MTB 1 Flashcards

1
Q

Presentation of CVID

A

Adults

Recurrent sinupulmonary infxn

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2
Q

Common infxn’s in CVID

A

Giardiasis
Spruelike intestinal malabsorption
AI dz - pernicious anemia

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3
Q

Increase risk of what in CVID

A

Lymphoma

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4
Q

Decrease in output of B lymphocytes w normal number of B cells and normal amt of lymphoid tissue

A

CVID

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5
Q

TX for CVID

A

IVIG

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6
Q

Presentation of Bruton’s

A

Male children

Sinupulmonary infxn

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7
Q

Which tissues are diminished in Bruton’s

A

B cells
Lymphoid tissue
tonsils/ adenoids/lymph nodes/spleen

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8
Q

TX for Bruton

A

IVIG

Tx Infxns

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9
Q

Presentation of SCID

A

Recurrent sinupulm infxn start at 6 months

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10
Q

TX for SCID

A

Bone Marrow Transplant

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11
Q

Increased dz’s in IgA deficiency

A

Vitiligo
Thyroiditis
RA

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12
Q

Presentation of Hyper IgE syndrome

Tx?

A

Skin infxn w Staph

Tx: PPX ABX - Dicloxacillin, Cephalexin

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13
Q

TX for Wiskott Aldrich

A

Bone Marrow Transplant

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14
Q

Presentation of CGD

A

Mucopurulent LNs
Aphthous ulcers
Obstructive granulomas in GI or Urinary tract

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15
Q

Infxn with staph, burkholderia, nocardia, aspergillus

A

CGD

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16
Q

Increased sensitivity of dihydrohodamine 123 test

A

CGD

17
Q

Presentation of Hyper IgM

A

Poor specific response to immunizations
Recurrent sinupulmonary infxn
PCP

18
Q

Leukocyte Adhesion Deficiency Presentation

A

Absence of pus formation
Delayed umbilical cord separation
Poor wound healing
Periodontitis - necrotizing