Neuromuscular/Chest Wall Disorders Flashcards
What PFT measurements can assess respiratory muscle strength?
NIF (MIP)
VC
What PFT measurement can assess airway clearance?
Maximum espiratory pressure (MEP)
What neuromuscular disorder is characterized by:
Neuropathic pain, dysautonimia, ascending paralysis, and treatment is with plasmapharesis or IVIG
GBS
Supportive respiratory care in GBS?
NIPPV or MV
What neuromuscular disorder is characterized by:
ptosis, descending weakness that’s worse as the day progresses, treatment is with pyridostigmine, immunsupression, plasmapharesis/IVIG, or thymectomy
Myasthenia gravis
Supportive respiratory care of myasthenia gravis during crisis?
NIPPV or MV
What neuromuscular disorder is characterized by:
associated with small cell lung cancer, improving weakness with use, treatment with IVIG
Lambert-eaton
Supportive respiratory care of lambert-eaton syndrome?
NIPPV early
MV late
What neuromuscular disorder is characterized by:
Cognitive impairment, frontotemportal dememntia, signs of UMN and LMN weakness, treatment with riluzole
ALS
Supportive respiratory care of ALS?
NIPPV or MV
What neuromuscular disorder is characterized by:
GI symptoms, bilateral CNS weakness, and treatment with antitoxin
Botulism
Supportive respiratory care with botulism?
MV, often prolonged
What are factors of VC and NIF that are associated with impending respiratory failure requiring mechanical ventilation in GBS?
VC < 20 ml/kg
NIF -30
Also associated are rapid disease progression, bulbar dysfunction, bilateral facial muscle weakness, and dysautonomia
What are the only diseasemodifying treatment
options for GBS?
Plasmapheresis or IVIG
True or False: as opposed to GBS, weakness from CIDP responds to steroids
TRUE
Can also use plasmapharesis or IVIG as well