Neuromuscular/Chest Wall Disorders Flashcards

1
Q

What PFT measurements can assess respiratory muscle strength?

A

NIF (MIP)

VC

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
2
Q

What PFT measurement can assess airway clearance?

A

Maximum espiratory pressure (MEP)

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
3
Q

What neuromuscular disorder is characterized by:

Neuropathic pain, dysautonimia, ascending paralysis, and treatment is with plasmapharesis or IVIG

A

GBS

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
4
Q

Supportive respiratory care in GBS?

A

NIPPV or MV

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
5
Q

What neuromuscular disorder is characterized by:

ptosis, descending weakness that’s worse as the day progresses, treatment is with pyridostigmine, immunsupression, plasmapharesis/IVIG, or thymectomy

A

Myasthenia gravis

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
6
Q

Supportive respiratory care of myasthenia gravis during crisis?

A

NIPPV or MV

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
7
Q

What neuromuscular disorder is characterized by:

associated with small cell lung cancer, improving weakness with use, treatment with IVIG

A

Lambert-eaton

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
8
Q

Supportive respiratory care of lambert-eaton syndrome?

A

NIPPV early

MV late

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
9
Q

What neuromuscular disorder is characterized by:

Cognitive impairment, frontotemportal dememntia, signs of UMN and LMN weakness, treatment with riluzole

A

ALS

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
10
Q

Supportive respiratory care of ALS?

A

NIPPV or MV

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
11
Q

What neuromuscular disorder is characterized by:

GI symptoms, bilateral CNS weakness, and treatment with antitoxin

A

Botulism

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
12
Q

Supportive respiratory care with botulism?

A

MV, often prolonged

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
13
Q

What are factors of VC and NIF that are associated with impending respiratory failure requiring mechanical ventilation in GBS?

A

VC < 20 ml/kg

NIF -30

Also associated are rapid disease progression, bulbar dysfunction, bilateral facial muscle weakness, and dysautonomia

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
14
Q

What are the only diseasemodifying treatment

options for GBS?

A

Plasmapheresis or IVIG

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
15
Q

True or False: as opposed to GBS, weakness from CIDP responds to steroids

A

TRUE

Can also use plasmapharesis or IVIG as well

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
16
Q

When is NIPPV indicated for patients with ALS?

Think VC and NIF cutoffs

A

VC < 50% predicted

NIF -60 cm H2O

17
Q

Symptoms of organophosphate poisoning?

A

SLUDGE

Salivation
Lacrimation
Urination
Defecation
GI upset
Emesis
18
Q

Chest wall deformity of concave depression, can cause limiting RV filling and restriction on PFTs

A

Pectus excavatum

the CAVE

19
Q

Chest wall deformity that causes protrusion of sterum, associated with congential heart disease or scoliosis

A

Pectus carinatum

20
Q

Angle used to measure the severity of hyperkyphosis or scoliosis?

A

Cobb angle

21
Q

What Cobb angle is associated with VQ mismatch?

A

> 65 degrees

22
Q

What happens to the TLC, VC, and RV in severe scoliosis?

A

↓ TLC and VC

Normal RV, making RV:TLC ↑