Non-inflammatory Vasculopathies

Question 1

Imaging findings of FMD (fibromuscular dysplasia)

Answer 1

• arterial stenosis, aneurysms and dissections (string of beads of alternating stenosis and dilation); most commonly involving the renal arteries

Question 2

Imaging findings of Marfan’s

Answer 2

• aneurysm and dissection of the proximal ascending aorta (sinotubular ectasia), aortic insufficiency, mitral valve prolapse and pulmonary artery dilation

Question 3

Name 3 vasculopathies that can result in multi-focal aneurysms

Answer 3

1) Ehlers Danlos (can also get spontaneous rupture, aneurysms, fistulas, dissections, etc.)
2) Grange Syndrome
3) Loeys-Dietz Syndrome