Nomenclature Flashcards
What is the nomenclature approach used for ACHD?
Sequential Segmental Approach
Who proposed the sequential segmental approach?
Praagh in 1960s and revised by Anderson and colleagues
What are the basic building blocks of the SSA?
Atria, Ventricles and the Great Arteries, AV and VA connections
Morphological characteristics of RAA
Blunt triangular appendage
Broad junction to RA
Morphological characteristics of LAA
Tubular
Narrow junction to LA
Morphological characteristics of RA
Pectinate muscles extend from RAA to postero-inferior wall of RA
Morphological characteristics of LA
Smooth posterior wall of LA
What atrial arrangements can you have?
Situs solitus
Situs inversus
Situs ambiguous (Right/Left isomerism = 2 x RA/2xLA)
How are the morphological characteristics in the SAA identified?
Echocardiogram
Morphological characteristics of RV
Coarse apical trabeculations
Muscular infundibulum between TV and PV
Septomarginal trabeculation and moderator band
Morphological characteristics of LV
Fine apical trabeculations
Fibrous continuity valves
Smooth septal surface
Ventricular Patterns
Balanced (Normal)
RV/LV Hypoplasia
Primitive morphological ventricle
How can you determine which is the primary ventricles in hypo-plastic RV/LV?
Based on morphological characteristics of large ventricle
Small ventricle in front and above –> large ventricle is LV
Small ventricle behind and below –> large ventricle is RV
What is a primitive morphological ventricle?
Very rare
Mixed morphological characteristics of LV and RV
Ventricular Arrangements
Normal Ventricular inversion (mirror image)