MTB 1

Question 1

Presentation of CVID

Answer 1

Adults

Recurrent sinupulmonary infxn

Question 2

Common infxn’s in CVID

Answer 2

Giardiasis
Spruelike intestinal malabsorption
AI dz - pernicious anemia

Question 3

Increase risk of what in CVID

Answer 3

Lymphoma

Question 4

Decrease in output of B lymphocytes w normal number of B cells and normal amt of lymphoid tissue

Answer 4

CVID

Question 5

TX for CVID

Answer 5

IVIG

Question 6

Presentation of Bruton’s

Answer 6

Male children

Sinupulmonary infxn

Question 7

Which tissues are diminished in Bruton’s

Answer 7

B cells
Lymphoid tissue
tonsils/ adenoids/lymph nodes/spleen

Question 8

TX for Bruton

Answer 8

IVIG

Tx Infxns

Question 9

Presentation of SCID

Answer 9

Recurrent sinupulm infxn start at 6 months

Question 10

TX for SCID

Answer 10

Bone Marrow Transplant

Question 11

Increased dz’s in IgA deficiency

Answer 11

Vitiligo
Thyroiditis
RA

Question 12

Presentation of Hyper IgE syndrome

Tx?

Answer 12

Skin infxn w Staph

Tx: PPX ABX - Dicloxacillin, Cephalexin

Question 13

TX for Wiskott Aldrich

Answer 13

Bone Marrow Transplant

Question 14

Presentation of CGD

Answer 14

Mucopurulent LNs
Aphthous ulcers
Obstructive granulomas in GI or Urinary tract

Question 15

Infxn with staph, burkholderia, nocardia, aspergillus

Answer 15

CGD

Question 16

Increased sensitivity of dihydrohodamine 123 test

Answer 16

CGD

Question 17

Presentation of Hyper IgM

Answer 17

Poor specific response to immunizations
Recurrent sinupulmonary infxn
PCP

Question 18

Leukocyte Adhesion Deficiency Presentation

Answer 18

Absence of pus formation
Delayed umbilical cord separation
Poor wound healing
Periodontitis - necrotizing