MTB 1 Flashcards
Presentation of CVID
Adults
Recurrent sinupulmonary infxn
Common infxn’s in CVID
Giardiasis
Spruelike intestinal malabsorption
AI dz - pernicious anemia
Increase risk of what in CVID
Lymphoma
Decrease in output of B lymphocytes w normal number of B cells and normal amt of lymphoid tissue
CVID
TX for CVID
IVIG
Presentation of Bruton’s
Male children
Sinupulmonary infxn
Which tissues are diminished in Bruton’s
B cells
Lymphoid tissue
tonsils/ adenoids/lymph nodes/spleen
TX for Bruton
IVIG
Tx Infxns
Presentation of SCID
Recurrent sinupulm infxn start at 6 months
TX for SCID
Bone Marrow Transplant
Increased dz’s in IgA deficiency
Vitiligo
Thyroiditis
RA
Presentation of Hyper IgE syndrome
Tx?
Skin infxn w Staph
Tx: PPX ABX - Dicloxacillin, Cephalexin
TX for Wiskott Aldrich
Bone Marrow Transplant
Presentation of CGD
Mucopurulent LNs
Aphthous ulcers
Obstructive granulomas in GI or Urinary tract
Infxn with staph, burkholderia, nocardia, aspergillus
CGD