Middle Ear Diseases Flashcards
Middle ear diseases
Congenital malformations Acute otitis media Retraction pocket Atelectasis Serous otitis media Mucous otitis media Ossicular chain disarticulation Otosclerosis Barotrauma Cholesteatoma
What is a congenital malformation?
Physical defect present in a baby at birth, irrespective of whether the defect is caused by a genetic factor or by prenatal events that are non genetic
What is a malformation?
Development of a structure is arrested, delayed, or misdirected early in embryonic life and the effect is permanent
Other names for congenital malformation
Birth defect
Congenital anomaly
Types of non genetic malformations
Non-syndromic or syndromic acquired by prenatal events such as infection, alcohol, and drugs
Types of genetic congenital malformations
Non syndromic and syndromic such as treacher Collins syndrome and crouzon syndrome
What is a syndrome?
The combination of signs, and symptoms which together represent a particular disease or disorder. Different parts of the body are affected
Treacher Collins syndrome
Autosomal dominant hereditary craniofacial malformation (dysostosis) that affects ears, eyelids, cheek bones and mandible
What is the cause of Treacher Collins syndrome?
Mutation in the TCOF1 gene located at Chromosome 5
What does Treacher Collins lead to?
Malformed outer and middle ear:conductive hearing loss
Eyes slant downward
Notch in the lower eyelids
Underdeveloped cheek bones
Mandibular hypoplasia (underdeveloped or shortened jaw)
Cleft palate in some cases
Types of congenital malformations affecting hearing
Treacher Collins Syndrome
Crouzon syndrome
What is crouzon syndrome?
Autosomal dominant hereditary craniofacial malformation (dysostosis) that affects ears, eyes, jaw and upper lip
Physical manifestation of Crouzon syndrome
Malformed outer and middle ear: conductive
Bulging eyes and vision problems, eyes don’t point in the same direction (strabismus)
Beaked nose
Underdeveloped upper jaw and enlarged mandible
Shortened upper lip
Cleft palate (in some cases)
What is acute otitis media?
Infection of mucous-membrane lining the middle ear tympanic cavity
Primarily disease of childhood, can occur at any age
First URTI, bacteria can enter through ET from nasopharynx
Happens in fall and winter
How does a patient with acute otitis media present?
Otalgia (earache) Aural pressure ( sense of fullness in the ear)
Audiometric findings for acute otitis media
Conductive hearing loss
What are the otoscopy results for acute otitis media?
Redness and decreased mobility of TM
When severe, TM can be seen to bulge outward
Speech audiometry for acute otitis media
SRT and PTA - 0-6dB if each other ( good agreement)
WRS is 96-100%
Retraction Pocket
Small area of the TM to be retracted toward the tympanic cavity resulting in a retraction pocket
Audiometric results for retraction pockets
Normal or slight conductive hearing loss depending on the size of the retraction pocket
Speech audiometry for retraction pockets
SRT and PTA (0-6dB, a good agreement)
WRS 96-100%
Tympanometry for retraction pockets
Type C
Atelectasis
Large area of the TM to be retracted (sucked inside) toward the tympanic cavity.
Large area of TM may cover or adhere to the ossicular chain and the promontory
Audiometry of atelectasis
Mild or moderate conductive hearing loss depending on the degree of retraction
Speech audiometry for atelectasis
SRT and PTA are at 0-6 dB of each other (a good agreement)
WRS is 96-100%
Tympanogram of atelectasis
Type B