forming a hard callus. Most distraction protocols recommend a consolidation/healing phase of at least 6 to 8 weeks.
Reference:
Crago C.A., Proffit W.R., and Ruiz R.L. Maxillofacial Distraction Osteogenesis. Pp. 357- 393. In: Proffit W.R., White R.P., and Sarver D.M. (Eds) Contemporary Treatment of Dentofacial Deformity. Philadelphia. Mosby. 2003.

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5
Q
A patient with an underlying diagnosis of Hemifacial Microsomia presents with severe unilateral hypoplasia of the ascending ramus, condyle, and glenoid fossa. There is little to no translational movement of the affected condyle. This mandibular-TMJ deformity is consistent with which skeletal type hemifacial microsomia?
A. Type I 
B. Type IIa 
C. Type IIb 
D. Type III
A

Answer: C
Rationale:
Patients with Hemifacial Microsomia (oculoauriculovertebral spectrum) will present with varying degrees of mandibular and temporomandibular joint hypoplasia as a primary finding in the condition. Kaban has refined a classification system useful in defining the degree of mandibular deformity in these patients. The specific type of mandibular/TMJ deformity present is a critical factor in deciding upon the specific reconstructive techniques that will be employed. The following is a brief synopsis of each Kaban type:
Type I: All skeletal components (glenoid fossa, condyle, ascending ramus) are present with a mild degree of hypoplasia. Normal function is present.
Type IIa: All of the skeletal components demonstrate a moderate degree of hypoplasia. While present, the condyle may appear to be malpositioned so that it is anterior and medial to the contralateral (normal) side. Function is affected, but remains satisfactory.
� Type IIb: There is moderate to severe hypoplasia of the glenoid fossa and the condyle- ramus complex. Despite an abnormal and severely hypoplastic condyle, many patients will still have a working joint and an actual “stop” where the condylar segment seats against the skull base. Most patients will demonstrate function that is limited to simple rotation of the condyle without any translational movements.
� Type III: This is the most severe form of mandibular hypoplasia with complete absence of the condyle-ramus complex and the glenoid fossa. The affected side of the mandible has no working articulation against the skull base.
Reference:
Kaban LB, Moses MH, Mulliken JB. Correction of hemifacial microsomia in the growing child: A follow-up study. Cleft Palate J 23 (Suppl 1) 50, 1986.
Kaban LB. Congenital Abnormalities of the Temporomandibular Joint. In: Kaban LB and Troulis MJ (Eds). Pediatric Oral and Maxillofacial Surgery. Pp. 302-339. Elsevier, Philadelphia, 2004.

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6
Q
During sagittal split osteotomy, the possibility of direct injury to the inferior alveolar neurovascular bundle can be minimized when the vertical component of the osteotomy is made over which of the following regions?
A. Lateral to the first molar
B. Lateral to the second molar
C. Lateral to the third molar
D. Lateral to the retromolar region
A

Answer: B
Rationale:
The position of the inferior alveolar neurovascular bundle is an important determinant in the design of the sagittal split osteotomy. The neurovascular bundle travels just under the facial cortical plate of the mandible. Whether the osteotomy is made with rotary instruments or a reciprocating saw, the vertical cut must be carried just through the cortical plate (i.e. monocortical). The thickness of the bone over the neurovascular bundle is greatest in the area of the second molar. The vertical osteotomy should be placed lateral to the second molar unless circumstances dictate otherwise.

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7
Q
In a distraction osteogenesis procedure, the latency phase of treatment corresponds to which of the following stages of bone healing?
A. Hematoma formation and inflamation
B. Soft callus formation
C. Hard callus formation
D. Bony maturation
A

Answer: B
Rationale:
Bony healing after a fracture or osteotomy consists of four histologically distinct stages: an inflammatory phase, soft callus formation, hard callus formation, and bony maturation/remodeling. During soft callus formation, fibrovascular structures bridge the osteotomized bone segments and there is recruitment of fibroblasts and mesenchymal stem cells within the fracture zone. It is this flexible soft callus which is lengthened via gradual traction during the subsequent distraction phase.

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8
Q

An 8-month-old female infant undergoes early mandibular advancement with distraction osteogenesis in order to alleviate airway obstruction related to severe mandibular hypoplasia. Bilateral mandibular osteotomies are completed and internal distractors are placed and confirmed. Surgery is followed by a 9 day latency phase. Upon activation of the right distractor, heavy resistance is encountered and the bone segments appear immobile. Which of the following is the most likely cause of this complication?
A. Excessive soft tissue resistance
B. Incomplete osteotomy at the time of surgery
C. Malfunction of the distractor
D. Early consolidation of the osteotomy

A

Answer: D
Rationale:
In most patients, a latency phase of 5 to 7 days allows for adequate formation of a soft callus before active distraction is initiated. If activation of the distractors is initiated too early, decreased bone formation results. If the latency period is too long, conversion to a hard callus begins and early healing of the osteotomy will prevent mandibular lengthening. In young children, bone healing occurs much faster and little or no latency phase is required.

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9
Q
The “Holdaway Ratio” is most useful in planning which of the following procedures?
A. Maxillary osteotomy
B. Mandibular osteotomy
C. Bimaxillary osteotomies
D. Genioplasty
A

Answer: D
Rationale:
The Steiner analysis is a cephalometric approach utilized to directly evaluate the protrusion of the upper and lower incisors. The position of the maxillary and mandibular incisors is related to Nasion-A point (N-A) and Nasion-B point (N-B) lines using both angular and linear measurements. Within this analysis, the “Holdaway Ratio” is used to evaluate the prominence of the mandibular incisors and bony chin. The ratio is calculated by comparing the distance of the lower incisor edge and pogonion to the N-B line. Ideally, the Holdaway Ratio should be approximately 1.0 in males and 0.5 to 1.0 in females. This relationship is useful in planning for genioplasty.

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10
Q

A 17 year old female patient presents for correction of her Class III dentoskeletal deformity consistent with a diagnosis of mandibular hyperplasia. A 4 mm of reverse overjet is noted. A submentovertex radiograph obtained during the initial evaluation reveals a “V” shaped mandible with divergent rami. Which surgical procedure for mandibular setback would result in the greatest alteration in intercondylar width in this patient?
A. Bilateral sagittal split osteotomies with lag screw fixation
B. Transoral vertical ramus osteotomies with lag screw fixation
C. Bilateral Inverted “L” osteotomies with miniplate fixation
D. Bilateral “C” osteotomies with miniplate fixation

A

Answer: A
Rationale:
One of the technical considerations that must be considered when choosing a specific procedure for mandibular setback surgery is the actual shape of the mandibular arch form and rami. In patients with a “U” shaped mandible, either bilateral sagittal split osteotomies (BSSO) or a transoral vertical ramus osteotomy may be utilized for mandibular setback in Class III patients. When the mandible is “V” shaped with flared rami, then the procedure that results in the least condylar width change is the transoral vertical ramus osteotomy. If a patient with a “V” shaped mandible undergoes BSSO, a gap is created posteriorly between the cortical plates of the proximal and distal segments. If lag screws are used for rigid fixation, the gap is closed and there is narrowing of the intercondylar width.

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11
Q

Which of the following is a special consideration when performing sagittal split osteotomy for mandibular advancement in children?
A. The lingula and inferior alveolar foramina are located in a more superior and posterior position in the ramus of children than in adults.
B. The sagittal bone cuts should be positioned as far medially as possible.
C. The propensity for “greenstick” fracture of the inferior border of the mandible is lower in children
than in adults.
D. Simultaneous removal of partially developed third molar teeth is not possible in children.

A

Answer: A
Rationale:
The lingula and inferior alveolar foramina are located in a more superior and posterior position in this age group. This has technical implications in determining the vertical placement of the medial osteotomy of the ramus. If the medial bone cut is positioned high on the ramus, then injury to the nerve is avoided , but the risk of unfavorable split (i.e. buccal plate fracture) increases. In children, the sagittal component of the osteotomy design should be placed as far laterally as possible in order to avoid injury to the developing teeth. Children will have a higher propensity for “greenstick” fracture along the inferior border of the mandible. Their bone is more cancellous in nature and this often results in a longer area of fracture along the inferior border of the mandible. Developing third molars can be removed after the mandibular ramus has been split. In cases where the third molar teeth are only partially developed, they can still be enucleated while the proximal and distal segments are separated

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12
Q

Which of the following is a contraindication for the use of a total mandibular subapical osteotomy?
A. Condylar hypoplasia
B. Relapse after sagittal split osteotomy
C. Skeletal apertognathia
D. Mandibular vertical alveolar deficiency

A

Answer: C
Rationale:
Skeletal anterior open bite (i.e. apertognathia) is the result of a maxillary growth problem and is frequently associated with a concomitant transverse maxillary discrepancy. The use of a total mandibular subapical osteotomy for correction of an anterior open bite requires counterclockwise movement of the dentoalveolar segment, does not address the maxillary deformity, and is associated with a high rate of skeletal relapse. Appropriate management of apertognathia requires correction of the maxillary problem usually consisting of segmental Le Fort I level surgery.
The use of the total mandibular subapical osteotomy is limited to correction of malocclusions that can be addressed by repositioning the mandibular alveolar process only. The subapical osteotomy does not change the anatomical position of the mandibular body or symphysis. As a result, application of the total mandibular subapical osteotomy is limited to situations where there is retrusion of the dentoalveolar process with an otherwise normal facial morphology.

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13
Q

A 16-year-old female patient undergoes a Le Fort I osteotomy for maxillary impaction. Two days after surgery, guiding elastics are removed and assessment of the patient’s occlusion reveals an anterior open bite. What is the most likely cause of this complication?
A. Severe condylar resorption associated with fixation
B. Failure of maxillary hardware
C. Incomplete seating of the condyles during surgery
D. Incomplete downfracture of the maxilla during surgery

A

Answer: C
Rationale:
Le Fort I level osteotomy may be complicated by intraoperative malpositioning of the maxillomandibular complex after the jaws have been wired together. Pressure applied to the chin may bring the maxillary osteotomy together while unintentionally displacing the mandibular condyles. This is often caused when bony interferences along the posterior maxilla exist.

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14
Q

A 23-year-old female undergoes maxillary superior positioning with a midline splitting of the maxilla to widen the transverse dimension 9 mm. Following an uneventful early post-operative course, she returns one year later with an anterior open bite. Which of the following would most likely explain the open bite?
A. Poor positioning of the mandibular condyles intra-operatively
B. Relapse of the transverse widening of the maxilla
C. Idiopathic condylar resorption
D. Failure of the hardware placed in the anterior maxilla

A

Answer: B
Rationale:
Transverse expansion of the maxillary arch is often complicated by lack of long term stability. This is especially true when large movements are undertaken. As transverse relapse occurs, the lingual cusps of the maxillary posterior teeth move along the lingual inclines of the lingual mandibular cusps and the anterior open bite deformity is recreated.

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15
Q

A patient arrives at the emergency department 2 weeks following a LeFort I osteotomy with advancement and impaction of the maxilla by another surgeon. The parents describe and uneventful course to date until profuse epistaxis lead them to call 911. On your arrival, the patient is stable with the exception of borderline hypotension and the bleeding has stopped without intervention. Which of the following would be the most prudent next step?
A. Place bilateral anterior nasal packs for 24 hours.
B. Return to the operating room for exploration of the surgical site.
C. Fluid resuscitation and referral back to the operating surgeon.
D. Arrange interventional angiography.

A

Answer: D
Rationale:
Bleeding during Le Fort I osteotomy and downfracture is usually the result of injury to the terminal branches of the internal maxillary artery including the descending palatine and sphenopalatine arteries. Even after the Le Fort I downfracture, intraoperative injury to the descending palatine vessels may occur as a result of significant maxillary advancement or impaction. Postoperative hemorrhage following maxillary surgery typically presents as epistaxis with bleeding into the anterior and/or posterior nasal cavity. This may occur at any point during the first month after the surgical procedure and may be the result of breakdown of previous clot or necrosis of arterial vessels which were stretched by the surgical movement. An initial “sentinel” episode of brisk bleeding may stop spontaneously giving the false impression that the problem has resolved. Angiography and interventional radiology techniques provide detailed visualization and localization of the source of bleeding. The bleeding vessel may be stopped by embolization without the need to reopen the wound, remove rigid fixation devices, and dismantle skeletal segments. Angiography also allows detailed visualization of the arterial system and detection and management of pseudoaneurysm involving the internal maxillary artery or its terminal branches.

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16
Q

Which of the following is the most common source of venous bleeding during maxillary osteotomy at the LeFort I level?
A. Facial vein
B. Pterygoid venous plexus
C. Laceration of the pterygoid musculature
D. Descending palatine veins

A

Answer: B
Rationale:
The pterygoid plexus of veins is located directly posterior and medial to the maxilla. Its location makes it vulnerable to injury during creation of the osteotomy and use of an osteotome for pterygomaxillary disjunction. It is the most common source of intraoperative venous hemorrhage in patients undergoing LeFort I osteotomy. Management of venous hemorrhage from the pterygoid plexus requires packing and application of topical hemostatic agents.

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17
Q

Aside from serial cephalometric radiographs, which of the following is considered the next most reliable method of estimating the facial skeletal maturity?
A. Evaluation of the C-spine
B. Hand-wrist films
C. Panoramic evaluation of dental development
D. Tanner’s developmental stages

A

Answer: A
Rationale:
Radiographic assessment of the hand-wrist anatomy has been utilized to estimate a patient’s skeletal age when early orthodontic or surgical treatment is contemplated. The theoretical basis is that the chronology of ossification in the bones of the hand and wrist can be related to the rest of the skeleton. The relationship between the bony development of the hand-wrist complex and the facial skeleton is not well correlated. Recently, the radiographic assessment of the cervical spine vertebrae for estimating skeletal development has been proposes. Although not perfect, the use of cervical spine development as an indicator of skeletal age is better correlated with the facial skeleton and the adolescent growth spurt. This technique has the additional advantage that no additional radiographs are required since the cervical vertebrae are visible on a cephalometric radiograph.

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18
Q
The most unstable skeletal movement in orthognathic surgery procedures is:
A. genioplasty – any direction.
B. maxillary inferior repositioning.
C. mandibular setback.
D. segmental maxillary expansion.
A

Answer: D
Rationale:
Segmental surgery for transverse maxillary expansion is associated with the highest rate of relapse following orthognathic surgery. Palatal soft tissue resistance and dental compensations often add to this instability.

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19
Q

A 16-year-old patient with a skeletal Class III malocclusion is beginning orthodontic treatment in preparation for eventual LeFort I osteotomy and bilateral sagittal split osteotomies. The patient has significant crowding in both maxillary and mandibular arches and dental compensations are present. If extraction of maxillary and mandibular premolars is indicated, which of the following combinations is most appropriate given the patient’s clinical findings and eventual surgical plan?
A. Extraction of maxillary first and mandibular second premolars
B. Extraction of maxillary second and mandibular first premolars
C. Extraction of maxillary and mandibular first premolars
D. Extraction of maxillary and mandibular second premolars

A

Answer: A
Rationale:
Extraction of maxillary first premolars in this clinical situation allows for adequate space for alignment of crowded maxillary incisors. The space created allows for correction of inclination for teeth that have drifted forward during development of dental compensations. As the maxillary first premolar spaces are closed, the anterior teeth are retracted maximizing the degree of maxillary skeletal advancement.
In Class III patients undergoing presurgical orthodontic treatment, extraction of mandibular first premolars is rarely indicated. This is because closure of the extraction spaces will require retraction of the anterior teeth resulting in less favorable tooth-lip balance. Extraction of the second mandibular premolars provides the necessary space for alleviation of crowding while avoiding retraction of the incisors.

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20
Q

Which of the following statements regarding Passavant’s Ridge is correct?
A. It is observed only as part of the cleft palate malformation.
B. It does not facilitate velopharyngeal closure.
C. It forms along the palatopharyngeus muscle.
D. It forms along the superior constrictor muscle.

A

Answer: D
Rationale:
Passavant’s ridge is a soft tissue prominence which extends into the pharynx. The structure is usually described in association with cleft palate, but has been described in many normal subjects. The soft tissue structure also frequently contributes positively to velopharyngeal closure. The ridge usually forms along the superior border of the superior pharyngeal constrictor muscle, but its exact position on the posterior pharyngeal wall may vary.

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21
Q

When performing Le Fort I osteotomy in an ungrafted bilateral cleft lip and palate patient, which of the following surgical techniques should be avoided?
A. Autogenous bone grafting and rigid fixation
B. Osteotome separation of the pre-maxilla from the nasal septum and vomer
C. Advancement of lateral segments for closure of cleft-dental gap
D. Circumvestibular incision and maxillary downfracture

A

Answer: D
Rationale:
Preservation of an anterior buccal mucosal pedicle is critical to preserving blood circulation to the premaxilla in patients that have not undergone previous bone graft reconstruction of bilateral cleft defects. A circumvestibular incision in the ungrafted bilateral cleft lip and palate patient would lead to aspectic necrosis of the premaxillary segment. Maxillary advancement in these patients is carried out through separate right and left vestibular incisions with limited tunneling anteriorly. A small vertical incision within the midline may be utilized for separation of the nasal septum and mobilization of the premaxillary segment.

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22
Q
A child born with an isolated cleft palate presents with severe myopia early in life. The most likely diagnosis is which of the following syndromes?
A. Pierre Robin Sequence
B. Stickler Syndrome
C. Van der Woude Syndrome
D. Velocardiofacial Syndrome
A

Answer: B
Rationale:
Isolated cleft palate is associated with an underlying syndrome more frequently (as much as 50%) than cleft lip and palate. Stickler syndrome has been identified as the most common diagnosis causing both cleft palate and Robin sequence. Patients with Stickler syndrome demonstrate a collagen metabolism disorder. Relevant clinical findings include early myopia and an increased risk of retinal detachment which may go un-noticed early in life. It is recommended that infants with an isolated cleft of the secondary palate undergo formal ophthalmologic evaluation at some point during their first year of life.
van der Woude syndrome can be caused by deletions in chromosome band 1q32, and linkage analysis has confirmed this chromosomal locus as the disease gene site. van der Woude syndrome is an autosomal dominant syndrome typically consisting of a cleft lip or cleft palate and distinctive pits of the lower lips. The degree to which individuals carrying the gene are affected is widely variable, even within families. These variable manifestations include lip pits alone, absent teeth, or isolated cleft lip and palate of varying degrees of severity. Other associated anomalies have also been described. About 1-2% of patients with cleft lip or palate have van der Woude syndrome.
Velocardiofacial syndrome (VCFS) is a genetic condition characterized by structural or functional palatal abnormalities, cardiac defects, unique facial characteristics, hypernasal speech, hypotonia, developmental delay, and learning disabilities. As many as 15-20% of patients have Robin sequence.

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23
Q
Which of the following surgical techniques for cleft palate repair retains an anterior soft tissue pedicle for improved flap perfusion?
A. von Langenbeck technique
B. Furlow Z-plasty technique
C. Bardach (2-flap) technique
D. Pushback procedure
A

Answer: A
Rationale:
The von Langenbeck palate repair technique involves the creation of two full thickness mucoperiosteal flaps with care taken to preserve anterior soft tissue pedicles. The theoretical advantage of the anterior soft tissue attachments is additional blood supply for the elevated flaps. During the Bardach (2-flap) and pushback procedures, similar soft tissue flaps are elevated, but no anterior pedicle is maintained. The Furlow procedure involves the use of double opposing Z-plasties with the musculature elevated with the posteriorly based flaps on the nasal and oral sides.

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24
Q
In the unrepaired cleft palate, the levator veli palatini muscle inserts abnormally into:
A. the medial pterygoid plate. 
B. the lateral pterygoid plate. 
C. the posterior hard palate. 
D. Passavant’s ridge.
A

Answer: C
Rationale:
The goals of cleft palate repair are twofold; first, water tight closure of the oral-nasal communication, and second, the creation of a dynamic soft palate for normal speech production. The most important muscular component of the soft palate is the levator veli palatini muscle which functions to elevate the velum and allow for appropriate speech production. In patients with an unrepaired cleft palate, the levator musculature is clefted and has abnormal insertions along the posterior edge of the hard palate.

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25
Q

In an infant born with a unilateral complete cleft lip and palate, primary repair of the cleft lip should be carried out when the child is:
A. 1 week of age and weighs 5 lbs (2.2kg).
B. 10 weeks of age and weighs 10 lbs (4.5 kg).
C. 10 months of age and weighs 10 lbs (4.5 kg).
D. 10 months of age and weighs 20 lbs (9.1 kg).

A

Answer B
Rationale:
Generally, cleft lip repair is carried out when the child is 10 to 12 weeks of age. General guidelines were developed for reduction of anesthetic risk and suggested that the surgery be undertaken when the child is approximately 10 weeks of age, weighs at least 10 lbs, and has a serum hemoglobin of at least 10 mg/dl. This has often been referred to as the “rule of 10’s” for the timing of cleft lip repair.

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26
Q
During primary repair of the cleft palate, utilizing Bardach’s (two-flap) technique, the palatal mucoperiosteal flaps are based upon which artery?
A. Ascending pharyngeal artery
B. Facial artery
C. Greater palatine artery
D. Sphenopalatine artery
A

Answer: C
Rationale:
Two-flap palatoplasty techniques involve the elevation of full-thickness mucoperiosteal flaps on each side of the cleft defect for oral side closure. After the nasal mucosa is closed, these soft tissue flaps are sutured together in the midline for closure of the cleft defect. During the initial dissection and elevation of the flaps, the greater palatine neurovascular bundles are identified and protected. The result is that the axial soft tissue flaps are raised based upon the blood supply of the greater palatine arteries bilaterally. If the greater palatine artery is injured or cauterized, then the axial pattern soft tissue flap becomes a random pattern flap (i.e. not based on one specific arterial supply) with perfusion from the palatal soft tissue attachments.

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27
Q

Secondary bone graft reconstruction of the cleft maxilla and alveolus is undertaken:
A. at the time of the palate repair during infancy.
B. when the maxillary central incisor is 2/3rds formed.
C. when the maxillary canine is 1⁄4 to 2/3 developed.
D. after partial eruption of the maxillary canine.

A

Answer: C
Rationale:
By definition, secondary bone graft reconstruction is carried out after the initial closure of the hard and soft palate. Generally, bone grafting is performed between 6 and 10 years of age, but the specific timing is based upon the child’s dental development instead of chronological age. Bone graft reconstruction of the cleft maxilla is undertaken based on the development of the permanent maxillary canine tooth. If partial eruption of the canine is allowed prior to bone graft placement, unfavorable periodontal outcome results.

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28
Q
The surgical technique for creation of a superiorly based pharyngeal flap requires elevation of which muscle from the posterior pharyngeal wall?
A. Palatopharyngeus muscle
B. Palatoglossus muscle
C. Superior constrictor muscle
D. Levator Veli Palatini
A

Answer: C
Rationale:
A superiorly based pharyngeal flap is commonly used for the management of velopharyngeal insufficiency related to cleft palate. A soft tissue flap is developed from the posterior pharyngeal wall. This is done by elevating the posterior pharyngeal wall soft tissues including the superior constrictor muscle off of the prevertebral fascia. This flap is then inset within the soft palate nasal side closure.

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29
Q
In the United States, the incidence of cleft lip or cleft lip with cleft palate is:
A. equal among all races.
B. greatest among Caucasians. 
C. greatest among African-Americans. 
D. greatest among Asian-Americans.
A

Answer: D
Rationale:
Cleft lip with or without cleft palate is a common congenital malformation with an incidence of approximately 1 in 700 live births, but significant variation is encountered when different ethnic/racial populations are examined. African Americans have an incidence which is significantly lower than the general population while Asians have the highest rate of birth prevalence. By contrast, isolated cleft palate has a lower overall incidence of approximately 1 in 2,000 live births with similar distribution among the different racial and ethnic populations.

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30
Q

The successful creation of velopharyngeal competence after superior pharyngeal flap surgery requires:
A. adequate lateral pharyngeal wall mobility.
B. palatal elongation at the time of surgery.
C. the presence of Passavant’s ridge.
D. glottic closure.

A

Answer: A
Rationale:
The superiorly based pharyngeal flap remains the standard approach for surgical management of patients with velopharyngeal insufficiency after cleft palate repair. The procedure involves the creation of a soft tissue flap from the posterior pharyngeal wall which is subsequently inset within the soft palate. The result is that the size of the nasopharyngeal cavity is decreased. The larger nasopharyngeal opening which could not be completely closed by the patient is instead converted into two (right and left) smaller lateral pharyngeal ports. Closure of these ports is easier for the patient to accomplish as long as adequate lateral pharyngeal wall motion is present.

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31
Q
Dynamic sphincter pharyngoplasty is performed by elevating myomucosal flaps which include which muscle?
A. Superior constrictor muscle
B. Palatopharyngeus muscle
C. Palatoglossus muscle
D. Tensor Veli Palatini
A

Answer: B
Rationale:
The dynamic sphincter pharyngoplasty procedure involves the use of two superiorly based myomucosal flaps created within each posterior tonsillar pillar. Each flap is elevated with care taken to include as much of the palatopharyngeous muscle as possible. The flaps are then attached to each other and inset within a horizontal incision on the posterior pharyngeal wall. The goal of this procedure is to create a single nasopharyngeal port that has a contractile ridge posteriorly in order to improve velopharyngeal closure.

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32
Q
Isolated cleft palate occurs most commonly:
A. in males.
B. on the right side.
C. in females.
D. on the left side.
A

Answer: C
Rationale:
In contrast to cleft lip and palate, there is a female predominance of cleft palate. The ratio is approximately 3:2.

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33
Q

The age at which the initial repair of a cleft palate is performed is based primarily on:
A. the anticipated development of speech.
B. the child’s ability to eat.
C. concerns for airway patency.
D. the anticipated need for bone grafting.

A

Answer: A
Rationale:
Ideally, one balances the need for an intact palate for normal speech production with the least interference of maxillary growth. Typically, children will begin to make purposeful speech at approximately 9 to 12 months of age. Most cleft palate centers recommend cleft palate repair between the ages of 9 and 18 months with the exact timing based upon the child’s language development as opposed to chronologic age. In a child who reaches an articulation age that requires an intact palate, failure to close the cleft leaves them vulnerable to the development of maladaptive speech patterns which are then difficult to break.

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34
Q

Which of the following is most appropriate in the feeding of an infant with an unrepaired cleft palate?
A. Using a squeezable bottle with a one-way valve
B. Using a reclined feeding position
C. Frequent burping of the infant
D. Fabrication of a custom feeding appliance or obturator

A

Answer: A
Rationale:
The presence of an unrepaired cleft palate causes difficulty with feeding due to the inability to form an adequate seal between the tongue and palate. The cleft defect prevents the infant from creating negative pressure needed to suck fluid from a bottle. Specialized feeding devices typically combine oversized nipples with reservoir spaces and large openings, a squeezable bottle to push fluid into the nipple assembly, and a one-way valve that allows the bolus of fluid to pass from the bottle to the nipple in order to minimize the amount of work the child must perform to feed. Infants should be positioned upright during feeding in order to facilitate management of the fluid bolus and secretions. Obturators for feeding have been used as feeding aids, but their value is not established. Their use has no effect on the infant’s ability to generate suction. The parent still must provide assisted feeds, and in infants with retrognathia and posteriorly positioned tongues, they create the risk of airway occlusion. Additionally, they must be monitored and adjusted frequently, making them both expensive and time consuming.

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35
Q

In addition to the classically described maxillomandibular anomalies, the most consistent finding associated with hemifacial microsomia is:
A. cataracts.
B. a tortuous internal carotid artery displaced toward the midline.
C. microtia.
D. a single central incisor.

A

Answer: C
Rationale:
Hemifacial microsomia is associated with several soft tissue anomalies in addition to the common skeletal manifestations. These include, but are not limited to, microtia, facial nerve palsy, skin tags, soft tissue and muscular hypoplasia, microphthalmos, and macrostomia.

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36
Q

Which of the following statements is correct regarding distraction osteogenesis of the maxilla in patients with clefts?
A. Long-term stability is greater when compared with traditional orthognathic surgery.
B. There is less likelihood of postoperative velopharyngeal insufficiency when compared with
traditional orthognathic techniques.
C. Less orthodontic finishing is required when compared with traditional orthognathic surgery.
D. Appliances are usually required to be retained for several months prior to removal.

A

Answer: D
Rationale:
Distraction osteogenesis has not been proven to provide significant advantages when one looks at post- operative stability or velopharyngeal insufficiency. Similar results have been seen when compared with studies done after traditional orthognathic surgery. There is no difference in orthodontic finishing requirements, and additional compensation may be required when compared with traditional techniques. During the consolidation phase, appliances (either internal or external) are kept in place for several months.

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37
Q

Which of the following statements best describes the most likely etiology of hemifacial microsomia?
A. X-linked condition
B. Autosomal recessive condition
C. Fibroblast growth factor receptor defect
D. Intrauterine vascular injury

A

Answer: D
Rationale:
The facial deformities associated with hemifacial microsomia are heterogeneous and demonstrate extreme variability of expression. Previous work by Poswillo suggested that early vascular disruption of the developing stapedial artery with expanding hematoma during intrauterine development resulted in destruction of differentiating tissues within the first and second branchial arches.

38
Q
Which of the following skeletal findings is associated with a diagnosis of holoprosencephaly?
A. Orbital hypertelorism
B. Premaxillary hyperplasia
C. Mandibular deficiency
D. Absence of nasal bones
A

Answer: D
Rationale:
Orbital hypotelorism with trigonocephalic skull deformity and absence of the nasal cavity and nasal bones are among the skeletal deformities frequently seen in infants with holoprocencephaly. Abnormal development of the premaxillary segment is also encountered and may result in a midline cleft or the characteristic single central incisor within a hypoplastic premaxilla. Mandibular morphology is normal.

39
Q
The CT image above demonstrates which of the following conditions?
A. Metopic suture craniosynostosis 
B. Coronal suture craniosynostosis 
C. Sagittal suture craniosynostosis 
D. Lambdoid suture craniosynostosis

A

Answer: B
Rationale:
The CT scan image shown above reveals right sided unilateral coronal suture craniosynostosis. The right coronal suture is absent and there is a classic skeletal deformity characterized by anterior plagiocephaly, orbital dystopia, and nasal bone asymmetry. This craniofacial deformity is the result of both arrested development at the site of the affected suture and an abnormal compensatory overgrowth at the site of the remaining open sutures. When the coronal suture is absent, the skeletal deformity also causes shortening of the anterior skull base on the affected side.

40
Q
What musculature must be re-approximated as a distinct layer during soft tissue closure following a transoral genioplasty procedure?
A. Genioglossus 
B. Mentalis
C. Digastric
D. Platysma
A

Answer: B
Rationale:
When a transoral approach to the bony chin is utilized, the mentalis musculature is routinely disrupted. These are paired muscles that insert on each side of the bony midline and are separated by a small fat pad. During closure, adequate repair of the mentalis muscles is critical in order to avoid a “witches chin” deformity.
Reference:
Posnick JC. Craniofacial and Maxillofacial Surgery in Children and Young Adults. Ed. J. C. Posnick. W. B Saunders, Philadelphia.

41
Q

Which of the following is a consideration when performing sagittal split osteotomy for mandibular advancement in children compared to adults?
A. The lingula and inferior alveolar foramina are located in a more inferior and anterior position within the ramus.
B. The sagittal bone cuts should be positioned more medial.
C. The propensity for “greenstick” fracture of the inferior border of the mandible is greater. D. Simultaneous removal of partially developed third molar teeth is not possible.

A

Answer: C
Rationale:
The lingula and inferior alveolar foramina are located in a more superior and posterior position in this age group. This has technical implications in determining the vertical placement of the medial osteotomy of the ramus. If the medial bone cut is positioned high on the ramus, then injury to the nerve is avoided, but the risk of unfavorable split (i.e. buccal plate fracture) increases. In children, the sagittal component of the osteotomy design should be placed as far laterally as possible in order to avoid injury to the developing teeth. Children will have a higher propensity for “greenstick” fracture along the inferior border of the mandible. Their bone is more cancellous in nature and this often results in a longer area of fracture along the inferior border of the mandible. Developing third molars can be removed after the mandibular ramus has been split. In cases where the third molar teeth are only partially developed, they can still be enucleated while the proximal and distal segments are separated
Reference:
Bell WH: Mandibular Advancement in Children Special Considerations. In Bell WH, Modern Practice in Orthognathic and Reconstructive Surgery. Vol. 3, 1992, WB Saunders. pp. 2516

42
Q

Which type of osteotomy procedure allows only a limited amount of mandibular advancement?
A. Bilateral saggittal split osteotomies
B. Inverted “L” osteotomies with bone grafts
C. Distraction osteogenesis after complete corticotomies
D. Trans-oral vertical ramus osteotomies

A

Answer: D
Rationale:
If any significant forward movement of the mandible is undertaken using trans-oral vertical ramus osteotomies, a large gap between the proximal and distal segments will result. The clinical applications of vertical ramus osteotomy procedures are limited primarily to mandibular set-back procedures and correction of relatively minor lower facial asymmetries. All other choices are reasonable approaches to a large mandibular advancement.
Reference:
Bell WH, Proffit WR, White RP, (eds.) Surgical correction of dentofacial deformities. Philadelphia: WB Saunders; 1980.

43
Q

A 7 year-old patient with Hemifacial Microsomia demonstrates complete absence of the ipsilateral condyle and the entire ascending ramus. There is a severe deficiency of posterior facial height on the affected side and a large maxillary cant. The patient has undergone an initial phase of interceptive orthodontic treatment and is ready for surgery. Which of the following is the most predictable surgical treatment?
A. Distraction osteogenesis of the affected side of the mandible B. Bilateral distraction osteogenesis of the mandible
C. Maxillary osteotomy for leveling of the occlusal plane
D. Costochondral graft for mandibular reconstruction

A

Answer: D
Rationale:
The patient described in this question has a Kaban Type III mandibular deformity with the complete absence of the condyle-ramus complex and glenoid fossa. The reconstructive approach for these patients consists of an initial phase of mandibular reconstruction using a costchondral graft for the construction of missing skeletal components (e.g. condyle- ascending ramus). This is typically carried out at approximately ages 6 to 12 years. A second stage of surgery is undertaken as the patient approaches skeletal maturity and typically consists of maxillomandibular surgery in order to normalize the occlusion and position of the lower facial skeleton.
Often, placement of a rib graft on the affected side is combined with a contralateral sagittal split osteotomy on the unaffected side. This allows for better three-dimensional repositioning of the distal segment of the mandible. At the same time, a posterior open bite on the affected side is created and maintained during the postoperative healing period with the use of an occlusal splint. This occlusal splint is then gradually reduced in order to facilitate dentoalveolar development of the maxilla on the affected side.
Distraction osteogenesis is a technique that allows for the lengthening of a skeletal part. In the type III deformity, there is no role for distraction osteogenesis since the condyle-ramus complex is congenitally missing and these anatomic parts can not be distracted into existence.
Reference:
Posnick JC. Hemifacial Microsomia: Evaluation and Treatment. In: Posnick JC (Ed). Craniofacial and Maxillofacial Surgery in Children and Young Adults. Pp: 419-445. W.B. Saunders. Philadelphia, 2000.

44
Q

An 3 year-old undergoes bilateral mandibular osteotomies with application of internal distraction appliances. Surgery is followed by a 2 day latency phase. The distraction appliances are then activated 0.75 mm four times daily for a total of 8 days and a consolidation phase of 8 weeks follows. Upon removal of the distraction appliances, bilateral mandibular nonunions are noted. Which of the following is the most likely cause of this complication?
A. Inadequate length of time for the latency phase
B. The rate and rhythm of the distraction phase
C. Inadequate rigidity of the device during consolidation phase D. Excessive soft tissue resistance during the advancement

A

Answer: B
Rationale:
In the above example, the most likely cause of the nonunions is the rapid rate of lengthening during the distraction phase. Most distraction protocols advocate a maximum daily rate of distraction of 1 mm total. In addition, many authors advocate a “rhythm” of distraction whereby the 1 mm total movement is divided into four incremental movements of 0.25 mm. This allows for gradual lengthening of the bony segments while avoiding excessive disruption of the bony regenerate (soft callus) and reduces soft tissue pain associated with activation of the device. In the above example, the patient’s rate of distraction was approximately 3 mm per day and a large movement (24 mm) resulted in a relatively short period of 8 days. Excessive lengthening over a short period may cause stretching of the soft callus with a thinned, hour-glass shaped bony regenerate or a fibrous nonunion.
Although the duration of the latency phase (2 days) described is shorter than is typical, the likelihood that it would have a negative consequence in a young child is very low. Average latency phase length is usually 5 to 7 days and allows for adequate formation of a soft callus before active distraction is initiated. In young children, bone healing occurs much faster and little or no latency phase is required.
Reference:
Crago C.A., Proffit W.R., and Ruiz R.L. Maxillofacial Distraction Osteogenesis. Pp. 357- 393. In: Proffit W.R., White R.P., and Sarver D.M. (Eds), Contemporary Treatment of Dentofacial Deformity. Philadelphia. Mosby. 2003.

45
Q

A patient undergoes bilateral sagittal split osteotomies for mandibular advancement and the distal segment if placed into the final surgical splint. After elimination of bony interferences, a bony gap remains between the anterior extent of the proximal and distal segments of the mandible. If lag-screw fixation is applied in this area, which of the following will occur?
A. There will be anterior displacement of the distal segment.
B. An anterior open bite will result
C. The mandibular condyles will be displaced medially
D. The mandibular condyles will be displaced laterally

A

Answer: D
Rationale:
Changes in intercondylar width may occur as a result of sagittal split osteotomy. As the distal segment is advanced, there is often the creation of a gap at the anterior-superior extent of the osteotomy site. If the segments are compressed together at the time of rigid fixation placement, there is a fulcrum based on the distal segment and lateral displacement of the condyle. Several techniques have been described in order to avoid unfavorable condylar displacement. These include the use of bicortical position screws, placement of bone shim between the proximal and distal segments, recontouring of the proximal/lingual aspect of the distal segment, and addition of a midline/symphyseal osteotomy. Use of lag screw fixation will compress the segments and actually cause lateral condylar displacement. Alternatively, lag screws may be utilized only when at least one position screw is placed first in order to maintain the anterior osteotomy gap.
Reference:
Tucker M.R., Frost D.E., and Terry B.C. Mandibular Surgery. In: Tucker M.R., Terry B.C., White R.P., and VanSickels J.E. (Eds), Rigid Fixation for Maxillofacial Surgery. J.B. Lippincott, New York, Pp. 251-295, 1991.

46
Q

A patient with unilateral failure of hardware (loss of fixation) one week following bilateral sagittal split osteotomies of the mandible may present with which of the following physical findings?
A. Unilateral open bite
B. Coincident maxillary and mandibular midlines
C. Deviation of the mandible on extreme opening
D. Increased lower facial height

A

Answer: A
Rationale:
Loss of fixation on one side of a bilateral sagittal split osteotomy typically causes a contralateral open bite, deviation of the mandible towards the side of the hardware failure, and lower facial asymmetry. The open bite occurs typically occurs as ramus height is lost and an early occlusal contact occurs. Midline shift occurs with loss of sagittal projection after fixation loss.
Reference:
Kaban L, et al. Complications in Oral and Maxillofacial Surgery. Complications of Orthognathic Surgery. WB Saunders; Philadelphia, Pennsylvania.

47
Q

Which of the following statements about nasal changes following Le Fort I osteotomy with maxillary advancement and impaction is true?
A. Nasolabial angle will increase
B. Alar base width will decrease
C. Dorsal hump will be less noticeable D. Nasal tip rotation will be unaffected

A

Answer: C
Rationale:
Movement of the maxilla directly affects the lower nasal anatomy and the nasal septum. When the maxilla is advanced and/or superiorly repositioned, the alar base width will increase, nasolabial angle will decrease, and increased superior rotation of the nasal tip is noted. As a result of these changes, the prominence of any dorsal hump will be reduced by the surrounding changes of the lower nasal dorsum.
Reference:
O’Ryan F, Schendel S. Nasal anatomy and maxillary surgery III. Surgical techniques for correction of nasal deformities in patients undergoing maxillary surgery. Int J Adult Ortho Orthogn Surg 4;157, 1989.

48
Q

Which of the following statements is correct regarding the use of distraction osteogenesis compared to conventional orthognathic surgical techniques for maxillary advancements of 5 millimeters or less?
A. Sagittal stability has been proven to be superior
B. Vertical stability has been proven to be superior
C. Perioperative morbidity is less
D. Long-term stability is similar

A

Answer: D
Rationale:
Distraction osteogenesis has not been proven to provide significant advantages when one looks at post-operative stability. Similar results have been seen when compared with studies done after traditional orthognathic surgery. There is no difference in orthodontic finishing requirements, and additional compensation may be required when compared with traditional techniques. During the consolidation phase, appliances (either internal or external) are kept in place for several months.
Reference:
Turvey TA, Ruiz RL, and Costello BJ. Surgical Correction of Midface Deficiency in Cleft Lip and Palate Malformation. Oral and Maxillofacial Surgery Clinics of North America: Secondary Cleft Surgery. Philadelphia: W.B. Saunders, 14: 491-507, 2002

49
Q

Which statement regarding surgically assisted rapid palatal expansion (SARPE) is correct?
A. Complete downfracture of the maxilla is required in order to realize adequate maxillary mobility.
B. The procedure creates more expansion within the anterior maxilla than the posterior maxilla.
C. The procedure is indicated when the amount of expansion necessary is less than 6 mm total.
D. The posterior maxilla may be adequately freed without the need for osteotomy in the lateral buttress region.

A

Answer: B
Rationale:
During surgically assisted rapid palatal expansion (SARPE), there is greater widening within the anterior maxilla than there is posteriorly. By contrast, a segmental osteotomy will produce more expansion posteriorly than anteriorly. This is the result of each procedure having a distinctive “hinge” pattern during the actual maxillary widening.
The SARPE procedure is reserved for cases in which greater than 8 to 10 mm of widening is necessary. If segmental osteotomy is undertaken for widening of greater than 10 mm, the likelihood of soft tissue dehiscence, periodontal defects, and poor long term stability increases.
The surgical approach requires that osteotomies be created at all of the points where potential resistance to lateral expansion will be encountered. These include the palatal suture, lateral buttresses, and pterygomaxillary junction. Complete maxillary downfracture is not required.
Reference:
Bailey LJ. Segmental Le Fort I osteotomy to effect palatal expansion. J Oral Maxillofac Surg 55:728-731, 1997.

50
Q

At the time of a LeFort I osteotomy, the width of the alar base of the nose can be controlled by which of the following?
A. Augmenting the piriform rim
B. Contouring the lateral extent of the alar cartilages C. Performing a V-Y closure of the upper lip
D. Pexy of the transverse nasalis muscle

A

Answer: D
Rationale:
Widening of the nasal base occurs anytime the maxilla is repositioned anteriorly or superiorly. In order to avoid undesirable nasal widening, a cinch-suture is passed through the transverse nasalis muscle on each side of the alar base of the nose and tied. Some surgeons prefer to pass this suture through the caudal edge of the nasal septum or anterior nasal spine.
Reference:
Schendel SA, Williamson L. Muscle reorientation following superior repositioning of the maxilla. J Oral Maxillofac Surg 41: 235-40, 1983.

51
Q
The Steiner analysis is useful in evaluating which of the following?
A. Upper and lower incisor position
B. The degree of lip incompetence
C. Lower facial height to width ratio
D. Vertical maxillary position
A

Answer: A
Rationale:
The Steiner analysis is a cephalometric analysis useful in evaluating the degree of maxillary and mandibular incisor protrusion relative to the surrounding skeletal structures. The position of the maxillary and mandibular incisors is related to Nasion-A point (N-A) and Nasion-B point (N-B) lines using both angular and linear measurements.
Reference:
Proffit W.R., Sarver D.M. Diagnosis: Gathering and Organizing the Appropriate Information. Pp. 127-170. In: Proffit W.R., White R.P., and Sarver D.M. (Eds) Contemporary Treatment of Dentofacial Deformity. Philadelphia. Mosby. 2003.

52
Q
  1. Which of the following two-jaw orthognathic surgical procedures demonstrates the greatest long-term skeletal stability?
    A. Maxillary impaction with mandibular advancement
    B. Maxillary advancement with mandibular advancement
    C. Maxillary downgraft with mandibular setback
    D. Maxillary transverse widening with mandibular setback
A

Answer: A
Rationale:
Long-term data on skeletal stability following orthognathic surgery suggests that some procedures are more predictable than others. Overall, surgical procedures aimed at the correction of Class II problems tend to be extremely stable. These include mandibular advancement, superior and/or anterior maxillary repositioning, and combinations of the two. Skeletal stability following mandibular setback and combined procedures for the correction of Class III situations are less reliable. Treatment plans that include the transverse widening of the maxilla are the most problematic in terms of long term stability.
Reference:
Proffit WR, Turvey TA, Phillips C. Orthognathic Surgery: a hierarchy of stability. Int J Adult Orthod Orthogn Surg 11: 191-204, 1996.

53
Q
A 48 year-old patient presents with obstructive sleep apnea and a respiratory disturbance index (RDI) of 110. Diagnostic work-up is undertaken and reveals that the patient has signs of pulmonary hypertension, intermittent ventricular ectopy, and moderate to severe congestive heart failure (cor pulmonale). Which of the following is the most appropriate initial surgical treatment?
A. Septoplasty, turbinectomy
B. Uvulopalatopharyngoplasty
C. Tracheostomy
D. Maxillo-mandibular advancement
A

Answer: C
Rationale:
Tracheostomy remains an extremely effective treatment modality in patients with obstructive sleep apnea because it completely bypasses all of the levels of obstruction within the upper airway. Although permanent tracheostomy is an unattractive alterative for patients, its use as a temporary measure can produce marked and rapid improvements in sleep architecture and oxygenation.
In the above clinical situation, the primary indication for tracheostomy as an initial therapy is the patient’s strikingly abnormal RDI and the presence of severe cardio-pulmonary consequences associated with OSA. The presence of life-threatening cardiac conditions requires that the upper airway be bypassed. In this example, tracheostomy may be utilized as an interim treatment until other procedures (e.g. maxillomandibular advancement) may be carried out in order to improve the patient’s upper airway.
Reference:
Tiner BD, Waite PD. Surgical and Nonsurgical Management of Obstructive Sleep Apnea. In: Miloro M, Ghali GE, Larsen PE, and Waite PD (Editors), Peterson’s Principles of Oral and Maxillofacial Surgery, Second Edition. Pp. 1297-1313. BC Decker, Hamilton, 2004.

54
Q

Which of the following statements about cleft lip and palate is correct? A. Overall prevalence is approximately 1 in 4000 live births.
B. Orofacial clefting rates are lowest in Native-Americans.
C. Isolated cleft palate is more common than cleft lip.
D. A syndromic diagnosis is more common with isolated cleft palate.

A

Answer: D
Rationale:
Cleft lip with or without cleft palate is a common congenital malformation with an incidence of approximately 1 in 700 live births, but significant variation is encountered when different ethnic/racial populations are examined. African Americans have an incidence which is significantly lower than the general population while Asians and Native-Americans have the highest rates of birth prevalence. By contrast, isolated cleft palate has a lower overall incidence of approximately 1 in 2,000 live births with similar distribution among the different racial and ethnic populations. Of note is that children with isolated cleft palate are almost five-times more likely to also have some other underlying syndromic condition.
Reference:
Costello BJ, Ruiz RL. Cleft Lip and Palate: Comprehensive Treatment Planning and Primary Repair. In: Miloro M, Ghali GE, Larsen PE, and Waite PD (Editors): Peterson’s Principles of Oral and Maxillofacial Surgery, Second Edition. BC Decker. Hamilton. 2004. Pp: 839-858.

55
Q

The superiorly based pharyngeal myomucosal flap contains a portion of what muscle? A. Superior constrictor
B. Palatopharyngeus
C. Palatoglossus
D. Tensor veli palatini

A

Answer: A
Rationale:
The pharyngeal flap is fashioned on the posterior pharyngeal wall by incising through mucosa and bluntly dissecting through superior constrictor until prevertebral fascia is identified. A superior pedicle is maintained for this finger-like, random pattern flap that is then sewn into the soft palate.
Reference:
Costello BJ, Ruiz RL. Reconstruction of Cleft Lip and Palate: Secondary Procedures. In Peterson’s Principles of Oral and Maxillofacial Surgery, ed 2. Miloro M, Larsen P, Ghali GE, and Waite P eds. Hamilton: Decker 2004:871-886.

56
Q

The diagnosis of velopharyngeal insufficiency is best established by which of the following?
A. Perceptual evaluation by a speech language pathologist
B. Fiberoptic nasopharyngoscopy
C. Videofluoroscopy
D. Nasometry

A

Answer: A
Rationale:
The determination of the presence or absence of velopharyngeal dysfunction is made during the perceptual speech evaluation performed by a speech language pathologist. During this examination, the speech pathologist relies on auditory and visual input perceived during spontaneous speech and during the production of standard phrases/words designed to test velopharyngeal function.
Nasopharyngoscopy and videofluoroscopy are instruments employed to further study individuals diagnosed with velopharyngeal dysfunction. These provide information regarding the cause and the magnitude of the dysfunction. The information gained therein may be used to select subsequent therapy and tailor it according to each individual’s functional anatomy.
Nasometry is a physiologic assessment tool that provides indirect, quantitative measurements of nasal, relative to oral, acoustic energy transmission. Its utility is in helping quantify dysfunction and perhaps as a biorationale device for training proper velopharyngeal function.
Reference:
Marsh JL. The evaluation and management of velopharyngeal dysfunction. Clin Plast Surg 2004;31:261-269.

57
Q
What physical finding should alert the surgeon to the possibility of a submucous cleft palate?
A. Alveolar notch
B. Nasolabial fistula
C. Enlarged adenoid pad
D. Bifid uvula
A

Answer: D
Rationale:
As described by Calnan, the classic clinical findings seen when a patient has a submucous cleft palate are a triad of bifid uvula, hard palate bony notch, and separation along the median raphe of the soft palate especially during elevation of the velum.
When a submucous cleft palate is present, the levator muscle is clefted and inserts abnormally into the posterior edge of the hard palate. The primary functional concern related to submucous cleft palate is the possibility that the patient will develop velopharyngeal insufficiency and hypernasal speech as with other cleft palate patients.
Reference:
Calnan, J. Submucous cleft palate. Br J Plast Surg. 1954; 6:264-82.
Ruiz RL, Costello BJ. Reconstruction of Cleft Lip and Palte: Secondary Procedures. In: Miloro M, Ghali GE, Larsen PE, and Waite PD (Editors): Peterson’s Principles of Oral and Maxillofacial Surgery, Second Edition. Pp: 871-886. BC Decker. Hamilton, Ontario, 2004.

58
Q

The repair of a submucous cleft palate is indicated:
A. after 3 or more episodes of otitis media during a 6 month period.
B. at the time of the diagnosis.
C. only in the presence of velopharyngeal dysfunction.
D. in the presence of obstructive sleep apnea.

A

Answer: C
Rationale:
The lone indication for repair of a submucous cleft palate is the presence of velopharyngeal dysfunction. While middle ear disease has long been associated with clefting of the secondary palate it’s incidence in the submucous cleft palate population may only be slightly higher compared with t he general population. Otitis media with effusion is managed with myringotomy and tube placement
It has been estimated that only 11% of children diagnosed with a submucous cleft will go on to develop velopharyngeal dysfunction. As such, repair at the time of diagnosis would represent overtreatment.
There is no direct association of submucous cleft palate and obstructive sleep apnea.
Reference:
Gosain AK, Conley SF, Marks S, Larson DL. Submucous Cleft Palate: Diagnostic Methods and Outcomes of Surgical Treatment.

59
Q

Phase I orthodontic treatment in the patient with a bilateral cleft lip and palate prior to maxillary bone graft surgery is primarily intended to:
A. collapse the cleft segments in order to obtain a class I molar relationship.
B. correct transverse maxillary dimension and align the pre-maxilla for symmetry.
C. expedite the exfoliation of remaining anterior primary teeth.
D. expand the cleft segments until a Class I molar relationship is obtained.

A

Answer: B
Rationale:
Surgical reconstruction of the child with cleft lip and palate requires familiarity with orthodontic management especially when considering sequencing of the procedures. Phase I orthodontic care of the child with bilateral cleft lip and palate should consist of maxillary transverse expansion to reduce cross-bites and align the pre-maxilla for position and symmetry. This will allow proper bone graft placement and consolidation of the premaxilla in the most appropriate position for function and aesthetics.
Reference:
Vig K, Turvey TA, Fonseca RJ: Orthodontic and Surgical Considerations in Bone Grafting in the Cleft Maxilla and Palate. In Facial Clefts and Craniosynostosis Principles and Management. Turvey et al. Saunders, Philadelphia, 1996. pg 396.

60
Q

Intravelar veloplasty during cleft palate repair is undertaken in order to reorient which aberrantly positioned muscle?
A. Salpingopharyngeus B. Palatoglossus
C. Levator veli palatini D. Tensor veli palatini

A

Answer: C
Rationale:
The term “intravelar veloplasty” was first used by Kriens in 1969 to describe a muscular reconstruction of the cleft palate. In particular, the levator veli palatini, which lie in an abnormal sagittal orientation and are aberrantly inserted at the posterior edge of the hard palate, are mobilized and re-oriented to lie transversely across the palate in a more normal orientation. The goal is to restore normal palatal function through the restitution of normal palatal functional anatomy.
The salpingopharyngeous, palatoglossus and superior constrictor, though part of the velopharyngeal mechanism, are not directly involved in this muscular reconstruction. The tensor veli palatini muscle passes around the hamular process and is not part of the musculature that is re-directed during veloplasty.
Reference:
Sommerlad BC. A Technique for Cleft Palate Repair. Plast Reconstr Surg 2003;112:1542- 1548.
The American Board of Oral and Maxillofacial Surgery 75

61
Q

When raising a superiorly based pharyngeal flap, dissection is carried to, but not through, which anatomic structure?
A. Superior pharyngeal constrictor muscle
B. Palatopharyngeous muscle
C. Pre-vertebral fascia
D. Pre-tracheal fascial

A

Answer: C
Rationale:
The superiorly based pharyngeal flap recruits tissue from the posterior wall of the pharynx and inserts it within the nasals side of the soft palate. The procedure involves the elevation of a superiorly based myomucosal flap (includes mucosa and superior pharyngeal constrictor muscle) off of the underlying pre-vertebral fascia. During the dissection, vertical incisions are made and blunt dissection is utilized to reach a glistening, distinct fascial layer. The soft palate is then split with dissection of the oral, nasal , and muscular layers. The flap is then inset into the nasal side closure and the oral mucosa is closed over the raw surface.
Reference:
Costello BJ, Turvey TA. Velopharyngeal insufficiency in patients with cleft palate. Oral Maxillofacial Surg Clin N Am 14 (2002) 539-551.

62
Q
One-stage repair of a cleft of the secondary palate is generally undertaken at what age?
A. Prior to 3 months of age
B. 3-6 months of age
C. 10-18 months of age
D. 3-5 years of
A

Answer: C
Rationale:
Cleft palate repair is generally undertaken between the ages of 10 and 18 months, The choice of timing is a balance between optimizing facial growth and the development of normal speech patterns. Repair prior to this age range has little impact on speech outcomes but does impact negatively on midfacial growth. Repair is then chosen to coincide with the generation of early speech such that a child who is not yet speaking need not undergo palatal repair with any sense of urgency. Delay of palatal repair beyond 18 months is generally felt to be detrimental to speech outcomes.
Reference:
LaRossa, D. The State of the Art in Cleft Palate Surgery. Cleft Craniofac J 2000;37:225- 228.

63
Q

A 17 year-old male with a history of a repaired left unilateral cleft lip and palate presents with a large Class III skeletal malocclusion. He is scheduled to undergo maxillary advancement via a LeFort I osteotomy. The anticipated incidence of postsurgical velopharyngeal insufficiency 6 months post surgery would be approximately:
A. 1%. B. 15%. C. 50%. D. 75%.

A

Answer: B
Rationale:
Deterioration in velopharyngeal function after maxillary advancement surgery in patients with cleft palates is a common occurrence. With the passage of time, a spontaneous recovery is observed such that, at 6 months, only approximately 15% will exhibit a persistent deterioration in their velopharyngeal function.
Reference:
Janulewicz JJ, Costello BJ, Buckley MJ, et al. The Effects of LeFort I Osteotomies on Velopharyngeal and Speech Functions in Cleft Patients. J Oral Maxillofac Surg 2004;62:308-314.

64
Q

During the primary repair of a cleft palate utilizing a two-flap technique, the greater palatine neurovascular bundle is transected during elevation of the left palatal flap. What is the next step in the surgical management of this patient?
A. Abort the procedure and reposition the flap.
B. Proceed with the palatoplasty procedure.
C. Proceed but without any further elevation of the flap.
D. Attempt re-anastamosis of the vessel.

A

Answer: B
Rationale:
Two-flap palatoplasty techniques involve the elevation of full-thickness mucoperiosteal flaps on each side of the cleft defect for oral side closure. After the nasal mucosa is closed, these soft tissue flaps are sutured together in the midline for closure of the cleft defect. During the initial dissection and elevation of the flaps, the greater palatine neurovascular bundles are identified and protected. The result is that the axial soft tissue flaps are raised based upon the blood supply of the greater palatine arteries bilaterally. If the greater palatine artery is injured or cauterized, surgery may proceed without any modifications. This is because of the abundant blood supply provided by the palatal soft tissue pedicle. Injury to the greater palatine artery simply converts the palatal flap’s blood supply from an “axial” pattern to a “random” pattern (i.e. not based on one specific arterial supply).
Reference:
Bardach J: Two-flap palatoplasty: Bardach’s technique. Operative Techniques in Plastic and Reconstructive Surgery, Vol 2. No 4(November), 1995: pp 211-214

65
Q

Initial management of the patient who develops velopharyngeal incompetence after LeFort I advancement surgery should be which of the following?
A. Double opposing Z-plasty (Furlow) palatoplasty
B. V-Y palatoplasty pushback surgery (Veau-Wardhill-Kilner Procedure)
C. Superiorly based pharyngeal flap
D. Observation for six months to one year

A

Answer: D
Rationale:
While a deterioration in velopharyngeal function is a very common manifestation after maxillary advancement surgery in the cleft palate population, the long term incidence is only approximately 18%. Because of the demonstrated recovery potential, it is most prudent to delay any interventions until sufficient time has passed to allow for spontaneous return of function.
A Furlow conversion, VY pushback and superiorly based pharyngeal flap are all surgical modalities employed in the surgical management of velopharyngeal insufficiency. Their use may be indicated in those where the velopharyngeal function fails to improve but again, only after waiting 6 months to 1 year to allow for spontaneous recovery.
Reference:
Janulewicz JJ, Costello BJ, Buckley MJ, et al. The Effects of LeFort I Osteotomies on Velopharyngeal and Speech Functions in Cleft Patients. J Oral Maxillofac Surg 2004;62:308-314.

66
Q
In a patient with cleft lip and palate, which of the following treatment modalities may cause growth restriction of the maxilla?
A. Lip adhesion procedure
B. Lip taping
C. Naso-alveolar molding devices
D. Pin retained orthopedic devices
A

Answer: D
Rationale:
All of the above listed treatment modalities are frequently utilized prior to definitive cleft lip repair in order to idealize the position of the maxillary dentoalveolar segments, improve the position of the alveolus and nasal base, and reduce the width of the cleft defect. The lip adhesion procedure involves the creation of a small “repair” of the cleft lip defect by attaching only the mucosa and lip skin without undertaking the repair of the orbicularis oris muscle. Lip adhesion is performed in order to convert a large complete cleft defect into a narrower, incomplete cleft defect. After several months, the patient is returned to the operating room and the definitive lip repair procedure (including the orbicularis muscle) is undertaken. Routine application of elastic bands and adhesive strips across the cleft defect may also help narrow the defect as well without the need for surgical intervention. Naso- alveolar molding devices are composed of a passive plate that fits over the maxillary segments and have attached wire and acrylic components for use in the molding of the nasal complex and lip taping. Unlike the other techniques listed, the use of pin-retained orthopedic devices (Latham appliance) involves more aggressive repositioning of the maxillary segments. Unfortunately, the use of these pin-retained devices with active orthopedic movement of the skeletal components is associated with maxillary growth restriction and a significant increase in the likelihood that orthognathic surgery will be necessary in the teenage years. The most popular theory to explain this association is that the aggressive skeletal movements produce disruption with hemorrhage at nasopalatine and maxillary suture regions.
Reference:
Berkowitz S. The comparison of treatment results in complete cleft lip/palate using conservative approach vs Millard-Latham PSOT procedure. Semin Orthod 2: 169, 1996.

67
Q

In a case of single-suture craniosynostosis, in what direction is cranial growth arrested? A. Parallel to the affected suture
B. Perpendicular to the affected suture
C. Parallel to the open sutures
D. Perpendicular to the open sutures

A

Answer: B
Rationale:
The term “craniosynostosis” refers to the premature fusion of one or more of the cranial vault sutures. The result is fusion of the bones adjacent to the suture and arrested sutural growth of the adjacent bones. The classic theory, known as Virchow’s law, states that premature fusion of a cranial suture results in limited development of the skull perpendicular to the fused suture and a compensatory overgrowth at the remaining open sutures.
Reference:
Nonsyndromic craniosynostosis: diagnosis and management. Ruiz, et.al. Oral and Maxillofacial Clinics of North America: Craniofacial Update.

68
Q
Most forms of craniofacial dysostosis syndromes (e.g. Crouzon, Apert, Saethre-Chotzen) demonstrate which of the following inheritance patterns?
A. X-linked recessive
B. X-linked dominant
C. Autosomal dominant
D. Autosomal recessive
A

Answer: C
Rationale:
The craniofacial dysostosis syndromes are inherited forms of craniosynostosis. Patients are born with more extensive sutural involvement which includes premature fusion of cranial vault sutures, but also affects the sutures of the mid-facial structures. This results in a typical morphological pattern that includes a total mid-face deficiency, proptosis, and a severe Angle Class III malocclusion.
Reference:
Chapter 6, Genetic etiologies of craniosynostosis by Ethylin Wang Jabs, MD.
Understanding craniofacial anomalies, the etiopathogenesis of craniosynostosis and facial clefting. Mooney and Siegel, Willey-Liss, New York, 2002.

69
Q

This CT image of a 3 month old male demonstrates which of the following conditions? (Sagittal suture is ossified)
A. Metopic synostosis B. Coronal synostosis C. Sagittal synostosis D. Lambdoid synostosis

A

Answer: C
Rationale:
The CT scan image shown above reveals sagittal suture craniosynostosis. The sagittal suture is absent and there is a classic scaphocephalic skeletal deformity. This is characterized by a narrow cranial vault in the bi-temporal and bi-parietal dimensions and elongation of the cranial vault in the antero-posterior dimension. This craniofacial deformity is the result of both arrested development at the site of the affected suture (e.g. sagittal) and an abnormal compensatory overgrowth at the site of the remaining open sutures (e.g. coronal and lambdoid).
Reference:
Posnick JC, Lin KY, Chen P, et al. Sagittal Synostosis: Quantitative assessment of presenting deformity and surgical results based on CT scans. Plast Reconstr Surg 92:1015, 1993.

70
Q
In diagnosing a child with a posterior cranial vault asymmetry characterized by unilateral flattening, benign positional skull molding must be differentiated from which type of craniosynostosis?
A. Lambdoid synostosis
B. Metopic synostosis
C. Sagittal synostosis
D. Bicoronal synostosis
A

Answer: A
Rationale:
When a lambdoid suture is absent, there is arrested skeletal growth across the affected occipital and parietal bones, which also results in significant flattening or posterior plagiocephaly, but that is where the similarities to positional plagiocephaly end.
Nonsynostotic Positional Plagiocephaly
Occipitoparietal flattening Ipsilateral frontal bossing Forward displacement of the ipsilateral ear
No bony ridging suture region
versus Lambdoid Synostosis
Occipitoparietal flattening Ipsilateral frontal flattening Posterior displacement of the ipsilateral ear
Bony ridging along involved
Reference:
From Positional plagiocephaly: evaluation and management. John Caccamese, DMD, MD, et.al. Oral and Maxillofacial Clinics of North America: Craniofacial Update.

71
Q

Which cranial vault suture(s) is most commonly involved in Crouzon Syndrome? A. The lambdoid suture(s)
B. The sagittal suture
C. The coronal suture(s)
D. The metopic suture

A

Answer: C
Rationale:
The craniosynostosis of Crouzon, Apert, and Pfeiffer syndromes involve sites of pathogenesis either unilaterally or bilaterally along the calvarial articulations of the coronal ring. Most commonly, patients affected with one of these craniofacial dysostosis syndromes will present with bilateral involvement of the coronal sutures.
Reference:
Chapter 16, Facial dysmorphology in the craniosynostoses: clinical implications by Katherine W.L. Vig, BDS, MS, Dorth.
Understanding craniofacial anomalies, the etiopathogenesis of craniosynostosis and facial clefting. Mooney and Siegel, Willey-Liss, New York, 2002.
The American Board of Oral and Maxillofacial Surgery 87

72
Q

In which disorder is absence of the frontal sinus most commonly noted? A. Apert Syndrome
B. Carpenter Syndrome
C. Cystic Fibrosis
D. Neurofibromatosis

A

Answer: C
Rationale:
Knowledge of how certain genetic disorders modify the craniofacial skeleton has an impact on directed surgical intervention. In cystic fibrosis, congenital absence of the frontal sinus is a noted feature of the disease. Patients with a diagnosis of cystic fibrosis are no more or less likely to sustain maxillofacial trauma than those of their age matched peers and are more susceptible to severe maxillofacial infections than that of the general population because of chemotherapeutic regimens and disorders of mucous regulation.
Reference:
Boat TF: Cystic Fibrosis. In Nelson Textbook of Pediatrics. Behrman, Kliegman, Jensen eds. Saunders, Philadelphia, 2000. pg 1315.

73
Q

The clinical term trigonocephaly is used to describe which form of craniosynostosis? A. Metopic
B. Sagittal C. Lambdoid D. Coronal

A

Answer: A
Rationale:
The term trigonocephaly (e.g. triangular-head) refers to a specific morphological pattern that may be the result of metopic suture craniosynostosis. In patients with absence of the metopic suture, there is a lack of skeletal growth perpendicular to the metopic suture which runs down the center of the forehead. At the same time, there is an increased, “compensatory,” growth at the cranial vault sutures that remain open. This results in the characteristic trigonocephalic deformity which includes a triangular-shaped forehead, hypotelorism, and horizontally retrusive lateral orbital rims.
Reference:
From Chapter 2, Terminology and classification of craniosynostosis by Marilyn Jones, MD. Understanding craniofacial anomalies, the etiopathogenesis of craniosynostosis and facial clefting. Mooney and Siegel, Willey-Liss, New York, 2002.
The American Board of Oral and Maxillofacial Surgery 89

74
Q
In a patient with Treacher Collins Syndrome, the reconstruction of zygomatic and orbital deformities should be delayed until what age?
A. 1to2years
B. 3to4years
C. 8 to 10 years
D. 4 to 17 years
A

Answer: C
Rationale:
Children with Treacher Collins Syndrome require multiple stages of skeletal reconstruction which include repair of the orbitozygomatic deformities and definitive orthognathic surgery. Reconstruction of the orbital hypoplasia and missing zygomatic arches is typically undertaken with the use of cranial bone grafts.
Whenever possible, orbitozygomatic reconstruction should be delayed until the orbital structures themselves are at or approaching skeletal maturity. By seven years of age, the cranio-orbitozygomatic skeleton is almost completely done growing. This makes late childhood the ideal time for construction of orbital and zygomatic components. If surgical correction of the orbital-zygomatic deformity is undertaken during infancy or early childhood, then subsequent growth may adversely effect the outcome.
Reference:
Waitzmann AA, Posnick JC, Armstrong D, et al. Craniofacial skeletal measurements based on computed tomography: II. Normal values and growth trends. Cleft Palate Craniofacial Journal 29:118, 1992.

75
Q

This CT scan image is of a 6 month old infant. What is the most appropriate course of treatment for the patient? (image shows right coronal suture is congenitally missing confirming the diagnosis of unilateral coronal craniosynostosis.)
A. Observation with no intervention
B. Reshaping of the posterior two-thirds of the cranial vault
C. Reshaping of the anterior cranial vault and fronto-orbital advancement
D. Non-surgical treatment with a custom cranial orthotic band

A

Answer: C
Rationale:
The CT Scan demonstrates that the right coronal suture is congenitally missing confirming the diagnosis of unilateral coronal craniosynostosis. Absence of growth perpendicular to this suture causes a characteristic craniofacial deformity that is characterized by orbital dystopia, shortening of the anterior cranial base on the affected side, and flattening of the forehead.
The treatment for this patient is designed to release the affected suture so that normal brain growth can occur and increased intracranial pressure is avoided. At the same time, the dysmorphic skeletal components are reshaped into a more anatomically correct position and contour. Reconstruction typically requires, bifrontal craniotomy for access, fronto- orbital osteotomies with reshaping, and reshaping of the anterior cranial vault.
Reference:
Turvey TA, Gudeman SK. Nonsyndromic Craniosynostosis. In: Turvey TA, Vig KWL, and Fonseca RJ (Editors): Facial Clefts and Craniosynostosis: Principles and Management. Pp: 596-629, W.B. Saunders. Philadelphia, 1996.

76
Q

During craniofacial surgery, a venous air embolism is suspected by the surgeon. Which of the following maneuvers would be most helpful in controlling the entry of air into the venous circulation?
A. Raising the patient’s head above the level of the heart
B. Limiting or avoiding irrigation of the involved surgical field
C. Application of bone wax to cut bone edges
D. Administration of a nitrous oxide – oxygen mixture

A

Answer: C
Rationale:
The cranial vault has a large number of diploic and emissary venous channels. These channels within the bone can be opened during a variety of surgical procedures including split-thickness cranial bone harvest, skull base procedures, and any reconstructive craniofacial operation that includes a craniotomy for access. As these venous channels are opened, air may travel to the right atrium. Because 35% of the pediatric population has a patent foramen ovale, the paradoxic passage of air from the right to left heart is possible and this air may then enter the cerebral and/or coronary circulation.
When air embolus is suspected during a craniofacial procedure, rapid control of the air entry portal is critical. Several technical maneuvers are useful in eliminating the entry of air into the cranial venous circulation. These include cessation of surgery, rapid lowering of the head below the level of the heart, copious irrigation of the involved field, manual compression of the venous channel, and the use of bone wax on cut bone surfaces. Nitrous oxide should be avoided and 100% oxygen administered.
Reference:
Greensmith AL, Meara JG, and Holmes AD. Complications related to cranial vault surgery. Oral Maxillofacial Surg Clin N Am 16 (2004) 465-473.

77
Q
Premature fusion (craniosynostosis) of the metopic suture will result in which of the following cranial vault deformities?
A. Brachycephaly
B. Scaphocephaly
C. Trigonocephaly
D. Posterior plagiocephaly
A

Answer: C
Rationale:
Metopic suture craniosynostosis results in a classic trigonocephalic skull dysmorphology. Because the metopic suture is absent and growth perpendicular to this region is arrested, there is a characteristic triangular shaped anterior skull. In addition, patients demonstrate horizontally retrusive lateral orbital rims and hypotelorism.

78
Q
A newborn child is noted to have multiple suture craniosynostosis associated with an underlying diagnosis of Crouzon syndrome. Which of the following represents the most appropriate age at which primary cranio-orbital surgery should be undertaken?
A. 4 to 12 months
B. 13 to 24 months
C. 3 to 5 years
D. 7 to 10 years
A

Answer: A
Rationale:
In untreated patients with more than one cranial vault suture affected, the likelihood of increased intracranial pressure exceeds 40 %. Despite this increased risk, signs of increased ICP are rarely seen prior to one year of age. Primary cranio-orbital decompression is typically undertaken at some point prior to one year of age.

79
Q

The Facial Bipartition Osteotomy differs from the Monobloc Osteotomy in that it:
A. utilizes a bifrontal craniotomy for the intracranial approach.
B. allows for fronto-orbital contouring at the time of surgery.
C. allows for correction of orbital hypertelorism.
D. is more commonly used in the reconstruction of Crouzon Syndrome.

A

Answer: C
Rationale:
The monobloc operation allows the surgeon to simultaneously advance the midface and fronto-orbital units through a transcranial approach for correction of the total midface deficiency characteristic of Crouzon syndrome. The facial bipartition procedure consists of the same surgical steps as the monobloc performed in combination with the removal of a section of bone from the midline. Because it allows correction of orbital hypertelorism, bipartition is often the procedure of choice for correction of the orbital and midfacial deformity associated with Apert syndrome.

80
Q

In an individual with Treacher Collins Syndrome, what surgical phase of reconstruction is best carried out at 8 to 10 years of age?
A. Craniosynostosis release
B. Distraction osteogenesis for mandibular advancement
C. Orbito-zygomatic reconstruction
D. Orthognathic surgery

A

Answer: C
Rationale:
Patients with Treacher Collins Syndrome frequently require bone grafts for construction of missing and hypoplastic orbital-zygomatic structures. Early surgery should be avoided since ongoing orbital growth may make the surgical outcome less predictable. Orbital structures are almost their adult size by approximately age 7. This makes late childhood the ideal time for construction of orbital and zygomatic components. If surgical correction of the orbital-zygomatic deformity is undertaken during infancy or early childhood, then subsequent growth may adversely effect the outcome.

81
Q
In an infant undergoing craniofacial reconstructive surgery involving a transcranial approach, which of the following clinical findings is an early indicator of cerebral air embolus?
A. Decreased end tidal CO2 levels
B. Increased end tidal CO2 levels
C. Oxygen desaturation
D. Hypertension
A

Answer: A
Rationale:
The pediatric cranial vault contains a number of diploic channels. As the cranium is exposed and craniotomy is completed, it becomes possible for air to enter the venous circulation and travel to the pulmonary vasculature. In children with a patent foramen ovale, air may also cross from the right to the left side of the heart and eventually enter the systemic, including cerebral, circulation. Air emboli may result in pulmonary hypertension, impaired coronary blood flow, and stroke. The earliest clinical sign of air embolism during a transcranial procedure is a decrease in end tidal CO2. This is often followed by hypotensive crisis.

82
Q
In a patient with Kaban Type IIb Hemifacial Microsomia, which of the following describes the condyle- ramus complex?
A. Unaffected
B. Minimally dysmorphic and hypoplastic
C. Severely dysmorphic and hypoplastic
D. Congenitally absent
A

Answer: C
Rationale:
The Kaban classification system is utilized to describe the mandibular skeletal defect associated with hemifacial microsomia. The Type I skeletal deformity is characterized by a mandibular condyle-ramus complex that is normal in morphology, but hypoplastic. Type IIa patients demonstrate an abnormally shaped ramus with more pronounced hypoplasia of the condyle and temporomandibular joint structures. In Type IIb, the deformity of the ramus is more severe and the condyle is severely hypoplastic and malpositioned. The Type III deformity consists of complete absence of the TMJ and ramus.

83
Q
Which of the following syndromes is associated with the finding of bilateral complex syndactyly of fingers and toes?
A. Apert syndrome
B. Carpenter syndrome
C. Crouzon syndrome
D. Saethre-Choetzen
A

Answer: A
Rationale:
All infants born with Apert syndrome demonstrate facial findings consistent with the other craniofacial dysostosis syndromes including craniosynostosis and total midfacial deficiency. In addition, patients with Apert syndrome have a high incidence of other anomalies including cleft palate, deafness, developmental delay, bilateral complex syndactyly of the fingers and toes, and other skeletal anomalies.

84
Q

A 16-year-old patient with a history of repaired cleft palate undergoes maxillary advancement and develops velopharyngeal insufficiency with significant hypernasality after the orthognathic procedure. What is the most appropriate next step?
A. Pharyngeal flap surgery 4 to 6 weeks postoperatively
B. Z-plasty for lengthening of the soft palate at 4 to 6 weeks postoperatively
C. Repeat Le Fort I level osteotomy for repositioning of the maxilla
D. Re-evaluation at 6 months postoperatively

A

Answer: D
Rationale:
Although most patients with repaired cleft palate who undergo maxillary advancement tolerate the change in soft palate position, a minority of patients will demonstrate a deterioration of velopharyngeal function and hypernasality. When it does occur, velopharyngeal insufficiency typically resolves with a return to the patient’s presurgical baseline by 6 months. It is prudent to delay subsequent surgery to reduce nasality for at least 6 months following maxillary advancement as most patients will not require surgical intervention.

85
Q

In the classic Millard (Rotation-Advancement) technique for cleft lip repair, the “C” flap may be utilized for reconstruction of the nostril sill or:
A. for recreating the philtral column on the cleft side.
B. for lengthening the cleft side columella.
C. for performing a gingivoperiosteoplasty.
D. may be banked for use at a later date.

A

Answer: B
Rationale:
The “C” flap is a soft tissue flap developed along the non-cleft side that may be utilized for a number of purposes depending on the anatomy of a particular cleft defect. Specific uses include nostril sill construction or lengthening of the lip.

86
Q

In the event that an alveolar cleft bone graft begins to extrude bone during the post-operative period, the surgeon should do which of the following?
A. Manage it expectantly with local debridement and supportive measures.
B. Immediately return to the operating room to remove the failed graft.
C. Immediately augment the graft with additional bone from another donor site.
D. Place additional sutures in the mucosa at the site of bone extrusion to prevent further bone loss.

A

Answer: A
Rationale:
Bone graft reconstruction of the cleft maxilla and palate is typically accomplished with the use of fresh, autogenous corticocancellous bone grafts harvested from the anterior iliac crest. Other bone harvest sites include the cranial vault and tibia. Necrosis and loss of a small bone fragment is a relatively common occurrence after bone graft repair of the cleft maxilla. In the absence of severe infection, management is conservative consisting primarily of local wound care measures such as frequent irrigation and hygiene. Many patients may loose several small bone fragments and still go on to heal an adequate amount of bone to accomplish the goals of cleft repair.

87
Q

Which of the following indications for bone graft reconstruction of the cleft maxilla and alveolus is unique to patients with bilateral deformities?
A. Provision of bone support to dentition
B. Creation of alveolar ridge continuity
C. Closure of oronasal fistulas
D. Stabilization of the premaxilla

A

Answer: D
Rationale:
The goals of bone graft reconstruction in patients with cleft lip and palate include:

88
Q

Which of the following techniques may cause unfavorable lateral condylar displacement during application of rigid internal fixation for a patient undergoing bilateral sagittal osteotomies for mandibular advancement?
A. Lag screw placement
B. Use of a bone shim in between segments
C. Recontouring of the distal segment
D. Addition of a symphysis osteotomy

A

Answer: A
Rationale:
Changes in intercondylar width may occur as a result of sagittal split osteotomy. As the distal segment is advanced, there is often the creation of a gap at the anterior-superior extent of the osteotomy site. If the segments are compressed together at the time of rigid fixation placement, there is a fulcrum based on the distal segment and lateral displacement of the condyle. Several techniques have been described in order to avoid unfavorable condylar displacement. These include the use of bicortical position screws, placement of bone shim between the proximal and distal segments, recontouring of the proximal/lingual aspect of the distal segment, and addition of a midline/symphyseal osteotomy. Use of lag screw fixation will compress the segments and actually cause lateral condylar displacement. Alternatively, lag screws may be utilized only when at least one position screw is placed first in order to maintain the anterior osteotomy gap.

89
Q
Which of the following clinical features is frequently encountered in patients with Treacher Collins Syndrome?
A. Malar Hypoplasia
B. Craniosynostosis
C. Partial anodontia
D. Bifid nose
A

Answer: A
Rationale:
Treacher Collins Syndrome is an autosomal dominant disorder affecting the hard and soft tissues of the
1st and 2nd branchial arches. It is commonly associated with a number of findings including malar hypoplasia with clefting of the zygomatic arches, mandibular hypoplasia with condyle-ramus anomalies, apertognathia, and hearing loss. Craniosynostosis, partial anodontia, and bifid nose are not associated with this disorder.

90
Q
In females, facial skeletal maturity typically occurs during which age range?
A. 11 to 13 years 
B. 14 to 16 years 
C. 16 to 18 years 
D. after age 18
A

Answer B
Rationale:
Females approach facial skeletal maturity at approximately 14 to 16 years of age. This is sooner than what is observed in males who reach completion of jaw growth at approximately 18 years of age.