What pattern of emphysema is this?
Panlobular
What pattern of emphysema is this?
Centrilobular
What pattern of emphysema is this?
Paraseptal
What is the lung pattern of alpha-1 antitrypsin deficiency?
Panlobular emphysema with extensive involvement of the lower lobes, often in young adults
What are the extrapulmonary findings of alpha-1 antitrypsin deficiency?
Liver - cholestasis and cirrhosis, the most common complication
What is the strongest risk factor for rapid deterioration of pulmonary function in alpha-1 antitrypsin deficient patients?
Smoking
How do you treat alpha-1 antitrypsin? (name similar disease type)
Like COPD